... and ESS-Binding Proteins thereby Causing Missplicing and Multiple Acyl-CoA Dehydrogenation Deficiency. Olsen, R. K. J., Brøner ...
... enoyl-coenzyme A reductase; unsaturated acyl coenzyme A reductase; butyryl coenzyme A dehydrogenase; short-chain acyl CoA ... Reaction: an acyl-[acyl-carrier protein] + NADP+ = a trans-2,3-dehydroacyl-[acyl-carrier protein] + NADPH + H+. Other name(s): ... Glossary: a very-long-chain acyl-CoA = an acyl-CoA thioester where the acyl chain contains 23 or more carbon atoms.. Other name ... Reaction: a meromycolyl-[acyl-carrier protein] + NAD+ = a trans-Δ2-meromycolyl-[acyl-carrier protein] + NADH + H+. Glossary: ...
Cpt1 catalyzes the transfer of the acyl group from coenzyme A to carnitine. ... For long-chain acyl-CoA, HPLC analysis was performed using the LC20 UFLC system (SHIMADU, Japan) composed of a column oven and ... Figure S6. LC-MS results of acyl-CoAs. (a) Positive ion electrospray scan mass spectra of the malonyl-CoA standard. (b) ... For short-chain acyl-CoA, high-pressure liquid chromatography (HPLC) analysis was performed using the Surveyor LC system ( ...
keywords = "2-Methylbutyryl coenzyme A dehydrogenase, Acyl-CoA dehydrogenase, Branched chain acyl coenzyme A dehydrogenase, ... Short/branched chain acyl-CoA dehydrogenase (SBCAD) deficiency, also known as 2-methylbutyryl-CoA dehydrogenase deficiency, is ... N2 - Short/branched chain acyl-CoA dehydrogenase (SBCAD) deficiency, also known as 2-methylbutyryl-CoA dehydrogenase deficiency ... AB - Short/branched chain acyl-CoA dehydrogenase (SBCAD) deficiency, also known as 2-methylbutyryl-CoA dehydrogenase deficiency ...
Acyl-coenzyme A thioesterase THEM4. 0.03. OrthoFinder. Functional Annotation. *GO. *Predicted GO ...
Acyl-coenzyme A dehydrogenase. General function:. Involved in acyl-CoA dehydrogenase activity. Specific function:. Catalyzes ... the dehydrogenation of acyl-CoA. Gene Name:. fadE. Uniprot ID:. Q47146 Molecular weight:. 89224. Reactions. An acyl-CoA + FAD ...
The amino acid carnitine is required for the transport of long-chain fatty acyl coenzyme A (CoA) esters into myocyte ...
Description acyl-Coenzyme A oxidase 2, branched chain. p-Value. q-Value. period. phase. ...
Full Name: Cytosolic acyl coenzyme A thioester hydrolase O-GlcNAc Score: 1 References ...
Peroxisomal acyl-coenzyme A oxidase 1. MNPDLRRERDSASFNPELLTHILDGSPEKTRRRREIENMILNDPDFQHED.... unknown. UDP-N- ... The coenzyme of various aerobic dehydrogenases, e.g., D-amino acid oxidase and L-amino acid oxidase. (Lehninger, Principles of ... Medium-chain specific acyl-CoA dehydrogenase, mitochondrial. MAAGFGRCCRVLRSISRFHWRSQHTKANRQREPGLGFSFEFTEQQKEFQA.... unknown. D- ... Short-chain specific acyl-CoA dehydrogenase, mitochondrial. MAAALLARASGPARRALCPRAWRQLHTIYQSVELPETHQMLLQTCRDFAE.... unknown. L- ...
1) Product Images from "Structural basis of the activation of TRPV5 channels by long-chain acyl-Coenzyme-A" ... Article Title: Structural basis of the activation of TRPV5 channels by long-chain acyl-Coenzyme-A ... Article Title: Structural basis of the activation of TRPV5 channels by long-chain acyl-Coenzyme-A ... Article Title: Structural basis of the activation of TRPV5 channels by long-chain acyl-Coenzyme-A ...
Medium-chain acyl-coenzyme A dehydrogenase deficiency: Six cases in the Chinese population. Li Yanhan, et al. Pediatrics ... Medium-chain acyl-coenzyme A dehydrogenase deficiency From NCATS Genetic and Rare Diseases Information Center ... Sudden neonatal death in individuals with medium-chain acyl-coenzyme A dehydrogenase deficiency: limit of newborn screening. ... Analysis of gene mutations of medium-chain acyl-coenzyme a dehydrogenase deficiency (MCADD) by next-generation sequencing in ...
Deficiency of acyl coenzyme a:diacylglycerol acyltransferase 1 increases leptin sensitivity in murine obesity models. ... Dissociation of obesity and impaired glucose disposal in mice overexpressing acyl coenzyme a:diacylglycerol acyltransferase 1 ... Leptin modulates the effects of acyl CoA:diacylglycerol acyltransferase deficiency on murine fur and sebaceous glands. J Clin ... Increased insulin and leptin sensitivity in mice lacking acyl CoA:diacylglycerol acyltransferase 1. J Clin Invest. 2002 Apr; ...
acyl-CoA thioesterase 1 [Source:HGNC Symbo.... ACOT12. 134526. ACOT12. acyl-CoA thioesterase 12 [Source:HGNC Symb.... ... The chemical reactions and pathways involving coenzymes, any of various nonprotein organic cofactors that are required, in ...
Name/Description: acyl-Coenzyme A dehydrogenase, very long chain. Entrez ID: 11370 ...
AMACR (ALPHA METHYL ACYL COENZYME A RACEMASE)**. 13000.0. ANNEXIN-1**. 13000.0. ARGINASE-1**. 13000.0. ...
