• Gierke
  • The treatment of Von Gierke disease may include restriction dietary intake of galactose or fructose, oral intake of cornstarch or nasogastric infusion of glucose and considering allopurinol to reduce the level of uric acid as well as calcium and multivitamins as dietary supplement. (medicalrealm.net)
  • accumulation
  • Clinical manifestations result, directly or indirectly, from inability to maintain an adequate blood glucose level during the post-absorptive hours of each day organ changes due to glycogen accumulation excessive lactic acid generation damage to tissue from hyperuricemia in GSD Ib, bleeding and infection risk from blood cell effects Hypoglycemia is the central clinical problem, the one that is most damaging, and the one that most often prompts the initial diagnosis. (wikipedia.org)