*  Succinyl-CoA:3-oxoacid CoA transferase deficiency
Succinyl-CoA:3-oxoacid CoA transferase catalyzes the transfer of coenzyme A from succinyl-coenzyme A to acetoacetate. It can be ...
*  Coenzyme Q10
... , also known as ubiquinone, ubidecarenone, coenzyme Q, and abbreviated at times to CoQ10 /ˌkoʊˌkjuːˈtɛn/, CoQ, or ... "Coenzyme Q10". National Cancer Institute. Bonakdar, Robert Alan; Guarneri, Erminia. "Coenzyme Q10". American Family Physician. ... Bhagavan, H. N.; Chopra, R. K. (Jun 2007). "Plasma coenzyme Q10 response to oral ingestion of coenzyme Q10 formulations". ... "4 Coenzyme Q oxidation reduction reactions in mitochondrial electron transport". In Kagan, V. E.; Quinn, P. J. Coenzyme Q: ...
*  Coenzyme M
... is a coenzyme required for methyl-transfer reactions in the metabolism of methanogens. The coenzyme is an anion with ... The coenzyme is the C1 donor in methanogenesis. It is converted to methyl-coenzyme M thioether, the thioether CH 3SCH 2CH 2SO− ... Methyl-coenzyme M reacts with coenzyme B, 7-thioheptanoylthreoninephosphate, to give a heterodisulfide, releasing methane: CH 3 ... Taylor CD, Wolfe RS (10 August 1974). "Structure and methylation of coenzyme M(HSCH 2CH 2SO 3)". J. Biol. Chem. 249 (15): 4879- ...
*  Coenzyme B
... is a coenzyme required for redox reactions in methanogens. The full chemical name of coenzyme B is 7- ... Coenzyme B reacts with 2-methylthioethanesulfonate (methyl-Coenzyme M, abbreviated CH 3-S-CoM), to release methane in ... methanogenesis: CH 3-S-CoM + HS-CoB → CH 4 + CoB-S-S-CoM This conversion is catalyzed by the enzyme methyl coenzyme M reductase ...
*  Coenzyme F420
... or 8-hydroxy-5-deazaflavin is a coenzyme involved in redox reactions in methanogens, in many Actinobacteria, and ... Coenzyme M Coenzyme B Methanofuran Tetrahydromethanopterin Deppenmeier U (2002). "Redox-driven proton translocation in ... The coenzyme is a substrate for coenzyme F420 hydrogenase, 5,10-methylenetetrahydromethanopterin reductase and ... Selengut JD, Haft DH (2010). "Unexpected abundance of coenzyme F420-dependent enzymes in Mycobacterium tuberculosis and other ...
*  Coenzyme A
... (CoA, CoASH, or HSCoA) is a coenzyme, notable for its role in the synthesis and oxidation of fatty acids, and the ... Coenzyme A is one of five essential coenzymes that is necessary in the reaction mechanism of the citric acid cycle. Its acetyl- ... The coenzyme was named coenzyme A to stand for "activation of acetate." In 1953, Fritz Lipmann won the Nobel Prize in ... Coenzyme A, three ADP, one monophosphate, and one diphosphate are harvested from biosynthesis. New research shows that coenzyme ...
*  Coenzyme Q10 deficiency
... is a deficiency of Coenzyme Q10. It can be associated with COQ2, APTX, PDSS2, PDSS1, CABC1, and COQ9. ... May 2009). "A nonsense mutation in COQ9 causes autosomal-recessive neonatal-onset primary coenzyme Q10 deficiency: a ... 8th Conference of the International Coenzyme Q10 Association. ...
*  Coenzyme-B sulfoethylthiotransferase
It does so by combining the hydrogen donor coenzyme B and the methyl donor coenzyme M. Via this enzyme, most of the natural gas ... In enzymology, coenzyme-B sulfoethylthiotransferase, also known as methyl-coenzyme M reductase (MCR) or most systematically as ... Ermler, U.; Grabarse, W.; Shima, S.; Goubeaud, M.; Thauer, R. K. (1997). "Crystal structure of methyl-coenzyme M reductase: The ... Bobik TA, Olson KD, Noll KM, Wolfe RS (1987). "Evidence that the heterodisulfide of coenzyme M and 7-mercaptoheptanoylthreonine ...
