Nogueira, C.; Meehan, T. & O'Donoghue, G. (2014). "Refsum's Disease and Cochlear Implantation". Annals of Otology, Rhinology, ... Adult Refsum disease may be divided into the adult Refsum disease 1 and adult Refsum disease 2 subtypes. The former stems from ... Refsum disease is an autosomal recessive neurological disease that results in the over-accumulation of phytanic acid in cells ... Adult Refsum disease should not be confused with infantile Refsum disease, a peroxisome biogenesis disorder resulting from ...

Wang, D; Zhou, J (2021). "The Kinocilia of Cochlear Hair Cells: Structures, Functions, and Diseases". Frontiers in Cell and ... such as polycystic kidney disease, congenital heart disease, mitral valve prolapse, and retinal degeneration, called ... Its importance to human biology has been underscored by the discovery of its role in a diverse group of diseases caused by the ... In addition, a defect of the primary cilium in the renal tubule cells can lead to polycystic kidney disease (PKD). In another ...

Autoimmune disease is recognized as a cause of cochlear damage. Although rare, autoimmune processes can target the cochlea ... People with HIV/AIDS may develop hearing problems due to the disease itself, medications they take for the disease, or an ... Ménière's disease (endolymphatic hydrops) occurs when there is elevated pressure in the endolymph in the cochlea. Its symptoms ... Charcot-Marie-Tooth disease variant 1E (CMT1E) is noted for demyelinating in addition to deafness. ...

Its areas of expertise include cancer treatment, kidney disease and cochlear implants. It has an affiliated research centre, ...

"Cochlear implantation is safe and effective in patients with MYH9-related disease". Orphanet Journal of Rare Diseases. 9: 100. ... MYH9-related disease. Mutations in MYH9 cause a Mendelian autosomal-dominant disorder known as MYH9-related disease (MYH9-RD). ... February 2014). "MYH9-related disease: a novel prognostic model to predict the clinical evolution of the disease based on ... The disease is transmitted as an autosomal-dominant trait, however, about 35% of index cases are sporadic. Sporadic forms ...

... "cochlear Meniere's disease frequently develops into Meniere's disease." Conversely, A 2006 study from doctors at the House Ear ... Cochlear hydrops (or cochlear Meniere's or cochlear endolymphatic hydrops) is a condition of the inner ear involving a ... Treatment for cochlear hydrops is the same as for Meniere's disease. Currently, no cure exists for either. If a patient has ... It is a form of endolymphatic hydrops and related to Ménière's disease. Cochlear hydrops refers to a case of inner-ear hydrops ...

Occasionally, the very young, the very old, or patients with a significant number of medical diseases at once may remain for ... Media related to Cochlear implants at Wikimedia Commons Cochlear Implants at Curlie Cochlear Implants information from the ... In the past, cochlear implants were only approved for people who were deaf in both ears; as of 2014[update] a cochlear implant ... Critics of cochlear implants from Deaf cultures also assert that the cochlear implant and the subsequent therapy often become ...

"Can we prevent cochlear implant recipients from developing pneumococcal meningitis?". Clinical Infectious Diseases. 46 (1): e1- ... 2010 update by the infectious diseases society of america". Clinical Infectious Diseases. 50 (3): 291-322. doi:10.1086/649858. ... Meningococcal disease occurs in epidemics in areas where many people live together for the first time, such as army barracks ... Other clues on the cause of meningitis may be the skin signs of hand, foot and mouth disease and genital herpes, both of which ...

... patchy localized cochlear disease (with or without fenestral involvement) to either the basal cochlear turn (grade 2A), or the ... Hence, the progression of disease is considerably slowed down and active disease process is arrested. This treatment cannot ... While the disease is considered to be hereditary, its penetrance and the degree of expression is so highly variable that it may ... The cochlear promontory may have a faint pink tinge reflecting the vascularity of the lesion, referred to as the Schwartz sign ...

... used as a measure of disease frequency in epidemiology Cochlear implant Chemical injury syndrome, an increased sensitivity to ...

... cochlear diseases MeSH C09.218.568.217 - endolymphatic hydrops MeSH C09.218.568.217.500 - Ménière's disease MeSH C09.218. ... auditory diseases, central MeSH C09.218.807.186.094 - auditory perceptual disorders MeSH C09.218.807.186.432 - hearing loss, ... 568.315 - labyrinthitis MeSH C09.218.568.900 - vestibular diseases MeSH C09.218.568.900.883 - vertigo MeSH C09.218.705.496 - ... central MeSH C09.218.807.800 - vestibulocochlear nerve diseases MeSH C09.218.807.800.675 - neuroma, acoustic MeSH C09.218. ...

... surgery of the endolymphatic sac for Ménière's disease and cochlear implant surgery. It is more and more common in the United ... Conditions treated by neurotologists include: Vestibular (balance) diseases, such as Ménière's disease and vestibular ... and who treat diseases of the ear with medicine or surgery. In some instances, otology and neurotology are considered together- ... with diseases that affect the ears, balance system, temporal bone, skull base, and related structures of the head and neck. ( ...

Deep brain stimulation (DBS) has been effective at treating movement disorders such as Parkinson's disease, and cochlear ... Immunohistochemical markers showed a surprising presence of hyperphosphorylated tau, an indicator of Alzheimer's disease, near ...

... present in Ménière's disease Cochlear hydrops, a variant of Meniere's disease/Endolymphatic Hydrops without vertigo. Hydrops ...

This includes late deafened adults, cochlear implant users, and people who experience tinnitus, Meniere's disease, hyperacusis ...

