Single ventricleDORVConnected to the right ventrInjected from the right ventricleTranspositionTetralogyOutflow tractVentricular SeptumAnatomicPredominantlyGreat arteriesCardiacDefectsLeftAriseTaussig-BingRight atriumLethalityEndocardialDiagnosis of doubleDefinitionOccursBlood vesselIncidenceBabiesChambersFallotSurgeryDisorders
Single ventricle4
- Welcome to Little Hearts Matter ❤️ We are the only national UK charity offering specialised support to anyone affected by the diagnosis of single ventricle heart condition. (lhm.org.uk)
- Fetal echocardiographic parameters comparing BV repair versus single ventricle (SV) palliation were obtained, including the presence or absence of an apex-forming bLV was recorded. (mcmaster.ca)
- In format the book appears similar to a large collection of case reports covering all types of congenital heart disease, including complex lesions such as single ventricle and atrial isomerism. (stanford.edu)
- The Single Ventricle Home Monitoring Program at AdventHealth for Children was developed for babies with single ventricle-type congenital heart disease to help anticipate any potential issues and provide support through the vulnerable period between discharge from the hospital and the Glenn operation. (adventhealth.com)
DORV15
- Double outlet right ventricle (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole or in part) to the right ventricle (RV). (wikipedia.org)
- Double outlet right ventricle (DORV), as depicted in the image below, is a type of ventriculoarterial connection in which both the aorta (AO) and pulmonary artery (PA) arise entirely or predominantly from the right ventricle (RV). (medscape.com)
- Double outlet right ventricle (DORV) with transposition of the great arteries accounts for 26% of cases of DORV. (medscape.com)
- Electrocardiographic findings are rarely diagnostic for double outlet right ventricle (DORV). (medscape.com)
- [ 11 ] Of the 12 infants in whom double outlet right ventricle (DORV) was diagnosed and confirmed with angiography, 11 previously received a diagnosis based on subxiphoid two-dimensional echocardiography. (medscape.com)
- If you have DORV you have one big ventricle instead of two and blood travels from the heart in all directions. (lhm.org.uk)
- Double outlet right ventricle (DORV) is a congenital heart defect that occurs when the aorta and the main pulmonary artery both connect to the right ventricle instead the aorta connecting to the left ventricle. (umms.org)
- In double outlet right ventricle (DORV), both the aorta and pulmonary valve connect to the right ventricle. (msdmanuals.com)
- 2003 ). DORV is a congenital cardiac malformation in which both pulmonary artery and aorta predominantly arise from the right ventricle, and ventricular septal defect (VSD) always coexists (Lev et al. (springeropen.com)
- The term double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. (medscape.com)
- Double outlet right ventricle (DORV) is a complex cardiac malformation in which the majority of both pulmonary and aortic trunks arise from the right ventricle, typically coexisting with a VSD. (mhmedical.com)
- Double outlet right ventricle (DORV) refers to a congenital cardiac malformation in which most of the pulmonary artery and the aorta arise from the right ventricle, one subtype of which is known as the Taussig-Bing heart. (mhmedical.com)
- The surgical definition of DORV requires that at least 90% of the area of the outflow tracts arise from the right ventricle. (mhmedical.com)
- Therefore, cases of tetralogy of Fallot (see Chapter 52 ) in which the majority of the aortic outflow tract arises from the right ventricle could also be defined as DORV. (mhmedical.com)
- BACKGROUND: Atrioventricular septal defect (AVSD) and double outlet right ventricle (DORV) with normally related great arteries and normal ventricular sizes are associated with a good long-term prognosis after biventricular (BV) repair. (mcmaster.ca)
Connected to the right ventr1
- In a normal heart, the pulmonary artery is connected to the right ventricle and the aorta is connected to the left ventricle. (anavara.com)
Injected from the right ventricle1
- Most of the aorta arises from the right ventricle, the volume of venous blood was injected from the right ventricle into the aorta, which decided the oxygen saturations. (springeropen.com)
Transposition6
- Regardless of the end of the clinical spectrum (tetralogy of Fallot [TOF] or transposition of the great arteries [TGA]) at which double outlet right ventricle occurs, findings on anteroposterior and lateral chest radiography depend on the degree of pulmonary (or subpulmonary) stenosis. (medscape.com)
- Transposition of the Great Arteries (TGA) Transposition of the great arteries (in this case, dextro-transposition) occurs when the aorta arises directly from the right ventricle and the pulmonary artery arises from the left ventricle. (msdmanuals.com)
- The anatomic dysmorphology of double outlet right ventricle can vary from that of tetralogy of Fallot (TOF) on one end of the spectrum to complete transposition of the great arteries (TGA) on the other end (see the image below). (medscape.com)
- Brain Abscess in an Adult with Unrepaired Double-Outlet Right Ventricle with Transposition of Great Arteries and Pulmonic Stenosis. (escardio.org)
- The most common congenital diagnoses were Tetralogy of Fallot (n = 11), congenitally corrected transposition of the great arteries (ccTGA) (n = 9) and double outlet right ventricle (n = 6). (nih.gov)
