Budd-Chiari Syndrome: A condition in which the hepatic venous outflow is obstructed anywhere from the small HEPATIC VEINS to the junction of the INFERIOR VENA CAVA and the RIGHT ATRIUM. Usually the blockage is extrahepatic and caused by blood clots (THROMBUS) or fibrous webs. Parenchymal FIBROSIS is uncommon.Radiology, Interventional: Subspecialty of radiology that combines organ system radiography, catheter techniques and sectional imaging.Portasystemic Shunt, Transjugular Intrahepatic: A type of surgical portasystemic shunt to reduce portal hypertension with associated complications of esophageal varices and ascites. It is performed percutaneously through the jugular vein and involves the creation of an intrahepatic shunt between the hepatic vein and portal vein. The channel is maintained by a metallic stent. The procedure can be performed in patients who have failed sclerotherapy and is an additional option to the surgical techniques of portocaval, mesocaval, and splenorenal shunts. It takes one to three hours to perform. (JAMA 1995;273(23):1824-30)Syringomyelia: Longitudinal cavities in the spinal cord, most often in the cervical region, which may extend for multiple spinal levels. The cavities are lined by dense, gliogenous tissue and may be associated with SPINAL CORD NEOPLASMS; spinal cord traumatic injuries; and vascular malformations. Syringomyelia is marked clinically by pain and PARESTHESIA, muscular atrophy of the hands, and analgesia with thermoanesthesia of the hands and arms, but with the tactile sense preserved (sensory dissociation). Lower extremity spasticity and incontinence may also develop. (From Adams et al., Principles of Neurology, 6th ed, p1269)Syndrome: A characteristic symptom complex.Foramen Magnum: The large hole at the base of the skull through which the SPINAL CORD passes.Encephalocele: Brain tissue herniation through a congenital or acquired defect in the skull. The majority of congenital encephaloceles occur in the occipital or frontal regions. Clinical features include a protuberant mass that may be pulsatile. The quantity and location of protruding neural tissue determines the type and degree of neurologic deficit. Visual defects, psychomotor developmental delay, and persistent motor deficits frequently occur.Platybasia: A developmental deformity of the occipital bone and upper end of the cervical spine, in which the latter appears to have pushed the floor of the occipital bone upward. (Dorland, 27th ed)Cranial Fossa, Posterior: The infratentorial compartment that contains the CEREBELLUM and BRAIN STEM. It is formed by the posterior third of the superior surface of the body of the sphenoid (SPHENOID BONE), by the occipital, the petrous, and mastoid portions of the TEMPORAL BONE, and the posterior inferior angle of the PARIETAL BONE.Meningomyelocele: Congenital, or rarely acquired, herniation of meningeal and spinal cord tissue through a bony defect in the vertebral column. The majority of these defects occur in the lumbosacral region. Clinical features include PARAPLEGIA, loss of sensation in the lower body, and incontinence. This condition may be associated with the ARNOLD-CHIARI MALFORMATION and HYDROCEPHALUS. (From Joynt, Clinical Neurology, 1992, Ch55, pp35-6)Decompression, Surgical: A surgical operation for the relief of pressure in a body compartment or on a body part. (From Dorland, 28th ed)Subarachnoid Space: The space between the arachnoid membrane and PIA MATER, filled with CEREBROSPINAL FLUID. It contains large blood vessels that supply the BRAIN and SPINAL CORD.Decompressive Craniectomy: Excision of part of the skull. This procedure is used to treat elevated intracranial pressure that is unresponsive to conventional treatment.Down Syndrome: A chromosome disorder associated either with an extra chromosome 21 or an effective trisomy for chromosome 21. Clinical manifestations include hypotonia, short stature, brachycephaly, upslanting palpebral fissures, epicanthus, Brushfield spots on the iris, protruding tongue, small ears, short, broad hands, fifth finger clinodactyly, Simian crease, and moderate to severe INTELLECTUAL DISABILITY. Cardiac and gastrointestinal malformations, a marked increase in the incidence of LEUKEMIA, and the early onset of ALZHEIMER DISEASE are also associated with this