A malformation of the heart in which the embryonic common PULMONARY VEIN was not incorporated into the LEFT ATRIUM leaving behind a perforated fibromuscular membrane bisecting the left atrium, a three-atrium heart. The opening between the two left atrium sections determines the degree of obstruction to pulmonary venous return, pulmonary venous and pulmonary arterial hypertension.
A congenital heart defect characterized by downward or apical displacement of the TRICUSPID VALVE, usually with the septal and posterior leaflets being attached to the wall of the RIGHT VENTRICLE. It is characterized by a huge RIGHT ATRIUM and a small and less effective right ventricle.
Developmental abnormalities in any portion of the ATRIAL SEPTUM resulting in abnormal communications between the two upper chambers of the heart. Classification of atrial septal defects is based on location of the communication and types of incomplete fusion of atrial septa with the ENDOCARDIAL CUSHIONS in the fetal heart. They include ostium primum, ostium secundum, sinus venosus, and coronary sinus defects.
The chambers of the heart, to which the BLOOD returns from the circulation.

Cor triatriatum in adults: three new cases and a brief review. (1/34)

We report 3 cases of cor triatriatum that were diagnosed late, in the 4th and 5th decades of life. The presentations of these 2 men and 1 woman varied substantially, both in anatomic and symptomatic aspects. The woman had an associated complex congenital anomaly, which is not uncommon in cases of cor triatriatum. We present our cases, along with a review of this rare congenital cardiac anomaly.  (+info)

Cor triatriatum sinistrum and persistent left superior vena cava: an original association. (2/34)

Cor triatriatum sinistrum is a rare congenital heart disease usually diagnosed in symptomatic children. Symptoms depend on the degree of obstruction to pulmonary venous return with pulmonary hypertension and other associated abnormalities. Persistent left superior vena cava is quite a common congenital heart disease (about 0.5% in healthy populations). It should be suspected every time a dilated coronary sinus is detected at the echo examination. Transthoracic and transoesophageal examinations visualize the site and the size of the fibrous membrane as well as the degree of obstruction, and allow the evaluation of pulmonary pressures that are very important clues for prognosis and therapy. This case report describes the clinical signs and the diagnostic ultrasound findings evaluated in comparison with magnetic resonance imaging, a well-defined gold standard in heart disease of this uncommon congenital association.  (+info)

Cor triatriatum sinister presenting in the adult as mitral stenosis. (3/34)

Cor triatriatum sinister is a rare congenital defect in which the left atrium is divided by a fibromuscular membrane into two distinct chambers. Classically, patients present in infancy although in some cases they remain asymptomatic until adulthood. The clinical features on presentation can mimic those of mitral stenosis due to the obstructive properties of the membrane. Cor triatriatum sinister presented in this case in an adult as mitral stenosis. Factors that may be relevant in determining late presentation are also discussed.  (+info)

A characteristic continuous wave Doppler signal in cor triatriatum? (4/34)

Continuous wave Doppler recordings of the turbulent jet through the restrictive orifice of a left atrial partition in a patient with corrected transposition of the great arteries and cor triatriatum showed alternate bands of high intensity diastolic and low intensity systolic signals with preservation of the normal configuration of the diastolic E and A peaks. It is thought that Doppler studies in cor triatriatum will provide useful complementary haemodynamic information in the echocardiographic diagnosis of this anomaly.  (+info)

Cor triatriatum sinister, not mitral stenosis, in an adult with previous Sydenham's chorea: diagnosis and preoperative assessment by cross sectional echocardiography. (5/34)

In cor triatriatum sinister, one of the rarest congenital cardiac anomalies, a membrane divides the left atrium into a pulmonary venous component above and the vestibule below. The importance of the anomaly lies in the effects of the resultant pulmonary venous obstruction that usually present in the first year of life and can mimic obstructed total anomalous venous drainage or congenital mitral stenosis. A case presented as mitral stenosis in the third decade of life, ten years after a well documented episode of Sydenham's chorea. The diagnosis was made rapidly by transthoracic echocardiography and transoesophageal echocardiography was used for complete assessment. Cardiac catheterisation added nothing to the non-invasive diagnosis or the preoperative assessment. Uncomplicated corrective surgery was undertaken.  (+info)

Ebstein's malformation with atrial septal defect, right cor triatriatum, and right overt accessory atrioventricular pathway. (6/34)

A 31 year old man was admitted to hospital for abrupt syncope. Two dimensional echocardiogram in the apical four chamber view showed Ebstein's malformation. This is the first documented case of Ebstein's malformation with atrial septal defect, right cor triatriatum, and a right overt accessory atrioventricular pathway.  (+info)

