Keto AcidsKetone OxidoreductasesCaproates3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)TransaminasesKetoglutaric AcidsAmino Acids, Branched-Chainp-FluorophenylalaninePhenylpyruvic AcidsMaple Syrup Urine DiseaseIsoleucineLeucineNorleucineKetoglutarate Dehydrogenase ComplexAmino Acids, EssentialPyruvatesMultienzyme ComplexesPseudomonasNitrogenValeratesPyruvic AcidAmino AcidsCoenzyme AStereoisomerismDietary ProteinsOxidation-ReductionSubstrate SpecificityButyratesKineticsUremiaNAD