Major aortopulmonary collateral arteries (or MAPCAs) are arteries that develop to supply blood to the lungs when native pulmonary circulation is underdeveloped. Instead of coming from the pulmonary trunk, supply develops from the aorta and other systemic arteries. Major aortopulmonary collateral arteries (MAPCAs) develop early in embryonic life but regress as the normal pulmonary arteries (vessels that will supply deoxygenated blood to the lungs) develop. In certain heart conditions the pulmonary arteries do not develop. The collaterals continue to grow, and can become the main supply of blood to the lungs. Though it is usually associated with congenital heart diseases with decreased pulmonary blood flow like tetralogy of Fallot or pulmonary atresia it may be seen sometimes in isolation i.e. not associated with any congenital heart disease in that case it is termed as isolated aortopulmonary collateral artery. In these cases it may be one of the cause of congestive cardiac failure in neonates. ...

Double outlet right ventricle is a rare birth defect of the heart.. The heart has 2 upper collecting chambers (right and left atrium), 2 lower pumping chambers (right and left ventricle), 1 artery leaving the right ventricle (pulmonary artery) and 1 leaving the left ventricle (aorta).. In a normal heart, the aorta leaves the left ventricle, carrying oxygen-rich (red) blood to the body. The pulmonary artery leaves the right ventricle, carrying oxygen-poor (blue) blood to the lungs.. In double outlet right ventricle, both of the hearts outlets - the pulmonary artery and the aorta - exit abnormally from the right ventricle. This causes the oxygen-rich and oxygen-poor blood to mix together before leaving the heart.. Many kinds of heart defects fall into the category of double outlet right ventricle. They all share the feature that the aorta and pulmonary artery both exit from the right ventricle. In addition, other parts of the heart may be different.. In double outlet right ventricle, there is ...

TY - JOUR. T1 - Detection of major aortopulmonary collateral arteries by transesophageal echocardiography in pulmonary atresia with ventricular septal defect. AU - Ma, Matthew Huei Ming. AU - Hwang, Juey Jen. AU - Lin, Jiunn Lee. AU - Shyu, Kou Gi. AU - Chen, Wei Jan. AU - Kuan, Peiliang. AU - Lien, Wen Pin. PY - 1993/1/1. Y1 - 1993/1/1. UR - http://www.scopus.com/inward/record.url?scp=0027377624&partnerID=8YFLogxK. UR - http://www.scopus.com/inward/citedby.url?scp=0027377624&partnerID=8YFLogxK. U2 - 10.1016/0002-8703(93)90684-2. DO - 10.1016/0002-8703(93)90684-2. M3 - Article. C2 - 8237775. AN - SCOPUS:0027377624. VL - 126. SP - 1227. EP - 1229. JO - American Heart Journal. JF - American Heart Journal. SN - 0002-8703. IS - 5. ER - ...

Double outlet right ventricle surgery is a procedure that fixes a type of heart malformation called double outlet right ventricle (DORV).

Retraining the morphological left ventricle in transposition of the great arteries has been successfully reported in infancy, while older age seems to be a contraindication. A 23-year-old woman with ¿S,D,D¿ transposition of the great arteries and ventricular septal defect developed severe right systemic ventricular dysfunction 22 years after Mustard procedure and ventricular septal defect closure. Hemodynamic investigation revealed moderate pulmonary hypertension and preserved left ventricular function. A pulmonary artery band was applied to obtain a left-right ventricular pressure ratio of 0.91. Her postoperative course was characterized by biventricular failure, treated effectively with inotropic support. Six months later, she underwent a Mustard baffle takedown and arterial switch procedure. Her postoperative course was uneventful. She was discharged home on postoperative day 15. At 24-months follow-up, she is in excellent clinical condition; echocardiographic evaluation shows good left ventricular

D-TGA is one of the most common forms of congenital heart disease, constituting 5% to 7% of cardiac malformations. Since the original description of the arterial switch operation in 1975 by Jatene et al,9 the arterial switch operation has become the procedure of choice for repair of D-TGA with intact ventricular septum or ventricular septal defect. Because of the rapid decline in the work capacity of the left ventricle after birth in children with D-TGA with an intact ventricular septum or a small ventricular septal defect, anatomic correction with the arterial switch operation must be performed during the first weeks of life.10 This practice provides a uniformity of age at repair that is rare among congenital heart defects. Furthermore, the arterial switch operation is performed with extremely low early mortality rates, negligible late mortality rates, and infrequent need for reoperation.1,11 We previously reported that neurocognitive performance in children with D-TGA has been below expected ...

Among 61 heart specimens of tetralogy of Fallot with or without pulmonary atresia, four presented with an accessory tricuspid valve leaflet. This structure caused partial or almost complete obstruction of the ventricular septal defect. Depending on the morphology, the accessory tissue was classified into mobile or fixed types. The mobile variety was tethered by long chordae tendineae which permitted a wide excursion of the leaflet through the ventricular septal defect into the left ventricular outflow tract where it represented a potential cause of obstruction. The fixed variety was attached to the edges of the defect by short chordae which reduced considerably its movements. This type created a fixed obstruction of the ventricular septal defect without involving the subaortic left ventricular outflow tract. The precise morphology of the accessory tricuspid valve tissue is of considerable surgical significance. When mobile, the tissue must be resected at the time of surgical repair. When ...

Introduction: We aimed to develop a classification method to discriminate ventricular septal defect and atrial septal defect by using severalhemodynamic parameters.Patients and Methods: Forty three patients (30 atrial septal defect, 13 ventricular septal defect; 26 female, 17 male) with documentedhemodynamic parameters via cardiac catheterization are included to study. Such parameters as blood pressure values of different areas,gender, age and Qp/Qs ratios are used for classification. Parameters, we used in classification are determined by divergence analysismethod. Those parameters are; i) pulmonary artery diastolic pressure, ii) Qp/Qs ratio, iii) right atrium pressure, iv) age, v) pulmonary arterysystolic pressure, vi) left ventricular sistolic pressure, vii) aorta mean pressure, viii) left ventricular diastolic pressure, ix) aorta diastolicpressure, x) aorta systolic pressure. Those parameters detected from our study population, are uploaded to multi-layered artificial neuralnetwork and the network

Trisomy 18, or Edwards syndrome, is the second most common chromosome anomaly after trisomy 21. Various types of congenital heart diseases are seen in the majority of trisomy 18 patients. Palliative treatment of right ventricular outflow tract (RVOT) stenosis includes options like balloon dilatation, stenting and surgery. Herein, we present a case with trisomy 18 and double outlet right ventricle, pulmonary stenosis, and ventricular septal defect. During the follow-up, at the age of three months, his saturation dropped to 70% and an interventional procedure was planned. The patient was considered high risk, and after discussing treatment options with the family, RVOT stenting was chosen. The patient was lost on the 8th day of the follow-up. ...

