... at eMedicine Juvet, Stephan (2010). "Rare lung diseases III: Pulmonary Langerhans' cell ... Langerhans cell histiocytosis (LCH) is an abnormal clonal proliferation of Langerhans cells, abnormal cells deriving from bone ... was diagnosed with Langerhans cell histiocytosis.[citation needed] Langerhans cell histiocytosis is occasionally misspelled as ... "Langerhans Cell Histiocytosis Treatment (PDQ®): Health Professional Version". Langerhans Cell Histiocytosis Treatment (PDQ®). ...
Philip T. Cagle; Timothy C. Allen; Roberto Barrios (1 December 2007). Color atlas and text of pulmonary pathology. Lippincott ... Non-Langerhans cell histiocytosis refers to a family of histiocytosis characterized by the absence of Langerhans cells. Many ... The spectrum of non-langerhans cell histiocytoses include: Benign cephalic histiocytosis Generalized eruptive histiocytoma ... "Non-Langerhans-Cell Histiocytosis". NIH. The Genetic and Rare Diseases Information Center (GARD). Retrieved 19 March 2019. ...
Nonhereditary recurrent pneumothorax and/or pulmonary cysts can occur with Langerhans cell histiocytosis and ... it is associated with clear cell renal cell carcinoma and papillary renal cell carcinoma. If it develops in someone with BHD, ... clear cell renal cell carcinoma), hereditary papillary renal cancer (papillary renal cell carcinoma), and hereditary ... When this occurs, the result is that these cells have no functional copies of the FLCN gene, allowing the cells grow out of ...
... chronic hypersensitivity pneumonitis non-specific interstitial pneumonia sarcoidosis pulmonary Langerhans cell histiocytosis ... Pneumoconiosis Silicosis Asbestosis Idiopathic pulmonary fibrosis Pulmonary fibrosis Emphysema Travis WD, King TE, Bateman ED, ... The scarring (fibrosis) involves the pulmonary interstitium (the supporting framework of the lung). UIP is thus classified as a ... In case of idiopathic pulmonary fibrosis, certain medications like nintedanib and pirfenidone can help slow the progression. ...
Yousem SA, Dacic S, Nikiforov YE, Nikiforova M. Pulmonary Langerhans Cell Histiocytosis: Profiling of Multifocal Tumors Using ... Cell Cycle. 2013, 12(4):547-52. Chan JM, Bilodeau E, Celin S, Nikiforov Y, Johnson JT. Ewing sarcoma of the thyroid: Report of ... Cell. 2014 Oct 23;159(3):676-90. Nikiforov YE, Carty SE, Chiosea SI, Coyne C, Duvvuri U, Ferris RL, Gooding WE, Hodak SP, ... Homologous chromosomes move and rapidly initiate contact at the sites of double-strand breaks in genes in G0-phase human cells ...
... including pulmonary Langerhans cell histiocytosis, emphysema, Sjögren's syndrome, or Birt-Hogg-Dubé syndrome. VEGF-D levels ... There are two major cell morphologies in the LAM lesion: small spindle-shaped cells and cuboidal epithelioid cells. LAM cells ... and in circulating LAM cells (cells in blood and urine). Angiomyolipomas and pulmonary LAM cells from women with the sporadic ... LAM cells behave, in many ways, like metastatic tumor cells. LAM cells appear to arise from an extrapulmonary source and ...
Langerhans cell histiocytosis (LCH) Lymphangioleiomyomatosis (LAM) Lymphocytic interstitial pneumonia (LIP) Birt-Hogg-Dubé ... A focal lung pneumatosis, is an enclosed pocket of air or gas in the lung and includes blebs, bullae, pulmonary cysts, and lung ... "Pulmonary cyst". Radiopaedia. Retrieved 2019-05-01. Hansell, DM.; Bankier, AA.; MacMahon, H.; McLoud, TC.; Müller, NL.; Remy, J ... "Pulmonary bullae , Radiology Reference Article , Radiopaedia.org". Radiopaedia. Retrieved 16 June 2019. Dr Daniel J Bell and Dr ...
United States Pulmonary Langerhans' cell histiocytosis, a type of interstitial lung disease Cassidy International Airport, an ...
... cell histiocytosis Pulmonary alveolar proteinosis Conditions specifically affecting the interstitium are called interstitial ... of which there are several types Sarcoidosis Eosinophilic pneumonia Lymphangioleiomyomatosis Pulmonary Langerhans' ... Pulmonary function test demonstrates a decrease in the forced vital capacity. Due to the chronic nature of this disease, the ... PULMONARY FUNCTION TESTS A Workshop on Simple Spirometry & Flow Volume Loops. Archived 2010-03-31 at the Wayback Machine Dr. S ...