Inferior sinus venosus defect associated with incomplete cor triatriatum dexter and patent foramen ovale. (7/34)

Sinus venosus atrial septal defect (SVD) is a rare cardiac abnormality in adults. Particularly, the inferior type is difficult to depict by transthoracic echocardiography because of its infero-posterior location to the fossa ovalis. We describe the case of a 33-year-old woman whose chest X-ray taken during bronchopneumonia revealed a cardiomegaly. Further echocardiographic investigations showed an underlying inferior SVD, an incomplete cor triatriatum dexter and a large patent foramen ovale (PFO). The diagnosis was confirmed by cardiac magnetic resonance imaging (CMR) and during surgical repair.  (+info)

Spontaneous echo contrast of unexpected etiology. (8/34)

Cor triatriatum sinister is a rare congenital anomaly characterized by the presence of a fibromuscular membrane dividing the left atrium into two chambers: one entering the four pulmonary veins, the other connecting to the mitral valve. The extent of the communication between the two chambers and the presence of associated lesions determine the severity of symptoms and the complications. We report the case of a 20-year-old man firstly diagnosed with obstructive cor triatriatum sinister and severe pulmonary hypertension.  (+info)

Cor triatriatum is a rare congenital heart defect in which there is an abnormal partition within the right atrium, resulting in the presence of three distinct chambers within the atrium. The partition can be a membrane, a band of tissue, or a combination of both. This condition can cause blood flow abnormalities and increase the risk of stroke, heart failure, and other complications. Treatment options may include medications, surgery, or a combination of both, depending on the severity of the condition.

Ebstein anomaly is a rare congenital heart defect that affects the tricuspid valve, which is located between the right atrium and right ventricle of the heart. In this condition, the tricuspid valve is not functioning properly, which can lead to a backup of blood in the right atrium and a decrease in blood flow to the lungs and the rest of the body. The tricuspid valve is made up of three flaps, or leaflets, that open and close to allow blood to flow through the valve. In Ebstein anomaly, one or more of these leaflets are abnormal, which can cause them to bulge into the right atrium or to be attached to the wrong part of the heart. This can make it difficult for the valve to open and close properly, which can lead to a backup of blood in the right atrium and a decrease in blood flow to the lungs and the rest of the body. Ebstein anomaly can also cause the right ventricle to become enlarged and weakened, which can lead to heart failure. It is a congenital heart defect, which means that it is present at birth and is not caused by any known environmental factors. Treatment for Ebstein anomaly may include medications to manage symptoms and improve heart function, or surgery to repair or replace the tricuspid valve.

Heart septal defects, atrial, also known as atrial septal defects (ASDs), are a type of heart defect that occurs when there is a hole in the wall (septum) that separates the two upper chambers of the heart, the atria. This hole allows blood to flow from one atrium to the other, which can cause a variety of symptoms and complications. ASDs can be present at birth (congenital) or can develop later in life (acquired). They are more common in females than males and are often associated with other heart defects. Symptoms of ASDs may include shortness of breath, fatigue, chest pain, and a heart murmur. In some cases, ASDs may not cause any symptoms and may be discovered incidentally during a routine physical examination or imaging test. Treatment for ASDs depends on the size and location of the defect, as well as the presence of any associated heart problems. Small ASDs may not require treatment and may close on their own over time. Larger ASDs may require surgery or other medical interventions to repair the defect and improve heart function.