Tetralogy of Fallot includes a Large Ventricular Septal Defect (VSD), the aorta overrides left and right ventricles, right ventricular outflow tract is obstructed, and the wall of the right ventricle thickens. More blood shunts through the VSD to the left side as the obstruction impedes the RV outflow, resulting in Cyanosis;[1] Tetralogy of Fallot has four key features. A Ventricular Septal Defect (a hole between the ventricles) and many levels of obstruction from the right ventricle to the lungs (Pulmonary Stenosis) are the most important. Also, the Aorta (major artery from the heart to the body) lies directly over the Ventricular Septal Defect, and the right ventricle develops thickened muscle.[2]. Adults with Tetralogy of Fallot suffer shortness of breath and cant tolerate exercise. Brain abscesses, strokes and heart infections can arise as complications. Tetralogy of Fallot patients fingers may have clubbing which is enlargements at the distal ends. If Tetralogy of Fallot remains ...

Ventricular septal defect (VSD) is the most common form of congenital cardiovascular anomaly, occurring in nearly 50% of all infants with a congenital heart defect and accounting for 14 to 16% of cardiac defects that require invasive treatment within the first year of life. Congenital VSDs may occur alone or in combination with other cardiac malformations. Large VSDs that go unrepaired may give rise to cardiac enlargement, congestive heart failure, pulmonary hypertension, Eisenmengers syndrome, delayed fetal brain development, arrhythmias, and even sudden cardiac death (summary by 3,4:Wang et al., 2011, 2011). Other congenital cardiac defects caused by mutation in the NKX2-5 gene include atrial septal defect with or without atrioventricular conduction defects (ASD7; 108900), tetralogy of Fallot (see TOF, 187500), conotruncal malformations (see 217095), and hypoplastic left heart syndrome (HLHS2; 614435). For a discussion of genetic heterogeneity of ventricular septal defect, see VSD1 (614429). ...

Define Sinus venosus atrial septal defect. Sinus venosus atrial septal defect synonyms, Sinus venosus atrial septal defect pronunciation, Sinus venosus atrial septal defect translation, English dictionary definition of Sinus venosus atrial septal defect. Noun 1. atrial septal defect - an abnormal opening between the left and right atria of the heart septal defect - a congenital abnormality in the septum...

INTRODUCTION. According to the Baltimore-Washington Infant Study, tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease and accounts for 6.7% of all live babies born with congenital heart disease.1 Tetralogy of Fallot comprises four heart defects: a large ventricular septal defect (VSD), overriding aorta, right ventricular (RV) hypertrophy, and RV outflow tract obstruction (RVOTO). This latter abnormality determines the clinical course of the patient; for example, patients with minimal obstruction will have physiological signs, such as a VSD with a net left-to-right shunt and mild to no cyanosis (referred to as a pink tet), whereas those with severe obstruction will be severely cyanotic and require early intervention. Approximately 80% of patients with TOF will have degrees of pulmonary stenosis, and 20% will have pulmonary atresia.1. Patients with TOF typically undergo VSD closure and relief of the RVOTO within the first 6 months of life. The type of surgery ...

Complete atrioventricular septal defect is a congenital heart condition caused by a hole in the wall separating the left and right chambers of the heart.

Double outlet right ventricle (DORV) is a rare congenital disorder where both of the great arteries, namely the aorta and the pulmonary artery, arise from the right ventricle.

BACKGROUND: Although satisfactory results of corrective surgery for atrioventricular septal defects (AVSDs) with complex lesions such as double-outlet right ventricle (DORV) or atrial isomerism have been reported in recent years, the optimal surgical

Patient born with Pulmonary Stenosis, Double Outlet Right Ventricle, Transposition of the Great Arteries, Ventricular Septal Defect, and Atrial Septal Defect. Scanned 19.5 Years later. - stl file processed This file was created with democratiz3D. Automatically create 3D printable models from CT scans. Learn more. tetralogy of fallot, ventricle, auricle, pulmonary, stenosis, double outlet right ventricle, transposition of the great arteries, ventricular septal defect, atrial septal, defect, ct scan with contrast, mediastinum, lung, sternum, ribs, bronchi, trachea, cava, vein, inferior, superior, aorta, ascending, descending, mediastinum, thorax, 3d, model, .stl, printable ...

Patient born with Pulmonary Stenosis, Double Outlet Right Ventricle, Transposition of the Great Arteries, Ventricular Septal Defect, and Atrial Septal Defect. Scanned 19.5 Years later. - stl file processed This file was created with democratiz3D. Automatically create 3D printable models from CT scans. Learn more. tetralogy of fallot, ventricle, auricle, pulmonary, stenosis, double outlet right ventricle, transposition of the great arteries, ventricular septal defect, atrial septal, defect, ct scan with contrast, mediastinum, lung, sternum, ribs, bronchi, trachea, cava, vein, inferior, superior, aorta, ascending, descending, mediastinum, thorax, 3d, model, .stl, printable ...

A cyanosed neonate was diagnosed as having concordant atrioventricular connection and single cardiac outlet and aorta from right ventricle with atresia of the pulmonary valve. She underwent a systemic to pulmonary artery shunt and is now thriving. Additionally, the tricuspid valve was imperforate and a large ventricular septal defect caused an unusual pattern of intracardiac blood flow. The tricuspid valve ring and right ventricular cavity appeared to be of normal size. The good outcome in this patient suggests that these features may be advantageous for corrective operation. ...

Methods Pulmonary stenosis and a large ventricular septal defect (VSD) had been diagnosed prenatally. Postnatal echocardiogram revealed an APV, pulmonary stenosis, a large sub-aortal VSD, and right ventricular hypertrophy.. Genetic analysis of the JAG-1 gene showed a frame-shift-mutation in exon 12 of the JAG-1 gene that had not been described before.. The patient underwent corrective heart surgery at 9 months of age. The VSD and the native pulmonary artery orifice were closed surgically. A valved xenograft conduit (Contegra®, 14 mm) was implanted between the RV and the pulmonary artery.. ...

A 21-year-old patient with pulmonary atresia and ventricular septal defect (PA-VSD) was admitted to the hospital for tubal ligation. Invasive arterial and central venous (CVP) pressure, pulse oximetric oxygen saturation (SpO2), and (from the tip of o

Pulmonary atresia with ventricular septal defect is a rare heart condition characterised by a lack of connection between the right ventricle and the pulmonary arteries.