... including sickle cell disease) Systemic diseases: sarcoidosis, pulmonary Langerhans cell histiocytosis: ... pulmonary hypertension or 'pulmonary venous hypertension'). However, in some patients, the raised pressure in the pulmonary ... Pulmonary Hypertension Wikimedia Commons has media related to Pulmonary hypertension. Scholia has a topic profile for Pulmonary ... Risk factors include a family history, prior pulmonary embolism (blood clots in the lungs), HIV/AIDS, sickle cell disease, ...
... histiocytosis, langerhans-cell MeSH C08.381.483.600 - pneumoconiosis MeSH C08.381.483.600.125 - asbestosis MeSH C08.381.483.600 ... non-small-cell lung MeSH C08.381.540.147 - carcinoma, small cell MeSH C08.381.540.150 - coin lesion, pulmonary MeSH C08.381. ... non-small-cell lung MeSH C08.785.520.147 - carcinoma, small cell MeSH C08.785.520.150 - coin lesion, pulmonary MeSH C08.785. ... pulmonary fibrosis MeSH C08.381.483.675 - radiation pneumonitis MeSH C08.381.483.725 - sarcoidosis, pulmonary MeSH C08.381. ...
... pulmonary veno-occlusive disease, lymphomatoid granulomatosis, pulmonary Langerhans cell histiocytosis, pulmonary epithelioid ... Experimental pulmonary arterial hypertension (aorta to pulmonary artery shunt) and effects of hyperkinesis (total pulmonary ... Liebow was one of the leading world experts in pulmonary pathology. He described many new pulmonary entities. The basis of many ... Liebow authored many of the seminal books on pulmonary diseases. He also published papers on sclerosing pneumocytoma, pulmonary ...
Langerhans cell histiocytosis Langerhans cell sarcoma Interdigitating dendritic cell sarcoma/tumor Follicular dendritic cell ... Jülg BD, Weidner S, Mayr D (March 2006). "Pulmonary manifestation of a Langerhans cell sarcoma: case report and review of the ... Langerhans cell sarcoma (LCS) is a rare form of malignant histiocytosis. It should not be confused with Langerhans cell ... Langerhans cell sarcoma can occur de novo, or can occur as a malignant transformation of Langerhans cell histiocytosis. The ...
In general, the cause of Langerhans Cell Histiocytosis is unknown. Regardless of the subtype of Langerhans cell histiocytosis, ... leading to hypoproteinemia and bleeding due to diminished clotting factor synthesis Pulmonary manifestations such as cough, ... Lipton, J. M.; Levy, C. F. (December 2021). "Langerhans Cell Histiocytosis - Hematology and Oncology". Merck Manuals ... Electron microscopy will show racket-like Langerhans cell granules within the specific infiltrating cells. The demonstration of ...
Tran, Gary; Huynh, Thy N.; Paller, Amy S. (March 2018). "Langerhans cell histiocytosis: A neoplastic disorder driven by Ras-ERK ... Abbott, Dawn E. E.; Allen, Andrew L. (March 2020). "Canine eosinophilic pulmonary granulomatosis: case report and literature ... Kumar, Neeta; Sayed, Shahin; Vinayak, Sudhir (2011-01-20). "Diagnosis of Langerhans cell histiocytosis on fine needle ... Kobayashi, Masayuki; Tojo, Arinobu (December 2018). "Langerhans cell histiocytosis in adults: Advances in pathophysiology and ...
Histologically, ECD differs from Langerhans cell histiocytosis (LCH) in a number of ways. Unlike LCH, ECD does not stain ... November 2010). "Pulmonary involvement in Erdheim-Chester disease: a single-center study of thirty-four patients and a review ... a non-Langerhans-cell histiocytosis, with interferon-alpha". Blood. 106 (9): 2992-2994. doi:10.1182/blood-2005-06-2238. PMID ... Langerhans Cell Histiocytosis, and Rosai-Dorfman Disease". Mayo Clinic Proceedings. 94 (10): 2054-2071. doi:10.1016/j.mayocp. ...
... granular cell tumor, Langerhans cell histiocytosis, fibrous histiocytoma, xanthogranuloma, Gaucher's disease, malakoplakia, and ... Wu, Pao-Shu (2020-08-01). "Pulmonary crystal-storing histiocytosis: a case report and literature review". International Journal ... Histiocytosis is an excessive number of histiocytes (an immune cell type which is part of the mononuclear phagocyte system). In ... The majority of patients (90%) are diagnosed with crystal-storing histiocytosis had a neoplastic B-cell disorder - most ...
Non-Langerhans-Cell Histoplasmosis Histrionic personality disorder Hittner-Hirsch-Kreh syndrome HIV Hm syndrome HMG-CoA lyase ... bundle tachycardia Histadelia Histapenia Histidinemia Histidinuria renal tubular defect syndrome Histiocytosis X Histiocytosis ... familial pulmonary capillary Hemangiopericytoma Hematocolpos Hemeralopia, congenital essential Hemeralopia, familial Hemi 3 ... Hagemoser-Weinstein-Bresnick syndrome Hailey-Hailey disease Hair defect with photosensitivity and mental retardation Hairy cell ...