*  Coenzyme F420 hydrogenase
... reduced coenzyme F420 Thus, the two substrates of this enzyme are H2 and coenzyme F420, whereas its product is reduced coenzyme ... In enzymology, a coenzyme F420 hydrogenase (EC 1.12.98.1) is an enzyme that catalyzes the chemical reaction H2 + coenzyme F420 ... The systematic name of this enzyme class is hydrogen:coenzyme F420 oxidoreductase. Other names in common use include 8-hydroxy- ... Baron SF, Ferry JG (1989). "Purification and properties of the membrane-associated coenzyme F420-reducing hydrogenase from ...
*  Hydroxyacyl-Coenzyme A dehydrogenase
... also known as HADH is an enzyme which in humans is encoded by the HADH gene. The HADH gene ... "Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial". Cardiac Organellar Protein Atlas Knowledgebase (COPaKB). Molven A, Matre ... A deficiency is associated with 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. Mutations also cause 3-hydroxyacyl-CoA ... "A preliminary analysis of the segregation of human hydroxyacyl coenzyme A dehydrogenase in human-mouse somatic cell hybrids". ...
*  Succinyl coenzyme A synthetase
... (SCS, also known as succinyl-CoA synthetase or succinate thiokinase or succinate-CoA ligase) is ... Succinyl Coenzyme A Synthetases at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular and Cellular ... 1]. Crystal structures for the E. coli SCS provide evidence that the coenzyme A binds within each α-subunit (within a Rossman ... "Deficiency of the alpha subunit of succinate-coenzyme A ligase causes fatal infantile lactic acidosis with mitochondrial DNA ...
*  Isobutyryl-coenzyme A dehydrogenase deficiency
Isobutyryl-coenzyme A Isobutyryl-coenzyme A dehydrogenase deficiency at NLM Genetics Home Reference. ... Isobutyryl-coenzyme A dehydrogenase deficiency, commonly known as IBD deficiency, is a rare metabolic disorder in which the ... Defects in the ACAD8 gene cause isobutyryl-coenzyme A dehydrogenase deficiency. The ACAD8 gene provides instructions for making ...
*  Methylated-thiol-coenzyme M methyltransferase
... coenzyme M methyltransferase. This enzyme catalyses the following chemical reaction methanethiol + coenzyme M ⇌ {\displaystyle ... Methylated-thiol-coenzyme M methyltransferase (EC 2.1.1.251, mtsA (gene)) is an enzyme with systematic name methylated-thiol: ... Methylated-thiol---coenzyme M methyltransferase at the US National Library of Medicine Medical Subject Headings (MeSH) ... Tallant, T.C.; Paul, L.; Krzycki, J.A. (2001). "The MtsA subunit of the methylthiol:coenzyme M methyltransferase of ...
*  Coenzyme Q - cytochrome c reductase
The coenzyme Q : cytochrome c - oxidoreductase, sometimes called the cytochrome bc1 complex, and at other times complex III, is ... It catalyzes the reduction of cytochrome c by oxidation of coenzyme Q (CoQ) and the concomitant pumping of 4 protons from the ... coenzyme Q: cytochrome C oxidoreductase) is known as the ubiquinone ("Q") cycle. In this cycle four protons get released into ... Calculated positions of bc1 and related complexes in membranes Coenzyme Q-Cytochrome-c Reductase at the US National Library of ...
*  Glucose-6-phosphate dehydrogenase (coenzyme-F420)
... (EC 1.1.98.2, coenzyme F420-dependent glucose-6-phosphate dehydrogenase, F420 ... Glucose-6-phosphate dehydrogenase (coenzyme-F420) at the US National Library of Medicine Medical Subject Headings (MeSH) ... Purwantini, E.; Daniels, L. (1996). "Purification of a novel coenzyme F420-dependent glucose-6-phosphate dehydrogenase from ... This enzyme catalyses the following chemical reaction D-glucose 6-phosphate + oxidized coenzyme F420 ⇌ {\displaystyle \ ...
*  Dihydronicotinamide adenine dinucleotide-coenzyme Q reductase
... may stand for NADH dehydrogenase NADH:ubiquinone reductase (non- ...
