Cathepsin ALysosomal Storage DiseasesCarboxypeptidasesLysosomesNeuraminidasebeta-GalactosidaseGangliosidosis, GM1Mucolipidosesbeta-N-AcetylhexosaminidasesIsoflurophateCathepsinsGlucuronidaseMannosephosphatesAcetylglucosaminidaseReceptor, IGF Type 2Cathepsin DAcid PhosphataseMicroscopy, ImmunoelectronHexosaminidasesGlycoproteinsalpha-MannosidaseFibroblastsCerebroside-SulfataseArylsulfatasesMolecular WeightMannosidasesMolecular Sequence DataTransfectionCell LineTransferases (Other Substituted Phosphate Groups)Amino Acid SequenceElectrophoresis, Polyacrylamide Gelalpha-L-FucosidaseKineticsHydrolasesbeta-GlucosidaseSulfatasesHexosephosphatesMutagenesis, Site-DirectedGalactosidasesalpha-GalactosidaseZymosanIduronidaseGlucosidasesCathepsin BGlucosylceramidaseGlycoside HydrolasesProtective AgentsAmmonium ChlorideGaucher DiseaseMucopolysaccharidosis Ialpha-GlucosidasesCathepsin LEndocytosisCytochalasin BPinocytosisGlycogen Storage Disease Type IILiverOligosaccharidesFabry DiseaseMethylmannosidesN-Acetylgalactosamine-4-SulfataseGalactosylceramidasePhagocytosisAspartylglucosylaminaseMannosyl-Glycoprotein Endo-beta-N-AcetylglucosaminidaseGangliosidosesCathepsin CNeutrophilsCells, CulturedDictyosteliumMacrophagesProtective ClothingGolgi ApparatusMicroscopy, ElectronChondro-4-SulfataseMucopolysaccharidosis IVMannoseL-Lactate DehydrogenaseCell CompartmentationLeukodystrophy, Globoid CellMucopolysaccharidosesCell FractionationEnzyme Replacement TherapyDipeptidyl-Peptidases and Tripeptidyl-PeptidasesMice, Inbred C57BLTime FactorsIduronate SulfataseHydrogen-Ion ConcentrationHexosaminidase AEnzyme PrecursorsLeukodystrophy, MetachromaticMucopolysaccharidosis IIThiolester HydrolasesAntipainHistocytochemistryEsterasesDisease Models, AnimalTay-Sachs DiseaseMuramidase