Langerhans cell histiocytosis) lower (e.g., cryptogenic fibrosing alveolitis, connective tissue disease, asbestosis, drug ... Enlargement of the right descending pulmonary artery can indirectly reflect changes of pulmonary hypertension, with a size ... cystic bronchiectasis Langerhans cell histiocytosis lymphangioleiomyomatosis Ground glass extrinsic allergic alveolitis ... Langerhans cell histiocytosis, lymphangioleiomyomatosis, cystic fibrosis, allergic bronchopulmonary aspergillosis) decreased (e ...
Pulmonary Langerhans cell histiocytosis Pulmonary lymphangioleiomyomatosis Honeycomb lung caused by idiopathic pulmonary ... proteinosis Sarcoidosis Pulmonary veno-occlusive disease Upper lung predominance Pulmonary Langerhans cell histiocytosis ... Prolonged ILD may result in pulmonary fibrosis, but this is not always the case. Idiopathic pulmonary fibrosis is interstitial ... Pulmonary edema Chronic: Idiopathic pulmonary fibrosis Connective tissue-associated interstitial lung diseases Asbestosis ...
Langerhans cell granulomatosis Langerhans cell histiocytosis Laparoschisis Laplane-Fontaine-Lagardere syndrome Large B-cell ... pulmonary Lymphangiomyomatosis Lymphatic filariasis Lymphatic neoplasm Lymphedema distichiasis Lymphedema hereditary type 1 ... large-cell, immunoblastic Lymphoma, large-cell Lymphoma, small cleaved-cell, diffuse Lymphoma, small cleaved-cell, follicular ... B-Cell, chronic Leukemia, Myeloid Leukemia, T-Cell, chronic Leukemia Leukocyte adhesion deficiency syndrome Leukocyte adhesion ...
... derived from specialised epidermic dendritic cells, the Langerhans cells) 2. Reactive histiocytosis (immunohistochemical ... Accordingly, pulmonary symptoms such as cough and dyspnea have been seen. CNS involvement (primary or secondary) can lead to ... Amongst leukocytes, E-cadherin expression is unique to Langerhans cells. Langerhans cells utilize E-cadherin to localize in the ... Cutaneous histiocytoma = Langerhans cells: CD1+, CD11c+, MHCII+, CD86+, E-cad+, Langerin+, CD14-, Thy1- Reactive histiocytosis ...
... large-cell MeSH C15.604.667.400.390.550.465 - lymphoma, large-cell, ki-1 MeSH C15.604.667.400.400 - histiocytosis, langerhans- ... pulmonary MeSH C15.604.515.827.865 - uveoparotid fever MeSH C15.604.515.841 - sezary syndrome MeSH C15.604.515.880 - tumor ... cell MeSH C15.604.667.400.400.360 - eosinophilic granuloma MeSH C15.604.667.400.410 - histiocytosis, non-langerhans-cell MeSH ... mantle-cell MeSH C15.604.515.569.480.475 - lymphoma, large-cell MeSH C15.604.515.569.480.475.300 - lymphoma, large-cell, ...
B-cell lymphoma, T-cell lymphomas, T cell leukemias, and Langerhans cell histiocytosis. Other hematological diseases are ... They may present with cutaneous and/or pulmonary allergic symptoms, mucosal ulcers, splenomegaly, current or history of ... Hematopoietic stem cells give rise to: 1) myeloid precursor cells that differentiate into red blood cells, mast cells, blood ... Similar non-clonal eosinophilia due to eosinophil precursor cell stimulation by clonal malignant cells is sometimes seen in ...
... sarcoidosis Indeterminate cell histiocytosis Interstitial granulomatous drug reaction Langerhans cell histiocytosis ( ... Primary cutaneous coccidioidomycosis Primary cutaneous histoplasmosis Primary pulmonary coccidioidomycosis Primary pulmonary ... The epidermis contains four cell types: keratinocytes, melanocytes, Langerhans cells, and Merkel cells. Of these, keratinocytes ... pale cell acanthoma) Clear cell squamous cell carcinoma (clear cell carcinoma of the skin) Chronic scar keratosis (chronic ...
NOS M9752/1 Langerhans cell histiocytosis, unifocal Langerhans cell granulomatosis, unifocal Langerhans cell histiocytosis, ... Merkel cell tumor Primary cutaneous neuroendocrine carcinoma M8248/1 Apudoma M8249/3 Atypical carcinoid tumor M8250/1 Pulmonary ... multifocal Langerhans cell histiocytosis, poly-ostotic M9754/3 Langerhans cell histiocytosis, disseminated Langerhans cell ... cell-large cell carcinoma Combined small cell-adenocarcinoma Combined small cell-squamous cell carcinoma M8046/3 Non-small cell ...