*  Coenzyme F420-0:L-glutamate ligase
... (EC 6.3.2.31, CofE-AF, MJ0768, CofE) is an enzyme with systematic name L-glutamate:coenzyme ... Coenzyme F420-0:L-glutamate ligase at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular and ... Li, H.; Graupner, M.; Xu, H.; White, R.H. (2003). "CofE catalyzes the addition of two glutamates to F420-0 in F420 coenzyme ... coenzyme F420-1 This protein catalyses the successive addition of two glutamate residues to cofactor F420 by two distinct and ...
*  3-hydroxyacyl-coenzyme A dehydrogenase deficiency
... (HADH deficiency) is a rare condition that prevents the body from converting ... Mutations in the HADH gene lead to inadequate levels of an enzyme called 3-hydroxyacyl-coenzyme A dehydrogenase. Medium-chain ... People with 3-hydroxyacyl-coenzyme A dehydrogenase deficiency have inadequate levels of an enzyme required for a step that ... Problems related to 3-hydroxyacyl-coenzyme A dehydrogenase deficiency can be triggered by periods of fasting or by illnesses ...
*  Medium-chain acyl-coenzyme A dehydrogenase deficiency
Hegyi, T.; Ostfeld, B.; Gardner, K. (1992). "Medium chain acyl-coenzyme a dehydrogenase deficiency and SIDS". New Jersey ... Wilcken, B.; Hammond, J.; Silink, M. (1994-05-01). "Morbidity and mortality in medium chain acyl coenzyme A dehydrogenase ... "Medium-Chain Acyl-Coenzyme a Dehydrogenase Deficiency". PMID 20301597. Leydiker, K. B.; Neidich, J. A.; Lorey, F.; Barr, E. M ...
*  Short-chain acyl-coenzyme A dehydrogenase deficiency
... (SCADD), also called ACADS deficiency and SCAD deficiency, is an autosomal ... The diagnosis of short-chain acyl-coenzyme A dehydrogenase deficiency is based on the following: Newborn screening test Genetic ... Short-chain acyl-coenzyme A dehydrogenase deficiency affected infants will have vomiting, low blood sugar, a lack of energy ( ... Short-Chain Acyl-Coenzyme A Dehydrogenase Deficiency". Molecular Genetics and Metabolism (Free full text). 95 (4): 195-200. doi ...
*  Reduced nicotinamide adenine dinucleotide-coenzyme Q reductase
... may stand for NADH dehydrogenase NADH:ubiquinone reductase (non- ...
*  Coenzyme F420-1:gamma-L-glutamate ligase
... coenzyme F420-1 ligase (GDP-forming). This enzyme catalyses the following chemical reaction GTP + coenzyme F420-1 + L-glutamate ... Coenzyme F420-1:gamma-L-glutamate ligase (EC 6.3.2.34, F420:gamma-glutamyl ligase, CofE-AF, MJ0768, CofE) is an enzyme with ... Coenzyme F420-1:gamma-L-glutamate ligase at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular and ... I Li, H.; Graupner, M.; Xu, H.; White, R.H. (2003). "CofE catalyzes the addition of two glutamates to F420-0 in F420 coenzyme ...
*  Very long-chain acyl-coenzyme A dehydrogenase deficiency
... (VLCADD) is a fatty-acid metabolism disorder which prevents the body ... Episodes of very long-chain acyl-coenzyme A dehydrogenase deficiency can be triggered by periods of fasting, illness, and ... pain cardiomyopathy Mutations in the ACADVL gene lead to inadequate levels of an enzyme called very long-chain acyl-coenzyme A ...
*  Coenzyme gamma-F420-2:alpha-L-glutamate ligase
... coenzyme alpha-F420-3 The enzyme caps the gamma-glutamyl tail of the hydride carrier coenzyme F420. Li, H.; Xu, H.; Graham, D.E ... coenzyme gamma-F420-2 (ADP-forming). This enzyme catalyses the following chemical reaction ATP + coenzyme gamma-F420-2 + L- ... Coenzyme gamma-F420-2:alpha-L-glutamate ligase (EC 6.3.2.32, MJ1001, CofF protein, gamma-F420-2:alpha-L-glutamate ligase) is an ... Coenzyme gamma-F420-2:alpha-L-glutamate ligase at the US National Library of Medicine Medical Subject Headings (MeSH) Molecular ...
*  Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
Mutations in the HADHA gene lead to inadequate levels of an enzyme called long-chain 3-hydroxyacyl-coenzyme A (CoA) ... Long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency, often shortened to LCHAD deficiency, is a rare autosomal ...