Cardiovascular malformation is the most common group of congenital malformations. The prevalence at live birth diagnosed in infancy in this study was 5.3 cases per 1000 live births. This is consistent with previous large studies using similar methodology.10-12Our register of live born congenital heart disease was set up in 1990 with prospective ascertainment of all cases since then but retrospective ascertainment of cases in 1987-9. We are confident of complete ascertainment of all cases of complex or clinically significant heart disease throughout this study, but there was probably some under ascertainment of minor heart disease in 1987-1989. Recent prospective studies, with ready availability of early echocardiographic examination, have shown a higher of prevalence of live born heart disease, almost all of which is accounted for by the detection of more small ventricular septal defects.13-15 Early recognition of congenital heart disease is important because clinical presentation and ...

ops:[{insert:MAHMOUD H, NICOLESCU AM, FILIP C, NICOLAE G, DUIC\u0103 G, B\u0103LGR\u0103DEAN M, CINTEZ\u0103 EE. Complex atrial septal defect closure in children. Rom J Morphol Embryol [online] 2019, 60(1):49-57 [viewed 08 July 2019] Available from: http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/31263827},{insert:\n,attributes:{list:ordered}},{insert:Bernstein, Daniel. Ostium Secundum Defect [online]. Nelson Textbook of Pediatrics, 2020 [viewed 08 July 2019]. Available from: https:\/\/www.us.elsevierhealth.com\/nelson-textbook-of-pediatrics-2-volume-set-9781455775668.html},{insert:\n,attributes:{list:ordered}},{insert:RAO PS, HARRIS AD. Recent advances in managing septal defects: atrial septal defects F1000Res [online] 2017 Nov 22:2042 [viewed 08 July 2019] Available from: http:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC5701442},{insert:\n,attributes:{list:ordered}},{insert:MARTIN SS, SHAPIRO EP, MUKHERJEE M. Atrial Septal Defects \u2013 Clinical ...

Atrial septal defect closure in adults - What options for getting an atrial septal defect repaired in an adult? Cath or surgery. A lot of asds can be closed by trans catheter approach. Occasionally (if thery are so large with no rims) need cardiac surgery.

Children with ventricular septal defect (VSD) often demonstrate failure to thrive (Ff1). Such patients usually have reduced systemic cardiac output which has been postulated as a cause for their growth retardation. This study was conducted to ascertain the mechanism of the reduced cardiac output in children with VSD and FT11 and also in a porcine model of VSD. Forward stroke volume was reduced in VSD-FIT children, 31±8 ml/m2, compared to normal children, 49±15 ml/m2 (P , 0.05), but was not reduced in children with VSD and normal growth and development (41±16 ml/m2). Forward stroke volume was also reduced in swine with VSD compared to controls. Contractility assessed by mean velocity of circumferential shortening (Vd) corrected for afterload was similar in normals and VSD-FTI children. Contractile performance was also similar in normal and VSD swine. Afterload assessed as systolic stress was similar in FIT-VSD children and normal subjects. Preload assessed as end-diastolic stress was ...

Children with ventricular septal defect (VSD) often demonstrate failure to thrive (Ff1). Such patients usually have reduced systemic cardiac output which has been postulated as a cause for their growth retardation. This study was conducted to ascertain the mechanism of the reduced cardiac output in children with VSD and FT11 and also in a porcine model of VSD. Forward stroke volume was reduced in VSD-FIT children, 31±8 ml/m2, compared to normal children, 49±15 ml/m2 (P , 0.05), but was not reduced in children with VSD and normal growth and development (41±16 ml/m2). Forward stroke volume was also reduced in swine with VSD compared to controls. Contractility assessed by mean velocity of circumferential shortening (Vd) corrected for afterload was similar in normals and VSD-FTI children. Contractile performance was also similar in normal and VSD swine. Afterload assessed as systolic stress was similar in FIT-VSD children and normal subjects. Preload assessed as end-diastolic stress was ...

BACKGROUND: Surgical correction of complete atrio-ventricular septal defect (AVSD) achieves satisfactory results with low morbidity and mortality, but may require reoperation. Our recent operative results at mid-term were followed-up. METHODS: From June 2000 to December 2007, 81 patients (Down syndrome; n=60), median age 4.0 months (range 0.7-118.6) and weight 4.7kg (range 2.2-33), underwent complete AVSD correction. Patch closure for the ventricular septal defect (VSD; n=69) and atrial septal defect (ASD; n=42) was performed with left atrio-ventricular valve (LAVV) cleft closure (n=76) and right atrio-ventricular valve (RAVV) repair (n=57). Mortality, morbidity, and indications for reoperation were retrospectively studied; the end point time to reoperation was analyzed using Kaplan-Meier curves. Follow-up was complete except in two patients and spanned a median of 28 months (range 0.4-6.1 years). RESULTS: In-hospital mortality was 3.7% (n=3) and one late death occurred. Reoperation

A ventricular septal defect (VSD) is a congenital defect in which theres a hole in the hearts wall. One of the most telling symptoms of VSD is a heart murmur, which often becomes evident a few days after birth. Read about diagnosis, symptoms, prognosis, complications and treatment.

TY - JOUR. T1 - The role of the total artificial heart in the treatment of post-myocardial infarction ventricular septal defect. AU - Ashfaq, Awais. AU - Jaroszewski, Dawn E.. AU - Pajaro, Octavio E.. AU - Arabia, Francisco A.. PY - 2013/2. Y1 - 2013/2. UR - http://www.scopus.com/inward/record.url?scp=84872312264&partnerID=8YFLogxK. UR - http://www.scopus.com/inward/citedby.url?scp=84872312264&partnerID=8YFLogxK. U2 - 10.1016/j.jtcvs.2012.11.018. DO - 10.1016/j.jtcvs.2012.11.018. M3 - Article. C2 - 23219500. AN - SCOPUS:84872312264. VL - 145. JO - Journal of Thoracic and Cardiovascular Surgery. JF - Journal of Thoracic and Cardiovascular Surgery. SN - 0022-5223. IS - 2. ER - ...

ventricular septal defect. you would not understand. what it means to fall in love. with the blue. to come to pour it. to read it in the cracks of light under heavy spines. to see it in green marseille waters. that occasionally hold a date. from a night that is small and silent. after basking in wine and hearty laughter. only to end at an audacious ocean of black. with spit in your drying throat. until it is launched atop of the lip of a wave. to challenge the ocean to stay still. or at least. to pull her goodbye a little closer. *. overriding aorta. when we were we. we used to swim. in a big pond. that only we knew about. behind a bush. down the road where. theres that huge house. where no one lives anymore. but everyone passes by. on the way to the way. missing the big pond because. theres a bush that hides. we. when we were we. swimming and leaving. bits of us to. drown away. ...

Delayed Bone Age & Ventricular Septal Defect & Wide Space Between the First and Second Toe Symptom Checker: Possible causes include Seckel Syndrome. Check the full list of possible causes and conditions now! Talk to our Chatbot to narrow down your search.