- Transposition of the great arteries is when the pulmonary artery (the blood vessel that carries blood from the right ventricle to the lungs) is switched in position with the aorta (the blood vessel that carries blood from the left ventricle to the body). (federalwaypediatrics.com)
Tetralogy1
- [9] Cardiac defects can include Tetralogy of Fallot, aortic arch interruption, double outlet right ventricle with arch vessel abnormalities, and atrioventricular septal defects (AVSD). (aao.org)
Outflow tract3
- Attempts have been made to define the malformation based on the relative area of each outflow tract arising from the right ventricle, with an anatomic threshold of 50% being used. (mhmedical.com)
- The right ventricle discharges blood into the pulmonary artery across the pulmonic (semilunar) valve located in the outflow tract (infundibulum). (medscape.com)
- The inflow tract (sinus) and outflow tract (infundibulum) of the right ventricle are widely separated. (medscape.com)
Ventricular Septum2
- Its posterior wall is formed by the [[ventricular septum]], which bulges into the right ventricle, so that a transverse section of the cavity presents a semilunar outline. (wikidoc.org)
- However, because the surface of the right ventricle is trabecular, small defects of the muscular portion of the ventricular septum may be difficult to see. (medscape.com)
Anatomic3
- MRI is useful to obtain additional anatomic information, such as the relationship of both ventricles. (medscape.com)
- Demir MT, Amasyall Y, Kopuz C, Aydln ME, Corumlu U. The double outlet right ventricle with additional cardiac malformations: an anatomic and echocardiographic study. (medscape.com)
- Double outlet ventricles: review of anatomic and imaging characteristics. (nih.gov)
Predominantly2
- However, the Congenital Heart Surgery Nomenclature and Database Project defines double outlet right ventricle as a type of ventriculoarterial connection in which both great vessels arise either entirely or predominantly from the right ventricle. (medscape.com)
- Double outlet left ventricle (DOLV) is a rare congenital cardiac malformation in which both the pulmonary artery and the aorta arise exclusively or predominantly from the morphologic left ventricle. (hacettepe.edu.tr)
Great arteries5
- Echocardiography can be used to correctly identify the relative position of the great arteries, the degree of subsemilunar narrowing, the position of the ventricular septal defect (VSD), and the status of the mitral valve and left ventricle. (medscape.com)
- In 1793, Aberanthy described a heart with the origin of both great arteries from the right ventricle. (medscape.com)
- In general, from a surgical perspective, defining the lesion as double outlet right ventricle is reasonable when more than 50% of both of the great arteries arise from the right ventricle. (medscape.com)
- Based on the location of ventriculoseptal defect (VSD) in relation to great arteries, double outlet right ventricle can be classified into 4 main categories: double outlet right ventricle with subaortic VSD, double outlet right ventricle with subpulmonary VSD, double outlet right ventricle with doubly committed VSD, and double outlet right ventricle with noncommitted VSD. (medscape.com)
- We describe a case of DOLV with situs solitus, d-loop ventricles, d-malposition of the great arteries (S, D, D), severe pulmonary stenosis, and a subaortic ventricular septal defect in which the left ventricle was also severely hypoplastic. (hacettepe.edu.tr)
Cardiac3
- Cardiac catheterization, once the criterion standard for confirming double outlet right ventricle, is now rarely required in the evaluation or preoperative planning of this cardiac disorder. (medscape.com)
- [ 12 ] A study that assessed the incidence and diagnostic accuracy of preoperative cardiac CT scanning for identifying detailed coronary artery anatomy in 318 children with TOF or Fallot type of double outlet right ventricle found a 95% concordance between cardiac CT scanning and surgical findings, and a 96.9% diagnostic accuracy for cardiac CT scanning. (medscape.com)
- Coronary sinus, normally located between the LEFT ATRIUM and LEFT VENTRICLE on the posterior surface of the heart, can serve as an anatomical reference for cardiac procedures. (bvsalud.org)
Defects3
- The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. (wikipedia.org)
- Some of the heart defects involve structures within the heart itself, such as the two lower chambers of the heart (the ventricles) or the valves that control blood flow through the heart. (medlineplus.gov)
- Ventricular septal defects (VSDs) commonly occur in the area between the sinus and the outlet tract of the right ventricle. (medscape.com)
Left14
- The only outlet from the left ventricle (LV) is a ventricular septal defect (VSD) . (medscape.com)
- The only outflow from the left ventricle (LV) is a ventricular septal defect (VSD), which diverts blood toward the RV. (medscape.com)
- Common findings in a child with double outlet right ventricle include right ventricular hypertrophy, right axis deviation, and, occasionally, evidence of left ventricular hypertrophy. (medscape.com)
- Create a tunnel through the hole in the heart to connect the left ventricle to the aorta. (sparrow.org)
- Some adults born with double-outlet right ventricle need medicine to help the right or left lower heart chambers work better. (sparrow.org)
- Because both great vessels arise from one ventricle, there is some degree of mixing of desaturated systemic venous blood and highly saturated pulmonary venous return that enters the right ventricle via flow through the left atrium, left ventricle, and VSD. (msdmanuals.com)
