Lysosomal Storage DiseasesLysosomal Storage Diseases, Nervous Systemalpha-MannosidosisMucopolysaccharidosis VIIGlycogen Storage Disease Type ILysosomesGaucher DiseaseFucosidosisGlycogen Storage DiseaseMucopolysaccharidosis IGlycogen Storage Disease Type IIAspartylglucosaminuriaMucolipidosesEnzyme Replacement TherapySphingolipidosesMucopolysaccharidosis IIIAspartylglucosylaminaseLeukodystrophy, MetachromaticCerebroside-SulfataseIduronidaseSandhoff DiseaseGangliosidosis, GM1Cholesterol Ester Storage DiseaseGangliosidoses, GM2GlucosylceramidaseMucopolysaccharidosis VIalpha-GalactosidaseNeuronal Ceroid-LipofuscinosesMetabolism, Inborn ErrorsGlycogen Storage Disease Type IVGlycogen Storage Disease Type IIIMucopolysaccharidosesFabry Diseasealpha-GlucosidasesGlucuronidaseN-Acetylgalactosamine-4-SulfataseNiemann-Pick DiseasesMucopolysaccharidosis IVbeta-N-Acetylhexosaminidasesbeta-MannosidosisPlant PoisoningTay-Sachs DiseaseHexosaminidase BMalvaceaeWolman DiseaseGenetic TherapyG(M2) Gangliosidealpha-MannosidaseSialic Acid Storage DiseaseGangliosidosesLeukodystrophy, Globoid Cellbeta-GlucosidaseSerine ProteasesChondro-4-SulfataseDependovirusCystinosisGlycogen Storage Disease Type VIIPsychosineHexosaminidase ADisease Models, AnimalMannosephosphatesGlucosylceramidesGenetic VectorsMultiple Sulfatase Deficiency DiseaseGlycosaminoglycansNiemann-Pick Disease, Type CTransient Receptor Potential ChannelsFibroblastsMucopolysaccharidosis IILiverMannosidasesDipeptidyl-Peptidases and Tripeptidyl-PeptidasesGlycosphingolipidsBrainGlucose-6-PhosphataseMutationMice, KnockoutTRPM Cation ChannelsCentral Nervous SystemAutophagySphingomyelin PhosphodiesteraseAcetylglucosaminidasePhenotypeGlycogen Storage Disease Type VCat DiseasesMice, Mutant StrainsLipid Metabolism, Inborn ErrorsGlycogen Debranching Enzyme SystemCarbohydrate Metabolism, Inborn ErrorsHydrolasesGlycogen Storage Disease Type VIDrug Storage1-DeoxynojirimycinIduronate SulfataseMolecular Sequence DataLipidosesImino Sugarsbeta-MannosidaseGene Transfer Techniquesbeta-Galactosidase