A collection of disease information resources and questions answered by our Genetic and Rare Diseases Information Specialists for Ventricular septal defects

Olives mother, Robin said her daughter is, funky and feisty. In the last two weeks, it seems like Olive is not - she cant seem to hold her own without high-flow oxygen. They pretty much told us there was nothing they could do. Weve heard that before, but we can physically see with our eyes that shes not able to support herself. The little girl was born with a myriad of heart and lung conditions including pulmonary atresia, major aortopulmonary collateral arteries and tetralogy of Fallot. If you combine all of these conditions, it makes her little heart and lungs unable to efficiently provide oxygenated blood to the rest of her little body.. Olive has undergone several procedures, include cardiac catheterization in order to widen her tiny pulmonary veins. However, her veins are scarring quickly and closing in fast. According to data provided by the Organ Transplant and Procurement Network, 21 people die each day waiting for an organ that never arrives. A new person is added to the ...

Due to advances in corrective surgery, congenital heart disease has an ever growing patient population. Atrial arrhythmias are frequently observed pre- and post-surgical correction. Pharmaceutical antiarrhythmic therapy is not always effective, therefore many symptomatic patients undergo catheter ablation therapy. In patients with atrioventricular septal defects (AVSD), ablation therapy itself has mixed success; arrhythmogenic recurrences are common, and because of the anatomical displacement of the atrioventricular node, 3-degree heart block post-ablation is a real concern. In order to develop optimal and safe ablation strategies, the field of congenital cardiac electrophysiology must combine knowledge from clinical electrophysiology with a thorough understanding of the anatomical substrates for arrhythmias. Using image-based analysis and multi-cellular mathematical modeling of electrical activation, we show how the anatomical alterations characteristic of an AVSD serve as arrhythmogenic ...

Atrioventricular Septal Defect (AVSD). In: Hay, Jr WW, Levin MJ, Deterding RR, Abzug MJ. Hay, Jr W.W., Levin M.J., Deterding R.R., Abzug M.J. Eds. William W. Hay, Jr, et al.eds. Quick Medical Diagnosis & Treatment Pediatrics New York, NY: McGraw-Hill; . http://accesspediatrics.mhmedical.com/content.aspx?bookid=2196§ionid=166955717. Accessed December 12, 2017 ...

Looking for interatrial septal defect? Find out information about interatrial septal defect. A congenital malformation of the septum between the atria of the heart Explanation of interatrial septal defect

Movie 4 Movie 5. Movie 4: TEE simultaneously demonstrating presence of a large defect in the posterior aspect of the atrial septum with left to right flow Movie 5: TEE 4 chamber view showing moderate right heart dilation secondary to the left to right shunt Conclusions:. She underwent successful patch closure of the atrial septal defect with re-routing of the right lower pulmonary vein to the left atrium. Sinus venosus atrial septal defects are rare and the inferior variety is even less frequently seen as compared to the superior type. This case describes such a unique entity and demonstrates the singular ability of cardiac magnetic resonance imaging to diagnose the lesion qualitatively and in addition provides quantitative information on its hemodynamic consequences.. Perspective : Arial septal defects occur in about 1.5 per 1,000 newborns. Caval vein defects are the least common forms of atrial communications forming only 2-10% of all inter-atrial communications (1). The superior form of ...

Atrioventricular septal defect. Four-chamber view shows the absent crux (arrow). RA - right atrium, LA - left arium, RV - right ventricle, LV - left ven

Atrioventricular Septal Defects - Learn about the causes, symptoms, diagnosis & treatment from the MSD Manuals - Medical Consumer Version.

Introduction: The aim of this study was to evaluate the following parameters of fetuses and neonates with omphalocele: the prevalence of coexisting congenital heart defects (CHD), abnormalities in heart function and the impact of coexisting CHD on fetal and neonatal survival. Material and methods: The study group consisted of 69 fetuses with omphalocele diagnosed and monitored at the Department of Prenatal Cardiology in our Institute in the years 2007-2017. The retrospective analisis of patients data was performed. For statistical analysis we used Chi-square test, t-Student test and U Mann-Whitney test.. Results: In the studied group omphalocele was an isolated defect in 31.9% of the cases (22/69), in 68.1% (47/69) coexisting defects were present, in 49.3% (34/69) the coexisting defect was CHD. The most common CHD coexisting with omphalocele were ventricular septal defect (VSD), double outlet right ventricle (DORV) and atrio-ventricular septal defect (AVSD). Abnormalities of heart function were ...

Atrial septal defect: Atrial septal defect,, congenital opening in the partition between the two upper chambers (atria) of the heart. The most common atrial septal defect is persistence of the

The patient was a 4-day-old, 3.95 kg boy with an antenatal diagnosis of double outlet right ventricle with subpulmonary ventricular septal defect (Taussig-Bing anomaly), d-malposed great vessels (side-by-side orientation, aortic valve is rightward and slightly anterior to the pulmonary artery), and severely hypoplastic aortic arch (segment between left common carotid and left subclavian arteries). Essentially, a single coronary arose from the right posterior sinus with an acute marginal artery arising alone from the left anterior sinus.. ...

A 64-year-old man presented with an inferior ST-elevation myocardial infarction. The patient underwent emergent percutaneous coronary intervention of his right coronary artery. Cine cardiac magnetic resonance imaging showed a contained rupture of the inferobasal wall with pseudoaneurysm formation (A). Delayed enhancement image showed the transmural infarct (B). Cardiac computed tomography multiplanar reconstruction also showed an associated ventricular septal defect (C). Transthoracic echo color Doppler image showed flow across ventricular septal defect (D). Although relatively rare, both pseudoaneurysms and ventricular septal defects are well-known mechanical complications after myocardial infarction that increase the risk of mortality. This patient had bovine pericardial patch repair of both defects 3 weeks later, after which he was discharged to cardiac rehabilitation. ...

The size of a VSD and its location in the heart determines what kind of symptoms it causes.. VSDs are usually found in the first few months of life by a doctor during a routine checkup. Most teens born with a VSD probably dont remember having it because it either goes away on its own or it was found so early in childhood that theres no memory of any surgery or recovery.. Teens who have small VSDs that havent closed yet usually dont notice any physical signs other than the heart murmur that doctors hear. They may need to see a doctor regularly to check on the heart defect and make sure there arent any problems.. The very small number of teens with moderate and large VSDs that havent been treated in childhood may notice some symptoms, however. These include shortness of breath, a feeling of tiredness or weakness (especially during exercise), poor appetite, and trouble gaining weight.. Most moderate to large VSDs are treated long before they ever causes problems.. ...

