Menkes Kinky Hair SyndromeDuodenoscopyCrohn DiseaseHepatolenticular DegenerationCation Transport ProteinsCopperAdenosine TriphosphatasesMetallochaperonesCeruloplasminRats, Inbred LECBrain Diseases, MetabolicMetal Metabolism, Inborn ErrorsCarrier ProteinsRecombinant Fusion ProteinsDimethyldithiocarbamateTrientineMutationMolecular Sequence DataPenicillamineRats, Mutant StrainsExtrapyramidal TractsBiological TransportDNA Mutational AnalysisMolecular ChaperonesSweat GlandsDroxidopaCutis LaxaAmino Acid SequenceEhlers-Danlos SyndromeChelation TherapyBase SequenceFluorescent Antibody Technique, IndirectSweatPhenotypeChelating AgentsGolgi ApparatusChromosomes, Human, Pair 13DNA PrimersMethoxyhydroxyphenylglycol3,4-Dihydroxyphenylacetic AcidProtein TransportCubital Tunnel SyndromeCell LineSweatingDopamine beta-HydroxylaseBinding SitesDisease Models, AnimalDNA, ComplementaryHomeostasisMice, Mutant StrainsFibroblastsSequence DeletionGenetic Complementation TestCloning, Molecular