Cystic Fibrosis Transmembrane Conductance RegulatorCystic FibrosisChloride ChannelsChloridesMice, Inbred CFTRMutationEpithelial CellsIon TransportColforsinIon Channel GatingNasal MucosaGold CompoundsIodidesCell LineCyclic AMPRespiratory Mucosaortho-AminobenzoatesAminophenolsAdenosine TriphosphateMembrane ProteinsAnionsCricetinaeCyclic AMP-Dependent Protein KinasesPatch-Clamp TechniquesBicarbonatesCell Membrane4,4'-Diisothiocyanostilbene-2,2'-Disulfonic AcidMolecular Sequence Data1-Methyl-3-isobutylxanthineProtein Structure, TertiaryChlorineSweatMembrane PotentialsEosine I BluishCHO CellsNitrobenzoatesBronchiTransfectionGlyburideAdenylyl ImidodiphosphateAmino Acid SequenceTracheaGenisteinMesylatesEpithelial Sodium ChannelsBiotinylationAmilorideEpitheliumThiazolidinesProtein FoldingSodium-Hydrogen AntiporterOocytesElectric ConductivityRecombinant ProteinsElectrophysiologyVas DeferensEndoplasmic ReticulumCells, CulturedSequence DeletionBase SequenceProtein BindingLungChloride-Bicarbonate AntiportersMutagenesis, Site-DirectedProtein TransportXenopus laevisBinding SitesKineticsPancreatic DuctsSweat GlandsHSC70 Heat-Shock ProteinsXenopusPseudomonas InfectionsRNA, MessengerTetramisoleCyanatesPhosphorylationPseudomonas aeruginosaNucleotidesAntiportersCOS CellsMutation, MissenseMucociliary ClearanceExocrine GlandsBiological TransportGene ExpressionRecombinant Fusion ProteinsFibrosisEpithelial Sodium Channel BlockersAmino Acid SubstitutionPoint MutationSodium-Potassium-Chloride SymportersGene Expression RegulationEndocytosisPhenylbutyratesBenzoatesProtein Structure, SecondaryExonsSodium ChannelsATP-Binding Cassette Transporters