Ketoglutarate Dehydrogenase ComplexPyruvate Dehydrogenase ComplexKetoglutaric AcidsKetone OxidoreductasesDihydrolipoamide DehydrogenaseDihydrolipoyllysine-Residue Acetyltransferase3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)Keto AcidsPyruvate Dehydrogenase (Lipoamide)Pyruvate Dehydrogenase Complex Deficiency DiseaseUDPglucose-Hexose-1-Phosphate UridylyltransferaseTransaminasesSaccharopine DehydrogenasesOxaloacetatesCoenzyme AThioctic AcidOrnithineGlutaratesThiamine PyrophosphateL-Lactate DehydrogenasePII Nitrogen Regulatory ProteinsMultienzyme ComplexesAlcohol DehydrogenaseKinetics