2019. Tretter, J. T., Vi-Hue, T., Gray, S., Ta, H., Loomba, R. S., OConnor, W., . . . Anderson, R. H. (2019). Assessing the criteria for definition of perimembranous ventricular septal defects in light of the search for consensus. ORPHANET JOURNAL OF RARE DISEASES, 14, ARTN 76. doi:10.1186/s13023-019-1044-2. Dejea, H., Garcia Canadilla, P., Cook, A., Guasch, E., Zamora, M., Crispi, F., . . . Bonnin, A. (2019). Comprehensive Analysis of Animal Models of Cardiovascular Disease using Multiscale X-Ray Phase Contrast Tomography. Scientific Reports, 9, 6996. doi:10.1038/s41598-019-43407-z. Garcia Canadilla, P., Cook, A., Mohun, T., Oji, O., Schlossarek, S., McKenna, W. J., . . . Captur, G. (2019). Myoarchitectural disarray of hypertrophic cardiomyopathy begins pre-birth. Journal of Anatomy. doi:10.1111/joa.13058. Garcia Canadilla, P., Dejea, H., Bonnin, A., Lombardi, C., Bjinens, B., & Cook, A. (2019). Revealing Cardiac Microstructure in a Human Fetal Heart of 8 weeks gestation with Synchrotron-based ...

Treatment of tetralogy of Fallot with complete intracardiac repair (corrective surgery) (costs for program #139935) ✔ University Hospital Münster ✔ Department of Congenital (CHD) and Acquired Heart Defects ✔ BookingHealth.com

Treatment of tetralogy of Fallot with complete intracardiac repair (corrective surgery) (costs for program #106305) ✔ University Hospital RWTH Aachen ✔ Department of Thoracic, Vascular Surgery and Cardiac Surgery ✔ BookingHealth.com

Bulboventricular foramen obstruction nay complicate the management of patients with single left ventricle. Bulboventricular foramen size was measured in 28 neonates and infants ,5 months old and followed up for 2 to 5 years in those patients whose only sytemic outflow was through the foramen. The bulboventricular foramen was measured in two planes by two-dimensional echocardiography, its area calculated and indexed to body surface area. One patient died before surgical treatment. The mean initial bulboventricular foramen area index was 0.94 cm2/m2in 12 patients (Group A) in whom the foramen was bypassed as the first procedure in early infancy. The remaining 15 patients underwent other palliative operations but the bulboventricular foramen continued to serve as the systemic outflow tract. There was one surgical death. Six (Group B) of the 14 survivors developed bulboventricular foramen obstruction during follow-up (mean initial bulboventricular foramen area index 1.75 cm2/m2). The remaining eight ...

Objective: Partial atrioventricular septal defect is also known as ostium primum type atrial septal defect. Complications such as atrioventricular valve insufficiency, complete atrioventricular bundle blocks requiring pace-maker and left ventricle outflow obstruction may occur during postoperative period. This study presents the surgical correction results of partial atrioventircular septal defect, thus we aimed to determine the comorbidities and mid-term outcomes. In this study, we aimed to report the results of partial atrioventircular septal defect. correction operations, their comorbidities and mid-term data after discharge. ...

The Cove Point Foundation Congenital Heart Resource Center is the worlds largest resource for information on pediatric and adult congenital heart disease. Cove Point contains comprehensive information on all congenital heart defects, including Atrial Septal Defect (ASD), Ventricular Septal Defect (VSD), Hypoplastic Left Heart Syndrome (HLHS), and Tetralogy of Fallot (ToF). Cove Point also includes adult congenital heart disease information on exercise and pregnancy concerns as well as pediatric information on general nutritional and health issues for patients with congenital heart disease.

DISCUSSION. The early mortality rate after SCPC operation in our study was 2.5%. Five (3.1%) patients underwent takedown of the SCPC of whom two at the same operation day and three later during the follow-up period. The rate of exclusion from the TCPC was 8.3%. Statistical analysis revealed that elevated mPAP preoperatively and the prior palliation with PAB were risk factors for both early mortality and takedown of the SCPC; however, the age, the morphology of the single ventricle, and the type of SCPC were not considered risk factors. The diagnosis of large multiple ventricular septal defects or the upstairs downstairs ventricles with double outlet right ventricle or double outlet left ventricle was associated with poor outcomes but due to the small number of patients a statistically significant correlation could not be found.. Preoperative mPAP has been reported as a risk factor for death after the Glenn procedure[8], and mortality in those receiving pulmonary artery banding was high[9], and ...

Results In the first family, we identified a de novo missense mutation (c.1366C,T, p.R456C) in a sporadic CDH patient with tetralogy of Fallot. In the second, a nonsense mutation (c.712G,T, p.G238*) was identified in two siblings with CDH and a large ventricular septal defect. The G238* mutation was inherited from their mother, who was clinically affected with congenital absence of the pericardium, patent ductus arteriosus and intestinal malrotation. Deep sequencing of blood and saliva-derived DNA from the mother suggested somatic mosaicism as an explanation for her milder phenotype, with only approximately 15% mutant alleles. To determine the frequency of GATA6 mutations in CDH, we sequenced the gene in 378 patients with CDH. We identified one additional de novo mutation (c.1071delG, p.V358Cfs34*).. ...

Although single individual reports have documented outcomes in children with pentalogy of are few data available for postoperative outcome of this cohort of patients after cardiac surgery. The aim of this study was to retrospectively review the clinical details of patients with pentalogy of Cantrell managed at two centers. Two cardiac surgical institutions retrospectively studied all patients with pentalogy of Cantrell and significant congenital heart disease who underwent surgical intervention, excluding PDA ligation, between 1992 and 2004. Seven children with pentalogy of Cantrell underwent surgical intervention at a median age of 60 days (range, 1-11 months). Three patients had tetralogy of Fallot, two double outlet right ventricle, one patient had tricuspid atresia, and one patient a perimembranous ventricular septal defect. The mean duration of postoperative ventilation was 112.8 days (range, 4-335 days) but three patients required ventilation for more than 100 days. Patients who had a ...

A 60-year-old man, who underwent repair of ventricular septal defect iVSD j40 years previously, presented with dyspnea on effort and leg edema. Further examination showed residual VSD, mitral and tricuspid valve insufficiency, atrial flutter and pulmonary hypertension. We performed repair of the residual VSD, mitral valve replacement, tricuspid valve annuloplasty, and the Maze procedure. After surgery, systolic pulmonary arterial pressure decreased from 70 to 39mmHg. On the 4th postoperative day, his hemodynamic state was stable and he weaned from ventilator. He showed hypoxia with sticky excretions, and reintubation was done 10 h after extubation. After intubation, pulmonary hypertension continued, nitroglycerine administration was not effective but inhaleted nitric oxide iNO jimproved pulmonary hypertension. On the 15th postoperative day, sildenafil administration from nasogastric tube was started the day before extubation. On postoperative echocardiogram on the 35th postoperative day, the ...

The Cove Point Foundation Congenital Heart Resource Center is the worlds largest resource for information on pediatric and adult congenital heart disease. Cove Point contains comprehensive information on all congenital heart defects, including Atrial Septal Defect (ASD), Ventricular Septal Defect (VSD), Hypoplastic Left Heart Syndrome (HLHS), and Tetralogy of Fallot (ToF). Cove Point also includes adult congenital heart disease information on exercise and pregnancy concerns as well as pediatric information on general nutritional and health issues for patients with congenital heart disease.