... : study of 20 cases. Am J Cardiol. Jan 1975;35(1):59-66. [Medline]. Niwayama G. Cor triatriatum. Am Heart J. Feb ... In the adult, cor triatriatum is frequently an isolated finding. Cor triatriatum dextrum is extremely rare and results from the ... Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum sinistrum) or right ... cor triatriatum dextrum) is subdivided by a thin membrane, resulting in three atrial chambers (hence the name). Cor triatriatum ...
This type of abnormality may be confused with cor triatriatum dexter. Very rarely, such a configuration of a large eustachian ...
"Sudden atrial fibrillation associated with acute alcohol ingestion and cor triatriatum". Proceedings. 22 (4): 335-336. doi: ...
A previously undescribed association with cor triatriatum and double right ventricular chamber". Japanese Heart Journal. 27 (1 ...
Cor triatriatum - A membrane that divides one of the atria results in "three" atria (hence "triatriatum"). This tends to affect ... Cor pulmonale - Untreated cor pulmonale can cause right heart failure from chronic pulmonary hypertrophy. Ventricular ...
Cor triatriatum*, specifically cor triatriatum dexter, occurs in dogs and is characterized by a fibrous division of the right ... cor pulmonale). Signs include difficulty breathing, cyanosis, and exercise intolerance. Trapped Neutrophil Syndrome* is an ...
... anemia Copper deficiency familial benign Copper transport disease Coproporhyria Cor biloculare Cor pulmonale Cor triatriatum ...
Acyanotic heart defect Atrial septal defect Cor triatriatum Dextro-Transposition of the great arteries Double aortic arch ...
... heart syndrome 746.8 Other specified congenital anomalies of heart 746.81 Subaortic stenosis congenital 746.82 Cor triatriatum ... 745.3 Common ventricle 745.4 Ventricular septal defect 745.5 Atrial septal defect 745.6 Endocardial cushion defects 745.7 Cor ...
... cor triatriatum MeSH C16.131.240.400.210 - coronary vessel anomalies MeSH C16.131.240.400.220 - crisscross heart MeSH C16.131. ...
... cor triatriatum MeSH C14.240.400.210 - coronary vessel anomalies MeSH C14.240.400.220 - crisscross heart MeSH C14.240.400.280 ... cor triatriatum MeSH C14.280.400.210 - coronary vessel anomalies MeSH C14.280.400.220 - crisscross heart MeSH C14.280.400.280 ...
... anglais, woodwind instrument Cor bovinum and Cor triatriatum, heart disease and defect Cor Caroli and Cor Hydrae, stars Côr ... Look up Cor, cor, or cor- in Wiktionary, the free dictionary. Cor or COR may refer to: Cor people, an ethnic group of Vietnam ... known as COR, a Canadian kosher certification agency Championship Off-Road (COR), an American off-road racing series Cor, a ... IATA airport code COR Corby railway station, UK, station code COR Corio railway station, Victoria, Australia, station code COR ...
Cor triatriatum: study of 20 cases. Am J Cardiol. Jan 1975;35(1):59-66. [Medline]. Niwayama G. Cor triatriatum. Am Heart J. Feb ... In the adult, cor triatriatum is frequently an isolated finding. Cor triatriatum dextrum is extremely rare and results from the ... Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum sinistrum) or right ... cor triatriatum dextrum) is subdivided by a thin membrane, resulting in three atrial chambers (hence the name). Cor triatriatum ...
... cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is divided into 2 compartments by a fold of tissue, a ... cor triatriatum, that is, a heart with 3 atria (triatrial heart), is a congenital anomaly in which the left atrium ( ... Cor triatriatum dextrum. Consider the following conditions in patients with suspected cor triatriatum dextrum:. * Prominent ... Cor triatriatum sinistrum. Consider the following conditions in patients with suspected cor triatriatum sinistrum:. * Bronchial ...
... severe pulmonary hypertension due to cor triatriatum sinister ... severe pulmonary hypertension due to cor triatriatum sinister ... Stunning tornado: severe pulmonary hypertension due to cor triatriatum sinister Xuan Zheng et al. Eur Heart J. 2023. . ...
A rare case of neonatal cyanosis due cor triatriatum dexter and a review of the literature. J Cardiovasc Med (Hagerstown). ... Cor triatriatum dexter, while extremely uncommon, should remain on the differential for cyanosis in a newborn. ... A case series of patients with cor triatriatum dexter: unique cause of neonatal cyanosis. Pediatr Cardiol. 2015;36(1):240-243. ... This video depicts the repair of an extremely rare congenital heart defect known as cor triatriatum dexter. In this condition, ...
Cor Triatriatum. *. Atrial Septal Defect. *. Coarctation of the Aorta. View the correct answer. ...
Other rare heart anomalies include patent foramen ovale; cor triatriatum; patent ductus arteriosus; critical pulmonary stenosis ...
