Isovaleryl-CoA dehydrogenase, mitochondrial. General function:. Involved in acyl-CoA dehydrogenase activity. Specific function: ... 5. Long-chain specific acyl-CoA dehydrogenase, mitochondrial. General function:. Involved in acyl-CoA dehydrogenase activity. ... 6. Short-chain specific acyl-CoA dehydrogenase, mitochondrial. General function:. Involved in acyl-CoA dehydrogenase activity. ... 7. Medium-chain specific acyl-CoA dehydrogenase, mitochondrial. General function:. Involved in acyl-CoA dehydrogenase activity ...
S)-3-Hydroxyisobutyryl-CoA. Show. HMDB0001057. 3-Methylglutaconyl-CoA. Show. HMDB0001113. Isovaleryl-CoA. Show. ... 2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency. HMDB ID. Name. Pathway. HMDB0000019. alpha-Ketoisovaleric acid. Show. ...