Mitochondrial ProteinsMitochondriaSirtuin 3Mitochondrial Membrane Transport ProteinsDNA, MitochondrialElectron Transport Complex IVMitochondria, LiverMitochondrial MembranesIron-Binding ProteinsSaccharomyces cerevisiaeFriedreich AtaxiaOxidative PhosphorylationMitochondria, HeartProtein TransportMitochondria, MuscleProtein BiosynthesisIntracellular MembranesMolecular Sequence DataSaccharomyces cerevisiae ProteinsChloramphenicolMitochondrial DiseasesAmino Acid SequenceMembrane Transport ProteinsCell RespirationMembrane ProteinsFungal ProteinsProtein PrecursorsMitochondrial ADP, ATP TranslocasesNeurospora crassaProteomeOxygen ConsumptionVoltage-Dependent Anion ChannelsGenes, MitochondrialMutationMitochondrial Proton-Translocating ATPasesProteomicsElectrophoresis, Gel, Two-DimensionalCarrier ProteinsElectron TransportOxidative StressProteinsNADH DehydrogenaseCitrate (si)-SynthaseNeurosporaProton-Translocating ATPasesBase SequenceBiological TransportElectron Transport Complex IProtein Sorting SignalsGenes, FungalAdenosine TriphosphateSubmitochondrial ParticlesHSP70 Heat-Shock ProteinsCytosolAdenine Nucleotide Translocator 2Uncoupling AgentsCytochromes cRNA, Transfer, LeuElectron Transport Chain Complex ProteinsRNA, MessengerMembrane Potential, MitochondrialGenome, MitochondrialOxidation-ReductionProtein Processing, Post-TranslationalSuccinate DehydrogenaseOrnithine CarbamoyltransferaseEthidiumCytochrome c GroupReactive Oxygen SpeciesSequence AlignmentMitochondrial DegradationOxytetracyclineSubcellular FractionsApoptosisCarbonyl Cyanide m-Chlorophenyl HydrazoneSequence Homology, Amino AcidEnergy MetabolismCell NucleusModels, BiologicalElectrophoresis, Polyacrylamide GelBlotting, WesternCytochromesCycloheximideVoltage-Dependent Anion Channel 1Heat-Shock ProteinsMolecular ChaperonesKineticsProtein BindingCardiolipinsProtein CarbonylationAdenosine TriphosphatasesRNAIron-Sulfur ProteinsMuscle, SkeletalMitochondrial SizeAntimycin AProtein Synthesis InhibitorsTetrahydrofolate DehydrogenaseCell LineLeucine