condition. Pathologic features include the development of NEUROFIBRILLARY TANGLES in neurons and the deposition of AMYLOID BETA-PROTEIN, similar to the pathology of ALZHEIMER DISEASE. (Menkes, Textbook of Child Neurology, 5th ed, p213)Pelvic Bones: Bones that constitute each half of the pelvic girdle in VERTEBRATES, formed by fusion of the ILIUM; ISCHIUM; and PUBIC BONE.Spinal Canal: The cavity within the SPINAL COLUMN through which the SPINAL CORD passes.Cerebrospinal Fluid Pressure: Manometric pressure of the CEREBROSPINAL FLUID as measured by lumbar, cerebroventricular, or cisternal puncture. Within the cranial cavity it is called INTRACRANIAL PRESSURE.Metabolic Syndrome X: A cluster of metabolic risk factors for CARDIOVASCULAR DISEASES and TYPE 2 DIABETES MELLITUS. The major components of metabolic syndrome X include excess ABDOMINAL FAT; atherogenic DYSLIPIDEMIA; HYPERTENSION; HYPERGLYCEMIA; INSULIN RESISTANCE; a proinflammatory state; and a prothrombotic (THROMBOSIS) state. (from AHA/NHLBI/ADA Conference Proceedings, Circulation 2004; 109:551-556)Osteotomy: The surgical cutting of a bone. (Dorland, 28th ed)Hepatic Veins: Veins which drain the liver.Venous Thrombosis: The formation or presence of a blood clot (THROMBUS) within a vein.Vena Cava, Inferior: The venous trunk which receives blood from the lower extremities and from the pelvic and abdominal organs.Portal Vein: A short thick vein formed by union of the superior mesenteric vein and the splenic vein.Thrombosis: Formation and development of a thrombus or blood clot in the blood vessel.Phlebography: Radiographic visualization or recording of a vein after the injection of contrast medium.Reye Syndrome: A form of encephalopathy with fatty infiltration of the LIVER, characterized by brain EDEMA and VOMITING that may rapidly progress to SEIZURES; COMA; and DEATH. It is caused by a generalized loss of mitochondrial function leading to disturbances in fatty acid and CARNITINE metabolism.Portasystemic Shunt, Surgical: Surgical venous shunt between the portal and systemic circulation to effect decompression of the portal circulation. It is performed primarily in the treatment of bleeding esophageal varices resulting from portal hypertension. Types of shunt include portacaval, splenorenal, mesocaval, splenocaval, left gastric-caval (coronary-caval), portarenal, umbilicorenal, and umbilicocaval.Galactosemias: A group of inherited enzyme deficiencies which feature elevations of GALACTOSE in the blood. This condition may be associated with deficiencies of GALACTOKINASE; UDPGLUCOSE-HEXOSE-1-PHOSPHATE URIDYLYLTRANSFERASE; or UDPGLUCOSE 4-EPIMERASE. The classic form is caused by UDPglucose-Hexose-1-Phosphate Uridylyltransferase deficiency, and presents in infancy with FAILURE TO THRIVE; VOMITING; and INTRACRANIAL HYPERTENSION. Affected individuals also may develop MENTAL RETARDATION; JAUNDICE; hepatosplenomegaly; ovarian failure (PRIMARY OVARIAN INSUFFICIENCY); and cataracts. (From Menkes, Textbook of Child Neurology, 5th ed, pp61-3)Software Design: Specifications and instructions applied to the software.Electronic Mail: Messages between computer users via COMPUTER COMMUNICATION NETWORKS. This feature duplicates most of the features of paper mail, such as forwarding, multiple copies, and attachments of images and other file types, but with a speed advantage. The term also refers to an individual message sent in this way.Leukemia, Myelogenous, Chronic, BCR-ABL Positive: Clonal hematopoetic disorder caused by an acquired genetic defect in PLURIPOTENT STEM CELLS. It starts in MYELOID CELLS of the bone marrow, invades the blood and then other organs. The condition progresses from a stable, more indolent, chronic phase (LEUKEMIA, MYELOID, CHRONIC PHASE) lasting up to 7 years, to an advanced phase composed of an accelerated phase (LEUKEMIA, MYELOID, ACCELERATED PHASE) and BLAST CRISIS.Leukemia, Myeloid: Form of leukemia characterized by an uncontrolled proliferation of the myeloid lineage and their precursors (MYELOID PROGENITOR CELLS) in the bone marrow and other sites.Benzamides: BENZOIC ACID amides.Pregnancy: The status during which female mammals carry their developing young (EMBRYOS or FETUSES) in utero before birth, beginning from FERTILIZATION to BIRTH.International Classification of