Elevated pulmonary venous pressure: Mitral stenosis, cor triatriatum, obstructed pulmonary venous return ...
Cor triatriatum From NCATS Genetic and Rare Diseases Information Center Cor triatriatum dexter From NCATS Genetic and Rare ...
"Q24.2 Cor triatriatum" "Q243" = "Q24.3 Pulmonary infundibular stenosis" "Q244" = "Q24.4 Congenital subaortic stenosis" "Q245 ... " = "I26.0 Pulmonary embolism with mention of acute cor pulmonale" "I269" = "I26.9 Pulmonary embolism without mention of acute ... cor pulmonale" "I27" = "I27 Other pulmonary heart diseases" "I270" = "I27.0 Primary pulmonary hypertension" "I271" = "I27.1 ...
... - totally 97 synonyms
Cor triatriatum. congenital heart defect in which there is a small extra chamber which results in slowing of the passage of ... Mouth, downturned corners (carp mouth). oral commissures positioned inferior to the midline labial fissure ... abnormally increased distance between the medial canthi (corners of the eye) of the eyelids ... a fold of the skin over the inner corner of the eyes, a broad nasal bridge with a highly arched palate, and streaks of skin ...
Cor Triatriatum Entry term(s). Atrium, Subdivided Left Atriums, Subdivided Left Cor Triatriatum Sinistrum Heart, Triatrial ... Cor Triatriatum - Preferred Concept UI. M0005164. Scope note. A malformation of the heart in which the embryonic common ... Cor Triatriatum Sinistrum. Heart, Triatrial. Hearts, Triatrial. Left Atrium, Subdivided. Left Atriums, Subdivided. Subdivided ...
Cor triatriatum Current Synonym true false 92275010 Accessory atrium Current Synonym true false ...
Cor Triatriatum Preferred Term Term UI T009677. Date01/01/1999. LexicalTag NON. ThesaurusID ... Cor Triatriatum Preferred Concept UI. M0005164. Scope Note. A malformation of the heart in which the embryonic common PULMONARY ... Cor Triatriatum Sinistrum Term UI T764049. Date01/13/2010. LexicalTag NON. ThesaurusID ... Cor Triatriatum. Tree Number(s). C14.240.400.200. C14.280.400.200. C16.131.240.400.200. Unique ID. D003310. RDF Unique ...
Cor Triatriatum Preferred Term Term UI T009677. Date01/01/1999. LexicalTag NON. ThesaurusID ... Cor Triatriatum Preferred Concept UI. M0005164. Scope Note. A malformation of the heart in which the embryonic common PULMONARY ... Cor Triatriatum Sinistrum Term UI T764049. Date01/13/2010. LexicalTag NON. ThesaurusID ... Cor Triatriatum. Tree Number(s). C14.240.400.200. C14.280.400.200. C16.131.240.400.200. Unique ID. D003310. RDF Unique ...
Cor Triatriatum Dexter: A Rare Cause of Aneurysmal Right Atrium Published: October 14, 2021. Pages 253-256 ...
... cor triatriatum; single ventricle; and large ASD (atrio-septal defect) with complete AVCD; cor triatriatum sinistrum with ... in Enugu State had congenital complex cardiac abnormalities and that the commonest forms seen were those with cor triatriatum ...
Cor triatriatum sinister (CTS) is a rare adult congenital heart disease. The usual presentation may vary according to the size ... Evaluation of Pulmonary Hypertension with Exercise Right Heart Catheterization in an Adult Patient with Cor Triatriatum ...
Cor triatriatum dexter. * Coronary sinus atrial septal defect. * Double aortic arch. * Double-outlet left atrium ...
C2849 Congenital Abnormality C99147 Neonatal Research Network Terminology C84651 Cor Triatriatum Cor Triatriatum A rare ... Cor pulmonale most often manifests as right ventricular hypertrophy; it can also lead to right ventricular failure. C95834 ... Signs and symptoms include hearing loss, dystopia canthorum (widely spaced inner corners of the eyes), and changes in the color ... C26693 Aneurysm C99147 Neonatal Research Network Terminology C34478 Chronic Pulmonary Heart Disease Cor Pulmonale Heart disease ...
Article: Stunning tornado: severe pulmonary hypertension due to cor triatriatum sinister. * Article: Resilience Mediates the ...
Cor triatriatum sinister. Diagnosis certain. Stefan Tigges. Published 31 Oct 2022. 87% complete ...
Article: Stunning tornado: severe pulmonary hypertension due to cor triatriatum sinister. * Article: Resilience Mediates the ...
Cor triatriatum 174683=Infundibular pulmonic stenosis 174684=Obstructive anomalies of heart, NEC 174685=Coronary artery ... Cor biloculare 174580=Other anomalies of bulbus cordis and cardiac septal closure 174590=Unspecified defect of septal ... Acute cor pulmonale 141510=Pulmonary embolism and infarction 141600=Primary pulmonary hypertension 141610=Kyphoscoliotic ...
Cor Triatriatum. *Coronary Vessel Anomalies. *Crisscross Heart. *Dextrocardia. *Ductus Arteriosus, Patent. *Ebstein Anomaly ...
Cor pulmonale. Cor triatriatum. Cornelia de Lange syndrome. Coronary heart disease. Cortical dysplasia. Corticobasal ...