TY - JOUR. T1 - Hemodynamics in congenital heart disease. AU - Peskin, Charles S.. AU - Tu, Cheng. PY - 1986. Y1 - 1986. N2 - This paper introduces a very general and flexible model for the study of hemodynamic changes in congenital heart disease. The generality of the model makes it possible to use the same computer program (which is included in an Appendix) to study both the fetal circulation and the adult circulation, as well as such diverse disease states as patent ductus arteriosus, ventricular septal defect, atrial septal defect, tetralogy of Fallot and transposition of the great arteries. In this paper, only patent ductus and ventricular or atrial septal defect are studied, with special emphasis on the influence of increasing pulmonary vascular resistance on the shunt flow. In the case of patent ductus and ventricular septal defect, the computed shunt flow is very time-dependent and the left-to-right shunt becomes first bidirectional and then right-to-left as the pulmonary resistance ...

Heterozygous mutations in NKX2.5, a homeobox transcription factor, were reported to cause secundum atrial septal defects and result in atrioventricular (AV) conduction block during postnatal life. To further characterize the role of NKX2.5 in cardiac morphogenesis, we sought additional mutations in groups of probands with cardiac anomalies and first-degree AV block, idiopathic AV block, or tetralogy of Fallot. We identified 7 novel mutations by sequence analysis of the NKX2.5-coding region in 26 individuals. Associated phenotypes included AV block, which was the primary manifestation of cardiac disease in nearly a quarter of affected individuals, as well as atrial septal defect and ventricular septal defect. Ventricular septal defect was associated with tetralogy of Fallot or double-outlet right ventricle in 3 individuals. Ebsteins anomaly and other tricuspid valve abnormalities were also present. Mutations in human NKX2.5 cause a variety of cardiac anomalies and may account for a clinically ...

Tricuspid atresia is a form of congenital heart disease whereby there is a complete absence of the tricuspid valve. Therefore, there is an absence of right atrioventricular connection. This leads to a hypoplastic (undersized) or absent right ventricle. This defect is contracted during prenatal development, when the heart does not finish developing. It causes the heart to be unable to properly oxygenate the rest of the blood in the body. Because of this, the body does not have enough oxygen to live, so other defects must occur to maintain blood flow. Because of the lack of an A-V connection, an atrial septal defect (ASD) must be present to fill the left ventricle with blood. Also, since there is a lack of a right ventricle there must be a way to pump blood into the pulmonary arteries, and this is accomplished by a ventricular septal defect (VSD). The causes of Tricupsid atresia are unknown. An atrial septal defect (ASD) and a ventricular septal defect (VSD) must both be present to maintain blood ...

Atrioventricular septal defect or AV Canal (AVSD) is a heart defect that involves the valves between the hearts upper and lower chambers and the walls between the chambers.

Click picture to show/hide bloodflows). Pathophysiology. The hemodynamics involved with double outlet right ventricle are dependent on the anatomy of the great vessels and associated defects. Decreased arterial oxygen saturation is almost always present, but as a result of wide variation in anatomy, patients may or may not appear cyanotic and/or develop congestive heart failure. Patients may even be asymptomatic altogether. Transposition-like physiology occurs with inadequate circulatory mixing of oxygenated and deoxygenated blood.. Therapy. Management of double outlet right ventricle in early infancy depends on associated defects. When operative therapy is required, the type of surgical correction depends on the anatomic characteristics of the defect and amenability. The goal of the surgical treatment is complete anatomic repair, which means connecting the left ventricle to the aorta, the right ventricle to the pulmonary artery, and closure of the VSD. Principles of open-heart surgery such as ...

Background: Single-stage biventricular repair remains a challenging and difficult decision in high-risk newborns and early infants with the presence of left ventricular outflow tract obstruction (LVOTO) or borderline hypoplasia of the left ventricle (LV). Methods: Six high-risk patients underwent the initial hybrid procedure (bilateral pulmonary banding + ductal stenting) for staged biventricular repair. Their median age was 17 days (range: 7-55 days). The diagnosis was interrupted aortic arch (IAA), ventricular septal defect (VSD), and LVOTO (n = 3); IAA and VSD (n = 1); and aortic annular hypoplasia, aortic arch hypoplasia, VSD, and LVOTO (n = 1). The last patient had borderline LV with large atrial septal defect (ASD) and aortic arch hypoplasia. The patient with borderline LV had also ASD closure with small fenestration. Results: One patient died of sepsis after the hybrid procedure. Other patients underwent biventricular repair 8 to 13 months later. Three patients had conventional repair ...

A 4-month-old, 2.4-kg female infant with medically refractory heart failure underwent uneventful surgical repair of a perimembranous ventricular septal defect, a secundum atrial septal defect, and a vascular ring (right aortic arch, aberrant left subclavian artery, left posterior patent ductus arteriosus). Surgery was uneventful, but 6 hours after surgery, in the intensive care unit, transthoracic echocardiographic (TTE) examination revealed a small echodensity along the right atrial free wall. Repeated TTE examination 18 hours later showed the echodense mass nearly obliterating the right atrial cavity (Fig. 1) (video clip; see supplemental data on www.anesthesia-analgesia.org). Heparin therapy was initiated for a presumed right atrial thrombus. The infant remained hemodynamically stable without evidence of compromised cardiac output. Due to unchanged echocardiographic findings, mediastinal exploration was performed on postoperative day 3. Surgical exploration unexpectedly revealed a large ...

The Fontan operation was initially designed to provide a physiological correction of tricuspid atresia, but its indications have been extended to more complex forms of congenitally malformed hearts. In selected patients with two adequately sized ventricles, but highly complex intra cardiac anatomy which makes a biventricular repair more hazardous and which would require multiple reoperations, a univentricular repair using Fontans principle has been proposed. Between 1978 and 1992, a modified Fontan operation was carried out in 34 such patients. Of the patients. 13 had double outlet right ventricle and 21 had transposed great arteries. Anomalies of ventricular loop were present in 14 patients. A non-committed ventricular septal defect was found in 26 whilst multiple defects were present in 10. All patients had anomalies of the atrioventricular valves, with straddling of the tricuspid valve,11 and/or of the mitral valve11, and abnormal tricuspid5, or mitral4 cordal attachments. Two patients had ...

Looking for online definition of double inlet atrioventricular connections in the Medical Dictionary? double inlet atrioventricular connections explanation free. What is double inlet atrioventricular connections? Meaning of double inlet atrioventricular connections medical term. What does double inlet atrioventricular connections mean?

