alpha 1-Antitrypsinalpha 1-Antitrypsin DeficiencyPulmonary EmphysemaPancreatic Elastasealpha 1-AntichymotrypsinEmphysemaTrypsin InhibitorsLeukocyte ElastaseReceptors, Adrenergic, alphaHypoxia-Inducible Factor 1, alpha SubunitSerpinsSerine Proteinase InhibitorsPhenotypeBase Sequencealpha7 Nicotinic Acetylcholine ReceptorMolecular Sequence DataIsoelectric FocusingLiverIntegrin alpha3beta1Integrin alpha4Integrin alpha6MutationRecombinant ProteinsIntegrin alpha5beta1OrosomucoidProtein BindingIntegrin alpha4beta1Interleukin-1alphaElectrophoresis, Polyacrylamide GelLiver DiseasesKineticsIntegrin alpha2beta1Binding SitesHepatocyte Nuclear Factor 1-alphaAmino Acid SequenceReceptors, Adrenergic, alpha-1HaptoglobinsProtein ConformationIntegrin alpha5Integrin alpha1beta1Receptors, Adrenergic, alpha-2ChymotrypsinIntegrin alpha6beta1Protein-Losing EnteropathiesMacroglobulinsGene Expression RegulationTransfectionIntegrin alpha6beta4Integrin alpha ChainsEndoplasmic ReticulumIntegrinsAlbuminsBlood ProteinsIntegrin alpha1DNAalpha-MacroglobulinsTrypsinHeterozygoteHomozygoteAlpha RhythmProtein C InhibitorModels, MolecularProprotein Convertase 5Cloning, MolecularPancreatinIntegrin alpha3FurinAllelesMice, Inbred C57BL