GangliosidosesLipidosesHexosaminidase AHexosaminidase BHexosaminidasesbeta-N-AcetylhexosaminidasesTay-Sachs DiseaseG(M2) GangliosideSandhoff DiseaseG(M2) Activator ProteinAcetylglucosaminidaseInterleukin-1betaChromosomes, Human, 4-5Sphingolipid Activator Proteinsbeta 2-MicroglobulinMolecular Sequence DataHymecromoneIsoenzymesGangliosidoses, GM2Electrophoresis, Starch GelAmino Acid SequenceReceptors, Adrenergic, betaIntegrin beta3SaposinsChromosomes, Human, 13-15Polymerase Chain ReactionMacromolecular SubstancesAcetylglucosamineBase SequenceKineticsCell LineLysosomesReceptors, Antigen, T-Cell, alpha-betaHeterozygote DetectionTransforming Growth Factor betaCells, CulturedIsoelectric FocusingMolecular WeightProtein ConformationRNA, MessengerElectrophoresis, Polyacrylamide GelHemoglobins, AbnormalMutationIntegrin alpha5beta1Integrin beta4Integrin beta ChainsGangliosidosis, GM1