Cor Triatriatum [C16.131.240.400.200] * Coronary Vessel Anomalies [C16.131.240.400.210] * Crisscross Heart [C16.131.240.400.220 ...
Cor Triatriatum Sinister and Supravalvular Mitral Stenosis. *Cough. *Cranial Cruciate Ligament Injury and Associated Disorders ...
Anomalies of Pulmonary Venous Return and Cor Triatriatum. *Pulmonary Venous Stenosis. *Surgical Management of Ebstein ...
  • Cor triatriatum (or triatrial heart) is a congenital heart defect where the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is subdivided by a thin membrane, resulting in three atrial chambers (hence the name). (wikipedia.org)
  • Cor triatriatum sinistrum is more common. (wikipedia.org)
  • [ 1 ] cor triatriatum, that is, a heart with three atria (triatrial heart), is a congenital anomaly in which the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is divided into two compartments by a fold of tissue, a membrane, or a fibromuscular band. (medscape.com)
  • The most popular theory holds that cor triatriatum sinister occurs when the common pulmonary vein fails to incorporate the pulmonary circulation into the left atrium and the common pulmonary venous ostium remains narrow (malincorporation theory). (medscape.com)
  • Cor Triatriatum Sinister Associated with Total Anomalous Pulmonary Venous Connection. (bvsalud.org)
  • Cor triatriatum sinister is rare congenital heart disease . (bvsalud.org)
  • Prenatal diagnosis of cor triatriatum sinister may be possible with fetal echocardiography and the diagnosis can be made earlier than postnatal imaging techniques . (bvsalud.org)
  • In the fetal echocardiography performed in our patient , cor triatriatum sinister was present and the main pathology was the flow of right and left pulmonary vein return from the accessory atrium to the right atrium . (bvsalud.org)
  • 3. Percutaneous balloon dilatation of cor triatriatum sinister. (prime-cardiology.com)
  • Subtotal cor triatriatum with left partial anomalous pulmonary venous return. (wikipedia.org)
  • Fig. 5 and 6) We made the diagnosis of cor triatriatum with partial atrioventricular septal defect and severe pulmonary hypertension in heart failure. (ispub.com)
  • Cor triatriatum (subdivided left atrium). (wikipedia.org)
  • ii] Cor triatriatum (CT) represents 0.1-0.4% of all congenital cardiac malformations and usually refers to the left atrium. (ispub.com)
  • Cor triatriatum dextrum is extremely rare and results from the complete persistence of the right sinus valve of the embryonic heart. (wikipedia.org)
  • Cor triatriatum represents 0.1% of all congenital cardiac malformations and may be associated with other cardiac defects in as many as 50% of cases. (wikipedia.org)
  • Cor triatriatum is a rare congenital anomaly with a ratio of men to women of 1.5:1. (ispub.com)
  • Cor triatriatum sinister presenting in the adult as mitral stenosis. (medscape.com)
  • Subtotal cor triatriatum with left partial anomalous pulmonary venous return. (wikipedia.org)
  • Biglioli P, Gherli T, Mastroni P, Puliga V, Alamanni F. A case of left cor triatriatum associated with an interatrial defect with partial anomalous venous return. (medscape.com)
  • Echocardiographic diagnosis of cor triatriatum sinister in the adult. (medscape.com)
  • Hamdan R, Mirochnik N, Celermajer D, Nassar P, Iserin L. Cor Triatriatum Sinister diagnosed in adult life with three dimensional transesophageal echocardiography. (medscape.com)
  • Cor triatriatum sinister (CTS) is a rare adult congenital heart disease. (bvsalud.org)
  • This video depicts the repair of an extremely rare congenital heart defect known as cor triatriatum dexter. (figshare.com)
  • Cor-triatriatum dexter with associated cyanosis in a 3-month-old girl. (medscape.com)
  • A large thin membrane consistent with cor triatriatum dexter was identified, creating intermittent obstruction to flow into the right ventricle. (figshare.com)
  • Cor triatriatum dexter, while extremely uncommon, should remain on the differential for cyanosis in a newborn. (figshare.com)
  • Mackman CA, Liedel JL, Woods RK, Samyn MM. A case series of patients with cor triatriatum dexter: unique cause of neonatal cyanosis. (figshare.com)
  • A rare case of neonatal cyanosis due 'cor triatriatum dexter' and a review of the literature. (figshare.com)
  • Diagnostic features and pitfalls in the two-dimensional echocardiographic evaluation of a child with cor triatriatum. (wikipedia.org)
  • Cor triatriatum represents 0.1% of all congenital cardiac malformations and may be associated with other cardiac defects in as many as 50% of cases. (wikipedia.org)
  • Cor triatriatum: study of 20 cases. (wikipedia.org)
  • Cor triatriatum in adults: three new cases and a brief review. (medscape.com)