- Although hearts with atrioventricular discordance (ie, congenitally corrected TGA) or univentricular atrioventricular connections (ie, double inlet left ventricle) can be correctly grouped in this spectrum of anomalies, this article focuses on only those hearts with atrioventricular concordance and 2 functional ventricles. (medscape.com)
- In this variant of double outlet right ventricle, the pulmonary artery preferentially receives left ventricular oxygenated blood, and the desaturated blood from the right ventricle streams to the aorta (TGA type). (medscape.com)
- This causes oxygen-rich blood to flow from the left ventricle to the right ventricle and mix with oxygen-poor blood. (anavara.com)
- The outcome of cases with a borderline small left ventricle (bLV) is unclear. (mcmaster.ca)
- Many morphologic variations of this malformation have been described but to the our knowledge DOLV with a hypoplastic left ventricle has not been reported before. (hacettepe.edu.tr)
- A hole in the wall between the right and left lower heart chambers, or the ventricles. (vejthani.com)
- The cavity equals in size that of the left ventricle, and is capable of containing about 85 c.c. (wikidoc.org)
- Medial rotation from the left exposes the left ventricle apex, left pulmonary veins, and left atrium. (medscape.com)
Arise2
- The aorta (AO) is anterior and to the right of the pulmonary artery (PA), and both arteries arise from the right ventricle (RV). (medscape.com)
- All of one vessel and most of the remaining vessel typically arise from the right ventricle. (medscape.com)
Taussig-Bing1
- The Taussig-Bing anomaly is a typical example of double outlet right ventricle with subpulmonary VSD. (medscape.com)
Right atrium2
- The structures initially seen from this perspective include the superior vena cava, right atrium, right ventricle, pulmonary artery, and aorta. (medscape.com)
- The right ventricle receives blood from the right atrium across the tricuspid valve, which is located in the large anterolateral (ie, sinus) portion of the right ventricle. (medscape.com)
Lethality1
- Mice homozygous for a knock-out allele exhibit a hypocellular placenta, abnormal placental labyrinth vasculature morphology, abnormal spongiotrophoblast inclusions, double outlet right ventricle, and partial lethality throughout fetal growth and development. (jax.org)
Endocardial1
- Essential modifiers of double outlet right ventricle: Revisit with endocardial surface images and 3-dimensional print models. (msdmanuals.com)
Diagnosis of double1
- MRI has been used in the diagnosis of double outlet right ventricle, but it is not yet a routine or well-established diagnostic modality forthis condition. (medscape.com)
Definition1
- The definition of a double outlet right ventricle has been a point of controversy among professionals in the field of congenital heart surgery. (medscape.com)
Occurs2
- In cases of a subaortic VSD, which occurs in 60-70% of patients, the VSD is closer to the aortic valve, thus oxygenated blood from the LV is directed to the AO and desaturated blood from the right ventricle (RV) is directed primarily to the PA (see the image below). (medscape.com)
- Not only was Claire born small, but she was also born with a type of congenital heart disease called double outlet right ventricle - a condition that occurs once in every 6,000 to 10,000 births, when the aorta and the pulmonary artery connect to the heart's ventricle. (childrensnational.org)
Blood vessel2
- Insert a blood vessel to connect the right ventricle to the pulmonary artery. (sparrow.org)
- Defined as the aorta (the blood vessel that pumps blood from the heart to the body) attaching to the right ventricle (the heart chamber that pumps blood from the right side of the heart to the lungs). (federalwaypediatrics.com)
Incidence1
- In the United States, the incidence of double outlet right ventricle is 0.09 cases per 1000 live births. (medscape.com)
Babies3
- In babies with double-outlet right ventricle, both the aorta and the pulmonary artery connect partially or completely to the right lower heart chamber. (sparrow.org)
- Babies with double-outlet right ventricle also have a hole between the lower heart chambers. (sparrow.org)
- Some babies with double-outlet right ventricle need heart repair surgery within the first few days of birth. (sparrow.org)
Chambers4
- The lower heart chambers are called the ventricles. (sparrow.org)
- In people with double-outlet right ventricle, there is also a hole between the lower heart chambers (ventricles), called a ventricular septal defect (VSD), which can be located in several places in the wall between the ventricles. (anavara.com)
- A double outlet right ventricle with a ventricular spetal defect (a hole between the two bottom chambers (ventricles) of the heart), that is considered to be closely related to the pulmonary origin. (nih.gov)
- A ventricular septal defect is when there is a hole between the two ventricles, which are the bottom two chambers of the heart. (federalwaypediatrics.com)
Fallot1
- Preoperative CT scanning is potentially useful for identifying coronary artery anatomy in children with TOF or Fallot type of double outlet right ventricle. (medscape.com)
Surgery1
- The shunt is removed later in life during heart surgery to repair the double-outlet right ventricle. (sparrow.org)
Disorders1
- Of these 3 subdivisions, the conal septum is clinically significant because it can be malpositioned in patients with congenital disorders (eg, double outlet right ventricle ). (medscape.com)