Objective: The focus of this study is to share the experience and outcomes of Contegra graft implantation in the paediatric and adult population in Pakistan. Methods: Between May 2007 and July 2011, 16 patients, underwent implantation of a Contegra valved conduit. All operations were performed through a median sternotomy with cardiopulmonary bypass. Indications included: Pulmonary atresia with ventricular septal defect (n=11), Tetralogy of Fallot with absent Pulmonary Valve (PV) syndrome (n=2), double outlet right ventricle, transposition of great arteries and pulmonary stenosis (n=1), isolated aortic valve disease (n=1) and a pseudo-aneurysm with infective endocarditis (n=1).Conduit sizes varied between 16-22 mm. Results: The three in hospital deaths were unrelated to the Contegra valved conduit. One patient was lost to follow up. Of the 12 survivors, 10 are currently free from re-operation or complications related to the conduit while one needed distal pulmonary artery dilatation owing to critical

The hippocampus is vulnerable to perinatal hypoxic/ischaemic insults with potential memory impairment in later life. We measured memory and hippocampal integrity in survivors of the Arterial Switch Operation (ASO) for Transposition of Great Arteries (TGA).. Methods We recruited 35 neurodevelopmentally normal children [mean (SD) age 10.9 (0.4) years] who had ASO and 21 age-matched healthy controls [11.6 (0.3) years]. Preterms and those with genetic syndromes and additional heart abnormalities were excluded. Clinical and intra-operative variables were analysed. All had standardised tests of intelligence, general memory and learning, academic achievements, and a special test of episodic memory (Rivermead Behavioural Memory Test). Hippocampal volumes (mm3) were measured using MRI corrected for intracranial volume.. Results In the 35 studied, 2 groups were identified: 25 with intact ventricular septum (TGA-IVS) and 10 with ventricular septal defect (TGA-VSD); median (IQR) age at ASO was 13 (9.5, ...

TY - JOUR. T1 - Role of transcatheter therapy in the treatment of coarctation of the aorta. AU - Horvath, Robert. AU - Towgood, Andrea. AU - Sandhu, Satinder K.. PY - 2008/12/1. Y1 - 2008/12/1. N2 - Coarctation of the aorta is one of the most common congenital heart defects. Transcatheter therapy for treatment of coarctation is effective, with low morbidity and mortality rates. The current trend is toward primary stent implantation for treatment, however, the results of balloon angioplasty in children and young adults are equivalent to the results following primary stent placement. Judicious use of stents is recommended in infants and children.. AB - Coarctation of the aorta is one of the most common congenital heart defects. Transcatheter therapy for treatment of coarctation is effective, with low morbidity and mortality rates. The current trend is toward primary stent implantation for treatment, however, the results of balloon angioplasty in children and young adults are equivalent to the ...

Because of the wide variability of pulmonary blood supply, diagnosis and surgical management of tetralogy of Fallot (TOF) with pulmonary atresia (PA) is more difficult than that of classic tetralogy of Fallot, and therefore, it is worthy of separate consideration. Tetralogy of Fallot is composed of a malaligned ventricular septal defect (VSD...

The present invention provides a delivery system for delivering a device for closing septal defects and the like. The system comprises an elongate, flexible urging member for urging the closure device through a catheter and a remotely located control means for advancing the urging member. The control means includes a threaded, generally tubular shaft connected to the urging member and a manually rotatable rotor mounted on the shaft, the rotor having threads which mate with the threads on the shaft so that rotation of the rotor through a known angle will advance the shaft, and hence the urging member, a known distance. In a preferred embodiment, the urging member includes a core wire adapted to retain a closure device prior to final deployment and a release lever for releasing the closure device from the core wire when the closure device is properly positioned.

Unilateral pulmonary artery discontinuity (UPAD) is a rare malformation which is associated with other intracardiac abnormalities. Cases accompanied by other cardiac abnormalities are often missed on prenatal echocardiography. We reported our case whi

Once an AVSD is diagnosed the child will be carefully monitored to see when they need surgery. If the heart is not able to operate properly then parents may be told that their child is in heart failure.. Symptoms of heart failure include the lungs and other organs becoming heavy or wet with fluid. A careful check will be kept on the childs weight as any increase can be due to fluid retention. To help get rid of the extra fluid the child may need special medicines called diuretics.. A complete AVSD causes pulmonary hypertension (high pressure of blood in the lung arteries), and an operation will need to be performed before the lungs are damaged.. This operation is open heart surgery, which means that the heart will need to be stopped and opened to repair it. A heart bypass machine will take over the job that the heart normally does.. The aim of the operation is to make the circulation of blood through the heart and lungs normal. A patch is put over the holes between the atria and ventricles. ...

Overview and classification of congenital heart disease - Fetal circulation - Assessment of patients with CHD - Conduct of anaesthesia in CHD - Cardiac catheterization - Closed cardiac procedures Systemic arterial-pulmonary arterial shunt - Coarctation of the aorta - Patent ductus arteriosus - Epicardial pacemaker insertion - Pulmonary artery banding - Cardiopulmonary bypass - Deep hypothermic circulatory arrest (DHCA) - Open cardiac procedures-notes on specific lesions Atrial septal defect - Ventricular septal defect - Atrio-ventricular septal defect - Tetralogy of Fallot - Transposition of the great arteries ...

Congenital heart diseases occur in at least 10 per 1000 live-born children; the incidence is much higher in stillborn infants and in spontaneous abortuses. This figure excludes bicuspid aortic valves, patent ductus arteriosus in premature infants, and tiny muscular ventricular septal defects with respective incidences of 10 to 20, 4 to 5, and 30 to 40 per 1000 live-born children. The distributions of various common types of congenital heart diseases at birth are given in Table 484-1. ...

Atrial septal defect (ASD) is a condition that requires early intervention because of the consequences over the right-side heart. Chronic atrial …

Within the lungs the blood is oxygenated. From the lungs the blood returns to the left atrium of the guts. Blood within the left atrium strikes to the left ventricle in the course of the left atrioventricular valve or the biscuspid valve. This valve has cusps, chordae tendineae and papillary muscle groups. while the left ventricle contracts, the blood strikes during the aortic semilunar valve and into the ascending aorta. j /1 White arrows = oxygen-rich blood Black arrows = oygen-poor blood D = ~ veins D = arteries y. _-------x. To lungs To lungs c. - - - - - - - - - From lungs e. - - - - - - - - - From lungs w. v. u. t. 1. s. J. r. okay. -------- q. 1. p. m. n. o. _ resolution Key: a. Pulmonarytrunk, b. Pulmonary semilunar valve, c. Left atrium, e. Left atrioventricular valve, f. Aortric semilunar valve, g. Left ventricle, h. Endocardium, i. Epicardium, j. Myocardium, ok. Parietal pericardium, I. Fibrous layer, m. Serous layer, n. Interventricular septum, o. Trabeculaecarneae, p. Inferior vena ...

RESULTS: A total of 805 patients with CHD were managed during the period. The age range was 9 days to 18 years, with a mean age of one and half years. The most common CHD managed was tetralogy of Fallot (38.5%), followed by ventricular septal defect (15.4%) and atrial septal defect (14.8%). Treatment received varied from modified Blalock-Taussig shunt to intracardiac repair among others. The length of hospital stay ranged from 7 days to 21 days with average of 9.3 days. The outcome depended on the type of CHD, time of presentation, associated comorbidity and the extent of accuracy of preoperative echocardiography diagnosis. The success rate of 85-95% on the average was recorded ...