Occasionally, if the disease has damaged blood vessels in the ear, cochlear implantation may be used to restore some sense of ... The classic form of the disease was first described by D. G. Cogan in 1945. Cogan syndrome is a rare, rheumatic disease ... Eye diseases, Deafness, Syndromes affecting the cornea, Syndromes affecting hearing, Rare syndromes, Autoimmune diseases). ... For more severe disease, oral corticosteroids may be necessary to reduce the inflammatory response. When large amounts of ...

There is no active congenital venereal disease. Here are the requirements for the Height and Weight standards to qualify for ... No hearing impairment, deformities/disabilities in-ears vestibule-cochlear system. ...

For more significantly impaired hearing, cochlear implants may also be considered. 30-50% of individuals with Norrie disease ... Peripheral vascular disease (PVD) has also been associated with Norrie disease. In a study of 56 patients with Norrie disease, ... Norrie disease is a rare disease and genetic disorder that primarily affects the eyes and almost always leads to blindness. It ... Norrie disease is caused by a mutation in the Norrin cystine knot growth factor gene, also known as the Norrie disease ( ...

Cochlear implant, Celiac or Coeliac disease, Congenital Adrenal Hyperplasia, Congenital heart defect, Cortical blindness, ... medical disciplines and genetic diseases programs. The organization's purpose is to help children with pediatric diseases to " ... Some bears are not for specific diseases but support for children and doctors. These include a bear for bullying and bears for ... Each bear has a specific name, disease, and shirt. Some bears are specialized with crutches, masks, hearing aids, and other ...

... hyperacusis and cochlear hydrops (a rare form of Ménière's disease). Silberman was unsure he could continue singing, and ...

... and Heart diseases. More Cochlear implant surgeries were performed during the period. More Organ implantation surgeries were ... Express News Service (4 October 2012). "43 cochlear implant surgeries performed". New Indian Express. Webdesk (4 April 2021 ...

It separates the cochlear duct from the vestibular duct. It helps to transmit vibrations from fluid in the vestibular duct to ... It may be damaged in Ménière's disease. It is named after the German anatomist Ernst Reissner. The vestibular membrane ... The vestibular membrane may be ruptured by an increase in the pressure of endolymph in the cochlear duct. This may occur in ... This alternative name is named after German anatomist Ernst Reissner (1824-1878). Floor of cochlear duct. Spiral limbus and ...

Generating inner ear organoids containing putative cochlear hair cells from human pluripotent stem cells. Cell Death & Disease ... Li-dong Z, Jun L, Yin-yan H, Jian-he S, Shi-ming Y. Supporting Cells-a New Area in Cochlear Physiology Study. J Otol. 2008 Jun ... Cochlear implants are a more invasive treatment that bypass the hair cells completely by sending electrical signals from the ... The cochlear implant involves a surgically implanted electrode array and an external device that processes sound. All studied ...

... and the microstimulation used in the treatments of Parkinson's disease (Deep Brain Stimulation) and deafness (Cochlear implants ...

... sensory or cognitive modality that might have been damaged as a result of an injury or a disease. Cochlear implants provide an ... Cochlear implants have been very successful among these three categories. Today the Advanced Bionics Corporation, the Cochlear ... Cochlear and brainstern auditory prostheses "neural interface for hearing restoration: Cochlear and brain stem implants". ... Proceedings of the IEEE 96:1076-84 J. K. Niparko and B. W. Wilson, "History of cochlear implants," in Cochlear Implants: ...

Feldman, Gerald L; Weaver, D. D; Lovrien, E. W (1977). "The Fetal Trimethadione Syndrome". American Journal of Diseases of ... "Timed conditional null of connexin26 in mice reveals temporary requirements of connexin26 in key cochlear developmental events ... Onkal, R; Djamgoz, M. B (2009). "Molecular pharmacology of voltage-gated sodium channel expression in metastatic disease: ... Disease. 4 (6): e652. doi:10.1038/cddis.2013.174. PMC 3698542. PMID 23744352. Pei, L; Wiser, O; Slavin, A; Mu, D; Powers, S; ...

... and kidney and heart diseases. Forty-three Cochlear implant surgeries were performed under a Cochlear implant scheme for ... Express News Service (4 October 2012). "43 cochlear implant surgeries performed". New Indian Express. Webdesk (4 April 2021 ...

The corresponding subtypes of MD are called vestibular MD, showing symptoms of vertigo, and cochlear MD, showing symptoms of ... Ménière's disease (MD) is a disease of the inner ear that is characterized by potentially severe and incapacitating episodes of ... Finally in 1995, the list was again altered to allow for degrees of the disease: Certain - Definite disease with ... Ménière's disease usually starts confined to one ear; it extends to both ears in about 30% of cases. People may start out with ...

This cochlear synaptopathy has been seen after prolonged noise exposure in both primate and non-primate models. Two possible ... Some diseases of unknown etiology have been proposed to be synaptopathies. Examples include autism spectrum disorder and ... Age-related cochlear synaptic and neural degeneration has also been demonstrated in mice. Molecules such as FMRP1 act as ... A synaptopathy is a disease of the brain, spinal cord or peripheral nervous system relating to the dysfunction of synapses. ...

"Free cochlear implants at Govt ENT Hospital soon". Times of India. 10 April 2015. Retrieved 24 July 2019. "treatment". ... Government ENT Hospital, which serves ear, nose and throat Diseases across Coastal Andhra, is located in Pedda Waltair, ... The hospital started a cochlear implant surgery programme in 2015. The hospital serves not only in Andhra Pradesh state it also ...