Diseases: A system of categories to which morbid entries are assigned according to established criteria. Included is the entire range of conditions in a manageable number of categories, grouped to facilitate mortality reporting. It is produced by the World Health Organization (From ICD-10, p1). The Clinical Modifications, produced by the UNITED STATES DEPT. OF HEALTH AND HUMAN SERVICES, are larger extensions used for morbidity and general epidemiological purposes, primarily in the U.S.Databases, Factual: Extensive collections, reputedly complete, of facts and data garnered from material of a specialized subject area and made available for analysis and application. The collection can be automated by various contemporary methods for retrieval. The concept should be differentiated from DATABASES, BIBLIOGRAPHIC which is restricted to collections of bibliographic references.Clinical Coding: Process of substituting a symbol or code for a term such as a diagnosis or procedure. (from Slee's Health Care Terms, 3d ed.)Primary Myelofibrosis: A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.Calreticulin: A multifunctional protein that is found primarily within membrane-bound organelles. In the ENDOPLASMIC RETICULUM it binds to specific N-linked oligosaccharides found on newly-synthesized proteins and functions as a MOLECULAR CHAPERONE that may play a role in PROTEIN FOLDING or retention and degradation of misfolded proteins. In addition calreticulin is a major storage form for CALCIUM and functions as a calcium-signaling molecule that can regulate intracellular calcium HOMEOSTASIS.Thrombocythemia, Essential: A clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.Myeloproliferative Disorders: Conditions which cause proliferation of hemopoietically active tissue or of tissue which has embryonic hemopoietic potential. They all involve dysregulation of multipotent MYELOID PROGENITOR CELLS, most often caused by a mutation in the JAK2 PROTEIN TYROSINE KINASE.CaliforniaInternal Medicine: A medical specialty concerned with the diagnosis and treatment of diseases of the internal organ systems of adults.Retinal Vein Occlusion: Blockage of the RETINAL VEIN. Those at high risk for this condition include patients with HYPERTENSION; DIABETES MELLITUS; ATHEROSCLEROSIS; and other CARDIOVASCULAR DISEASES.Autopsy: Postmortem examination of the body.Lymphedema: Edema due to obstruction of lymph vessels or disorders of the lymph nodes.Terminology as Topic: The terms, expressions, designations, or symbols used in a particular science, discipline, or specialized subject area.Ascites: Accumulation or retention of free fluid within the peritoneal cavity.Plasma: The residual portion of BLOOD that is left after removal of BLOOD CELLS by CENTRIFUGATION without prior BLOOD COAGULATION.Carcinoma, Hepatocellular: A primary malignant neoplasm of epithelial liver cells. It ranges from a well-differentiated tumor with EPITHELIAL CELLS indistinguishable from normal HEPATOCYTES to a poorly differentiated neoplasm. The cells may be uniform or markedly pleomorphic, or form GIANT CELLS. Several classification schemes have been suggested.Liver Neoplasms: Tumors or cancer of the LIVER.Liver Cirrhosis: Liver disease in which the normal microcirculation, the gross vascular anatomy, and the hepatic architecture have been variably destroyed and altered with fibrous septa surrounding regenerated or regenerating parenchymal nodules.Liver Regeneration: Repair or renewal of hepatic tissue.Liver: A large lobed glandular organ in the abdomen of vertebrates that is responsible for detoxification, metabolism, synthesis and storage of various substances.Factor VIII: Blood-coagulation factor VIII. Antihemophilic factor that is part of the factor VIII/von Willebrand factor complex. Factor VIII is produced in the liver and acts in the intrinsic pathway of blood coagulation. It serves as a cofactor in factor X activation and this action is markedly enhanced by small amounts of thrombin.Gastroenterology: A subspecialty of internal medicine concerned with the study of the physiology and diseases of the digestive system and related structures (esophagus, liver, gallbladder, and pancreas).Hemophilia A: The classic hemophilia resulting from a deficiency of factor VIII. It is an inherited disorder of