Congenital HyperinsulinismHyperinsulinismSulfonylurea ReceptorsReceptors, DrugPotassium Channels, Inwardly RectifyingDiazoxidePancreatectomyATP-Binding Cassette TransportersKATP ChannelsHypoglycemiaGlutamate DehydrogenaseInsulinPotassium ChannelsInsulin-Secreting CellsInfant, NewbornMutationMutation, MissenseHeterozygoteDiagnostic Techniques, EndocrineHyperammonemia