Motor NeuronsNeuronsMotor Neuron DiseaseSurvival of Motor Neuron 1 ProteinNeurons, AfferentBrain-Derived Neurotrophic FactorCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalMotor ActivityAxonsSMN Complex ProteinsNerve Tissue ProteinsAction PotentialsDisease-Free SurvivalReceptor, trkBTime FactorsCells, CulturedSurvivalSynapsesNerve DegenerationElectric StimulationMolecular Motor ProteinsImmunohistochemistryMice, TransgenicGanglia, InvertebrateNeuromuscular DiseasesSynaptic TransmissionSurvival AnalysisElectrophysiologyInterneuronsHippocampusDisease Models, AnimalDendritesNerve Growth FactorsBrainGraft SurvivalMovementAnimals, NewbornCholinergic NeuronsSuperoxide DismutaseDopaminergic NeuronsAplysiaMice, Inbred C57BLGanglia, SpinalNeuromuscular JunctionSensory Receptor CellsCerebral CortexElectromyographyAnterior Horn CellsPatch-Clamp TechniquesMutationNeural InhibitionSignal TransductionBulbar Palsy, ProgressiveRats, Sprague-DawleyModels, NeurologicalGABAergic NeuronsNeuronal PlasticityFacial NerveMice, KnockoutAxonal TransportAnimals, Genetically ModifiedCell Countgamma-Aminobutyric AcidMembrane PotentialsBehavior, AnimalAnalysis of VarianceMotor Skills DisordersBrain StemGreen Fluorescent ProteinsNeuropeptidesGene Expression Regulation, DevelopmentalCentral Nervous SystemCyclic AMP Response Element-Binding ProteinTreatment OutcomeCholine O-AcetyltransferaseExcitatory Postsynaptic PotentialsCell DeathNeurotrophin 3GangliaRNA, MessengerCell DifferentiationRats, WistarNeurofilament ProteinsNerve NetGlutamic AcidLocomotionNeural ConductionApoptosisNeurons, EfferentNeurogenesisGrasshoppersReaction TimeMuscle, Skeletal