ArylsulfatasesSulfatasesCerebroside-SulfataseSulfuric AcidsSulfatesEstersChondro-4-SulfataseSulfuric Acid EstersLeukodystrophy, MetachromaticN-Acetylgalactosamine-4-SulfataseDehydroepiandrosteroneMucopolysaccharidosis VIOligosaccharidesHeparitin SulfateCarbohydrate SequenceChromatography, Thin LayerHydrolysisMolecular Sequence DataSteryl-SulfataseTyramineDermatan SulfateCholesterol EstersHeparan Sulfate ProteoglycansSulfoglycosphingolipidsKeratan SulfateChondroitin Sulfate ProteoglycansMucopolysaccharidosis IVMucopolysaccharidosesLysosomesDextran SulfateGlycosaminoglycansChondroitin SulfatesSaposinsKlebsiellaDiazomethanePhotofluorographySphingolipid Activator ProteinsEnzyme RepressionSodium Dodecyl SulfateSulfurGalactolipidsMonoamine OxidaseKineticsMagnesium SulfateAmmonium SulfateAmino Acid SequenceHydrogen-Ion ConcentrationChondrodysplasia PunctataElectrophoresis, Polyacrylamide GelMolecular WeightAutacoidsSulfotransferasesChromatography, Ion ExchangeCopper SulfateProteoglycansNG-Nitroarginine Methyl EsterMycobacterium scrofulaceumBase SequenceImmunochemistryCitrobacterZinc SulfateChondroitinChemistryDehydroepiandrosterone SulfateChemical PhenomenaCloning, MolecularGlucuronidaseFibroblastsCells, CulturedMutationLiverCholesterol Ester Transfer ProteinsAmmonium ChlorideCell LineChromatographyThiosulfatesAcid PhosphataseCalcium SulfateSubstrate SpecificityIsoelectric FocusingCathepsin DImmunodiffusionTransferases (Other Substituted Phosphate Groups)Chromatography, GelNitrosoguanidinesEnzyme Replacement TherapyGenesDisaccharidesMannosyl-Glycoprotein Endo-beta-N-AcetylglucosaminidaseMethionineChromatography, High Pressure LiquidCarboxylic Ester HydrolasesChondroitinases and Chondroitin LyasesLysosomal Storage DiseasesHeparinSulfate AdenylyltransferaseCricetinaeChemical PrecipitationGlycosylationRestriction Mapping