A temporary pacemaker and intra-aortic balloon pump (IABP) where placed and the patient managed in the intensive care unit (ICU), where he remained hemodynamically unstable. The patient developed decompensated shock, acute kidney injury with metabolic acidosis (pH 6.9, bicarbonate ,10 mmol/L, lactate ,15 mmol/L) so continuous hemodiafiltration (HDF) was started. The patient developed ventricular fibrillation and underwent cardiopulmonary resuscitation for 25 mins. Post resuscitation the patient was on norepinephrine up ...

We had our level 2 ultrasound done with Dawn and she pointed out as we knew there were some heart abnormalities. This scan was to measure everything from head to toe. She would continue to take multiple pics of just the heart. We did find out it is a BOY, his name is Ethan Matthew. He is a Wolfe boy for sure, would not sit still long enough for Dawn to get a good picture of anything. The scan took a little over an hour. Immediately after she was done, we waited for Dr. Matt to see us. He came in and introduced himself. He was very kind and straight forward. He personally scanned the baby and viewed images himself and said he had some additional concerns he wanted to address with us. He noted the baby did have a congenital heart defect known as a complete atrioventricular septal defect (AVSD). Then he proceeded to say, unfortunately I am certain your baby has Down Syndrome. Right now he has 3 markers for Down Syndrome (DS), the heart defect (which accounts for 40% of DS), flat nasal bridge, and ...

Taussig-Bing anomaly is a rare congenital heart malformation and is one of the variants of double outlet right ventricle. It consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary v...

PATINO BAHENA, Emilia et al. Clinic aspect of Criss-cross: A case report. Arch. Cardiol. Méx. [online]. 2006, vol.76, n.2, pp.197-201. ISSN 1665-1731.. A 1-month-old girl was referred at our Institution with a history of heart failure and cyanosis. We established diagnosis of multiple congenital heart disease with criss-crossed atrioventricular connections but concordant. This type of anomaly has a variety of presentations of high diagnostic complexity. The multiple lesions included double outlet of the right ventricle, right subaortic stenosis, ventricular septal defect, coarctation of the aorta with hypoplasia of the arch, and persistent patency of the arterial duct, established through echocardiography, angiocardiography and magnetic resonance. These findings prompted palliative surgery and correction of the aortic arch.. Palabras llave : Criss-cross; Superoinferior ventricles; Crisscrossed atrioventricular connections; Congenital heart disease. ...

Most women with an atrial septal defect can go through pregnancy without problems related to the defect. However, having a larger defect or having complications such as heart failure, arrhythmias or pulmonary hypertension can increase the risk of complications during pregnancy.. The risk of congenital heart disease is higher for children of parents with congenital heart disease. Anyone with a congenital heart defect, repaired or not, who is considering starting a family should talk to a doctor. The doctor might recommend repair before pregnancy.. ...

Surgical strategy and approach are important in patients with aortic coarctation associated with intracardiac anomalies. In this study, surgical technique, indications and results of the single stage repair of aortic coarctation and intracardiac defects via median sternotomy were discussed. Between January 1987 and August 2002, 158 patients with aortic coarctation or interrupted aortic arch (IAA) underwent surgery. In 17 of them who had associated intracardiac anomalies, single stage approach via median sternotomy were performed. Their ages ranged from 1 month to 13 years (mean 2.2 3.3 years). Ventricular septal defect (VSD) and aortic stenosis were the most common associated lesions. Aortic coarctation was repaired under cardiopulmonary bypass initially and then intracardiac repair was performed. A short period of total circulatory arrest was necessary in two patients with IAA and one patient with extensive arcus hypoplasia. Among the patients who underwent single stage repair of aortic ...

Methods Patients of ES with age greater than or equal to 18 years and weight greater than or equal to 30 kgs in World Health Organisation (WHO) functional class II and III attending our congenital clinic were invited to participate in the study. Informed written consent was taken from all the patients before screening procedures were initiated for the study. A detailed clinical examination and non-invasive testing including electrocardiogram, chest X ray, pulmonary function tests (to exclude associated restrictive/obstructive lung disease) and echocardiography(including contrast echo if required for demonstrating right to left shunt) were conducted. Patients with simple congenital heart defects (atrial septal defect , 2cm, ventricular septal defect , 1cm and aortopulmonary communications , 0.4 cm) with echocardiographic evidence of right to left shunt were included. Medical therapy and clinical condition of the patients had to be stable for 3 months prior to screening. Patients on treatment with ...

Liao et al. investigated the long-term outcome of conventional surgery repair and perventricular device occlusion for doubly committed subarterial (DCSA) VSD. They analyzed single-center results using propensity score matching. There were no differences in adverse events within the two groups. The interventional treatment resulted in shorter mechanical ventilation times and hospital stay. The authors concluded that interventional device therapy might be an alternative for selected patients with DCSA VSD.. ...

Dr. Ruiz-Healy responded: Different Anatomy. A double outlet right ventricle means that both aorta (the blood vessel that carries |a href=/topics/oxygen track_data={

Atrial septal defect (ASD) in dogs is a congenital heart defect that occurs in utero whereby the affected patients heart fails to form properly. Specifically, the wall within the heart that separates the left and right atrium from each other does not form completely leaving a small

Through robotic-assisted surgery, TriHealth can provide repair for an atrial septal defect (ASD), which is a congenital heart defect that produces a hole in the wall of the atrium, the upper chamber of the heart.

A 46-year-old woman with secundum atrial septal defect. Mean pulmonary artery pressure is 20 mm Hg. A: The heart lies in the left chest. The pulmonary artery segment (PA) is greater in caliber than the aortic arch (Ao). The pulmonary artery branches of both lungs are all dilated, sharp edged, and extend nearly to the pleura. The narrow superior mediastinum and decreased concavity in the middle of the left heart contour are caused by cardiac rotation secondary to right heart dilatation. Furt.... ...

IVS, intact ventricular septum; TGA, transposition of the great arteries; VSD, ventricular septal defect From: Yoo S.-J., Lee Y.-H., Kim ES, Ryu HM et al. Three-vessel view of the fetal upper mediastinum: an easy means of detecting abnormalities of the ventricular outflow tracts and great arteries during obstetric screening. Ultrasound Obstet Gynecol 9:173-182, 1997.. ...

A 40-year-old man presents to his physicians office for a routine physical. In the past few years, he has neglected to attend these appointments. He reports having no complaints, except for some shortness of breath with exertion. Physical exam reveals a new murmur, characterized by a wide and fixed split S2 heart sound, especially during inspiration. An echocardiogram reveals an atrial septal defect. ...