• The study group comprised six leiomyosarcomas, five malignant peripheral nerve sheath tumours, two haemangiopericytomas and one epithelioid haemangioendothelioma. (nih.gov)
  • Epithelioid sarcoma (ES) is a rare, malignant soft tissue tumor. (logicalimages.com)
  • However, our search of the literature did not produce a significant volume of literature, or literature of sufficiently sound methodology, to permit our staff to make a determination regarding liver transplantation for other malignant diagnoses, such as metastatic disease, bile duct carcinoma and epithelioid hemangioendothelioma. (cms.gov)
  • Malignant vascular tumors: Epithelioid Hemangioendothelioma. (neoplasiaresearch.com)
  • Pulmonary epithelioid hemangioendothelioma (PEH) is a rare, low-to-intermediate malignant tumor of endothelial origin. (e-jyms.org)
  • Hepatic angiosarcomas and epithelioid hemangioendotheliomas can be easily overseen in liver biopsies, if they spread along the sinusoids without detoriation of the acinar architecture and without significant alteration of the surrounding liver cell plates. (springer.com)
  • Patients with UICC stages I or II hepatocellular carcinoma, the fibrolamellar variant of hepatocellular carcinoma, or epithelioid hepatic hemangioendothelioma are acceptable candidates for othotopic liver transplantation. (elsevierpure.com)
  • Hepatic epithelioid hemangioendothelioma: An international multicenter study. (clinic.cat)
  • Haemangiopericytoma and epithelioid haemangioendothelioma were associated with a more favourable prognosis. (nih.gov)
  • Background Epithelioid haemangioendothelioma (EHE) is a rare low-grade vascular neoplasm that can arise in the lung, liver, soft tissues or, less commonly, bone. (uni-luebeck.de)
  • An open-label, multicenter, phase II study of bevacizumab for the treatment of angiosarcoma and epithelioid hemangioendotheliomas. (uchicago.edu)
  • Genetic studies also led to the finding that WWTR1-CAMTA1 fusions are useful diagnostic markers for epithelioid hemangioendotheliomas, which can present as pleural-based masses. (nih.gov)
  • Novel YAP1-TFE3 fusion defines a distinct subset of epithelioid hemangioendothelioma. (uchicago.edu)
  • 15: Puls F, Niblett A, Clarke J, Kindblom LG, McCulloch T. YAP1-TFE3 epithelioid hemangioendothelioma: a case without vasoformation and a new transcript variant. (cancercentrum.se)
  • Mediastinal epithelioid hemangioendothelioma metastatic to lymph nodes and pleural fluid: report of a case. (uchicago.edu)
  • As its name implies, epithelioid hemangioendothelioma is an angiocentric vascular tumor with metastatic potential…These lesions may appear as a solitary, slightly painful mass in either superficial or deep soft tissue. (medicallessons.net)
  • Epithelioid hemangioendothelioma (EHE) is a rare tumor, first characterized by Sharon Weiss and Franz Enzinger in 1982 that both clinically and histologically is intermediate between angiosarcoma and hemangioma. (wikipedia.org)
  • Before the initial description of Weiss, the tumor had been reported under a variety of other names, including histiocytoid hemangioendothelioma, intravascular bronchoalveolar tumor (in the lung), and sclerosing cholangiocarcinoma. (wikipedia.org)
  • Introduction Foods for Epithelioid Hemangioendothelioma should be personalized for each individual and also must adapt when cancer treatment or tumor genetic change. (addon.life)
  • Hemangioendothelioma is a vascular tumor with several different morphologic patterns that can include a component of ovoid or spindled cells, but generally lacks an inflammatory component. (neoplasiaresearch.com)
  • We present a challenging lymphocyte-rich soft tissue lesion that was not recognized to be an unusual hemangioendothelioma until after several recurrences in the arm of a 63 year-old male, which was originally diagnosed as a follicular dendritic cell tumor instead. (neoplasiaresearch.com)
  • The most recent tumor consisted predominantly of epithelioid spindled cells with moderate amounts of bubbly pale to eosinophilic cytoplasm with rare discrete cytoplasmic vacuoles, admixed with a prominent lymphoid infiltrate and occasional erythrocytes. (neoplasiaresearch.com)
  • Epithelioid Hemangioendothelioma: A distinctive vascular tumor often mistaken for carcinoma. (neoplasiaresearch.com)
  • Recurrent EWSR1-CREB3L1 Gene Fusions in Sclerosing Epithelioid Fibrosarcoma. (lu.se)
  • CD31, CD34 and Fli-1 positive immunohistochemistry is strongly indicative of epithelioid lineage. (uni-luebeck.de)
  • Epithelioid Hemangioendothelioma is a rare form of cancer that affects the blood vessels of an individual and has an unknown etiology. (ipl.org)
  • Crazy sexy cancer is a documentary about a young lady, age 31, who was diagnosed with epithelioid Hemangioendothelioma, stage IV cancer on Valentine's day in 2003. (ipl.org)
  • Histology showed a nodular structure with clusters of epithelioid and spindled cells with a low proliferative index and mitotic count, suspended in a sclerotic stroma. (uni-luebeck.de)
  • Hemangioendothelioma, Epithelioid" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus, MeSH (Medical Subject Headings) . (uchicago.edu)
  • Histologic evaluation of the thyroid nodule showed multinodular proliferation of oval to polygonal-shaped epithelioid cells with oval nuclei and eosinophilic cytoplasm arranged in sheet- or cord-like patterns, accompanied by fibrous stroma and marked osseous metaplasia. (springeropen.com)