ACYL-COENZYME A:CHOLESTEROL ACYLTRANSFERASE 1,ACAT .... ... More 6L48_B P20839 SOAT1, ACACT, ACACT1, ACAT, ACAT1, SOAT, STAT. ...
Newborn screening information for short-chain acyl-CoA dehydrogenase deficiency ... Conditions Short-Chain Acyl-CoA Dehydrogenase Deficiency Short-chain acyl-CoA dehydrogenase deficiency (SCAD) is a condition in ... Short-chain acyl-CoA dehydrogenase specializes at breaking down short length fatty acid chains for energy. If you have a ... Short-chain acyl-CoA dehydrogenase deficiency (SCAD) is estimated to affect one in 40,000 to 100,000 newborns. ...
Medium-chain acyl-coenzyme A dehydrogenase deficiency. Medium-chain acyl-coenzyme A dehydrogenase (MCAD) is one of the enzymes ... Multiple acyl-CoA dehydrogenase deficiency. Multiple acyl-CoA dehydrogenase deficiency (MADD) represents a clinical spectrum in ...
Coenzyme A Ligases Medicine & Life Sciences 100% * Cholates Medicine & Life Sciences 99% ... ACS catalyzes the formation of acyl-CoA from fatty acid, and acyl-CoA is utilized for triglyceride formation in liver. ACS has ... ACS catalyzes the formation of acyl-CoA from fatty acid, and acyl-CoA is utilized for triglyceride formation in liver. ACS has ... ACS catalyzes the formation of acyl-CoA from fatty acid, and acyl-CoA is utilized for triglyceride formation in liver. ACS has ...
A publicly available article also appearing in PubMed about Medium-Chain Acyl-CoA Dehydrogenase Deficiency ... Medium-chain acyl-coenzyme A dehydrogenase deficiency: clinical course in 120 affected children. The Journal of pediatrics. ... Madsen KL, Preisler N, Orngreen MC, Andersen SP, Olesen JH, Lund AM, Vissing J. Patients with medium-chain acyl-coenzyme a ... Medium-Chain Acyl-Coenzyme A Dehydrogenase Deficiency. GeneReviews(®). 1993:(): [PubMed PMID: 20301597] ...
Short-Chain Acyl-CoA Dehydrogenase Deficiency. Medium-Chain Acyl-Coenzyme A Dehydrogenase Deficiency. Arginase Deficiency. Beta ... Very Long-Chain Acyl-Coenzyme A Dehydrogenase. X-linked Agammaglobulinemia. Ataxia-Telangiectasia ATM. Gyrate Atrophy of ...
Short chain acyl coenzyme A dehydrogenase deficiency. 4. Beckwith-Wiedemann syndrome (thought to be due to hyperinsulinism but ...
Medium-chain acyl-coenzyme A dehydrogenase deficiency: Six cases in the Chinese population. Li Yanhan, et al. Pediatrics ... Medium-chain acyl-coenzyme A dehydrogenase deficiency From NCATS Genetic and Rare Diseases Information Center ... Sudden neonatal death in individuals with medium-chain acyl-coenzyme A dehydrogenase deficiency: limit of newborn screening. ... Analysis of gene mutations of medium-chain acyl-coenzyme a dehydrogenase deficiency (MCADD) by next-generation sequencing in ...
... fatty acyl-coenzyme (Co)A reductase 1.. Assuntos. Antioxidantes/farmacologia , Dermatite Atópica/dietoterapia , Suplementos ...
Glycogen Resynthesis and Recovery from Exercise: Effects of Very-Long Chain Acyl-Coenzyme, A Dehydrogenase Deficiency. Kyle E. ...
Citrate lyase, acyl carrier (gamma) subunit; Covalent carrier of the coenzyme of citrate lyase; Belongs to the CitD family. ... Citrate lyase, acyl carrier (gamma) subunit; Covalent carrier of the coenzyme of citrate lyase; Belongs to the CitD family. ... Citrate lyase, acyl carrier (gamma) subunit; Covalent carrier of the coenzyme of citrate lyase; Belongs to the CitD family. ... Citrate lyase, acyl carrier (gamma) subunit; Covalent carrier of the coenzyme of citrate lyase; Belongs to the CitD family. ...
ACADSB Acyl-coenzyme A dehydrogenase, short/branched chain ADAMTS9-AS2 ADAM metallopeptidase with thrombospondin type 1 motif 9 ...
Human acyl-CoA thioesterase 1 ELISA Kit;Human CTE-I ELISA Kit;Human CTE-Ib ELISA Kit;Human inducible cytosolic acyl-coenzyme A ... thioester hydrolase ELISA Kit;Human long chain acyl-CoA thioester hydrolase ELISA Kit;Human long chain acyl-CoA hydrolase ELISA ... Kit;Human CTE1 ELISA Kit;Human ACH2 ELISA Kit;Human CTE-1 ELISA Kit;Human LACH2 ELISA Kit;Human acyl-coenzyme A thioesterase 1 ...
Acyl Coenzyme A Oxidase Medicine and Dentistry 66% * Acyl-CoA Oxidase Biochemistry, Genetics and Molecular Biology 66% ... acyl- CoA oxidase 1 (ACOX1), fatty acid binding protein 4 (FABP4,) and perilipin 1 (PLIN1)] was performed using a tissue ... acyl- CoA oxidase 1 (ACOX1), fatty acid binding protein 4 (FABP4,) and perilipin 1 (PLIN1)] was performed using a tissue ... acyl- CoA oxidase 1 (ACOX1), fatty acid binding protein 4 (FABP4,) and perilipin 1 (PLIN1)] was performed using a tissue ...