  • Cutaneous biopsy revealed RAE characterized by the proliferation of epithelioid and spindle-shaped cells in superficial and middermis lining vascular channels, arranged in clusters, and sometimes displaying an intravascular growth pattern. (thedoctorsdoctor.com)
  • First, more detailed study has been performed of histologic subtyping of epithelioid mesothelioma. (nih.gov)
  • Epithelioid Hemangioendothelioma affects about 0.1 percent of the American population with an overall 5-year survival rate of 55% after a standard primary radical treatment. (ipl.org)
  • 2. CAMTA-1 Expression in 24 Cases of Hepatic Epithelioid Hemangioendothelioma in a Single Institute: Diagnostic Utility for Differential diagnosis from Hepatic Angiosarcoma. (nih.gov)
  • The EHE Global Patient Registry empowers people with Epithelioid Hemangioendothelioma (EHE) to join together to improve our understanding of this ultra-rare sarcoma. (fightehe.org)
  • One of the members of the FOLD Planning Team has been diagnosed with an incredibly rare vascular sarcoma (blood vessel cancer), known as Epithelioid hemangioendothelioma (EHE) . (thefoldcanada.org)
  • Considering the biology and clinically variable natural history of epithelioid hemangioendothelioma, these results suggest that chronic Bartonella infection could have a role in the development of this vascular neoplasm. (nih.gov)
  • Background Epithelioid haemangioendothelioma (EHE) is a rare low-grade vascular neoplasm that can arise in the lung, liver, soft tissues or, less commonly, bone. (uni-luebeck.de)
  • 10. Epithelioid hemangioendotheliomas of the liver and lung in children and adolescents. (nih.gov)
  • This research study is studying a drug as a possible treatment for Angiosarcoma or Epithelioid hemangioendothelioma (EHE). (clinicaltrials.gov)
  • When solitary, epithelioid hemangioendothelioma lesions can exhibit a concentric ring or target appearance on contrast-enhanced CT and at MR and when numerous may be indistinguishable from angiosarcoma except for a more slowly advancing course. (johnshopkins.edu)
  • 8. Epithelioid Hemangioendothelioma: Update on diagnosis and Treatment. (nih.gov)
  • Fluorescence in situ hybridization for WWTR1-CAMTA1 has higher sensitivity and specificity for epithelioid hemangioendothelioma diagnosis. (cytopathology.org)
  • 12. Molecular characterization of epithelioid haemangioendotheliomas identifies novel WWTR1- camta1 fusion variants. (nih.gov)
  • Language": "en", "Country": "XG", "Code": "Background Information" }, { "Name": "Principle", "Value": "CD31 (JC70) Mouse Monoclonal Antibody (this antibody) may be used as the primary antibody for immunohistochemical staining of formalin-fixed, paraffin-embedded tissue sections. (roche.com)
  • Epithelioid hemangioendothelioma of skin and soft tissues: clinicopathologic and immunohistochemical study of 30 cases. (cytopathology.org)
  • Jebastin Thangaiah J, Hanley K, Nomani L, Policarpio-Nicolas ML. Cytologic features and immunohistochemical findings of epithelioid hemangioendothelioma (EHE) in effusion: A case series. (cytopathology.org)
  • [ 1 ] Epithelioid hemangioendothelioma (EHE) is an uncommon vascular tumour that was first described in 1975 by Dail and Liebow in the lung as an aggressive bronchoalveolar cell carcinoma. (medscape.com)
  • Epithelioid hemangioendothelioma, an ultra-rare cancer: a consensus paper from the community of experts. (nih.gov)
  • Robert (Bob) Thomas Capps Jr. of Steamboat Springs, CO passed away on April 2, 2023 in Nashville, TN at the age of 74 after battling Epithelioid hemangioendothelioma, or EHE, a rare form of cancer. (steamboatpilot.com)
  • Feb. 3, 2020) - Today, The EHE Foundation announced it will receive a $450,000 award from the Chan Zuckerberg Initiative (CZI) to drive progress towards treatments and a cure for Epithelioid Hemangioendothelioma (EHE), a rare vascular cancer. (fightehe.org)
  • are known to induce vasoproliferative tumors in immunocompromised patients and may play a role in the development of epithelioid hemangioendothelioma in immunocompetent patients. (nih.gov)
  • Histologically, the tumors were comprised of dendritic and epithelioid cells that often contained vacuoles representing intracellular lumina. (nih.gov)
  • Clinical characteristics of epithelioid hemangioendothelioma: a single-center retrospective study. (nih.gov)
  • They are a subtype of mesenchymal tumours, defined by their epithelioid morphology, which differentiates them from other vascular tumours. (medscape.com)
  • It is unclear whether the epithelioid hemangioendothelioma is truly neoplastic or an exuberant tissue reaction, nor is it clear if this is equivalent to Kimura's disease (see ANGIOLYMPHOID HYPERPLASIA WITH EOSINOPHILIA ). (nih.gov)
  • Histology showed a nodular structure with clusters of epithelioid and spindled cells with a low proliferative index and mitotic count, suspended in a sclerotic stroma. (uni-luebeck.de)
  • The support of doctors and researchers in the treatment and cure of Epithelioid Hemangioendothelioma (EHE), as well as offering support to EHE patients and families. (igive.com)
  • Bartonella henselae and B. koehlerae bacteremia was documented in two epithelioid hemangioendothelioma patients and B. koehlerae bacteremia in an asymptomatic partner of one of the patients. (nih.gov)
  • Management Strategies for Patients With Epithelioid Hemangioendothelioma: Charting an Indolent Disease Course. (nih.gov)
  • 4. [Atypical epithelioid hemangioendothelioma: a clinicopathological analysis of eight cases]. (nih.gov)
  • Epithelioid hemangioendothelioma of soft tissue: a proposal for risk stratification based on 49 cases. (cytopathology.org)