blood coagulation characterized by a permanent tendency to hemorrhage.Hearing Loss, Unilateral: Partial or complete hearing loss in one ear.Polycythemia Vera: A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs.Vascular Patency: The degree to which BLOOD VESSELS are not blocked or obstructed.Stents: Devices that provide support for tubular structures that are being anastomosed or for body cavities during skin grafting.Thrombophilia: A disorder of HEMOSTASIS in which there is a tendency for the occurrence of THROMBOSIS.Dictionaries as Topic: Lists of words, usually in alphabetical order, giving information about form, pronunciation, etymology, grammar, and meaning.ArgentinaAdenocarcinoma: A malignant epithelial tumor with a glandular organization.Splenic Neoplasms: Tumors or cancer of the SPLEEN.Jaagsiekte sheep retrovirus: A BETARETROVIRUS that causes pulmonary adenomatosis in sheep (PULMONARY ADENOMATOSIS, OVINE).Pulmonary Adenomatosis, Ovine: A contagious, neoplastic, pulmonary disease of sheep characterized by hyperplasia and hypertrophy of pneumocytes and epithelial cells of the lung. It is caused by JAAGSIEKTE SHEEP RETROVIRUS.Splenic DiseasesCarcinosarcoma: A malignant neoplasm that contains elements of carcinoma and sarcoma so extensively intermixed as to indicate neoplasia of epithelial and mesenchymal tissue. (Stedman, 25th ed)Jasminum: A plant genus of the family OLEACEAE. Members contain secoiridoid glucosides and this is the source of oil of jasmine.Autonomic Agents: Agents affecting the function of, or mimicking the actions of, the autonomic nervous system and thereby having an effect on such processes as respiration, circulation, digestion, body temperature regulation, certain endocrine gland secretions, etc.Gelsemium: A plant genus of the family LOGANIACEAE (classified by some botanists as Gelsemiaceae). The sometimes used common name of trumpet flower is also used for DATURA.Mothers: Female parents, human or animal.Pyloric Antrum: The region between the sharp indentation at the lower third of the STOMACH (incisura angularis) and the junction of the PYLORUS with the DUODENUM. Pyloric antral glands contain mucus-secreting cells and gastrin-secreting endocrine cells (G CELLS).Venae Cavae: The inferior and superior venae cavae.Foreign Bodies: Inanimate objects that become enclosed in the body.Eye Foreign Bodies: Inanimate objects that become enclosed in the eye.Medical Illustration: The field which deals with illustrative clarification of biomedical concepts, as in the use of diagrams and drawings. The illustration may be produced by hand, photography, computer, or other electronic or mechanical methods.Crowdsourcing: Social media model for enabling public involvement and recruitment in participation. Use of social media to collect feedback and recruit volunteer subjects.Coronary Thrombosis: Coagulation of blood in any of the CORONARY VESSELS. The presence of a blood clot (THROMBUS) often leads to MYOCARDIAL INFARCTION.Sinus Thrombosis, Intracranial: Formation or presence of a blood clot (THROMBUS) in the CRANIAL SINUSES, large endothelium-lined venous channels situated within the SKULL. Intracranial sinuses, also called cranial venous sinuses, include the superior sagittal, cavernous, lateral, petrous sinuses, and many others. Cranial sinus thrombosis can lead to severe HEADACHE; SEIZURE; and other neurological defects.Encyclopedias as Topic: Works containing information articles on subjects in every field of knowledge, usually arranged in alphabetical order, or a similar work limited to a special field or subject. (From The ALA Glossary of Library and Information Science, 1983)Pulmonary Embolism: Blocking of the PULMONARY ARTERY or one of its branches by an EMBOLUS.Fibrin: A protein derived from FIBRINOGEN in the presence of THROMBIN, which forms part of the blood clot.Platelet-Derived Growth Factor: Mitogenic peptide growth hormone carried in the alpha-granules of platelets. It is released when platelets adhere to traumatized tissues. Connective tissue cells near the traumatized region respond by initiating the process of replication.Carotid Artery Thrombosis: Blood clot formation in any part of the CAROTID ARTERIES. This may produce CAROTID STENOSIS or occlusion of the vessel, leading to TRANSIENT ISCHEMIC ATTACK; CEREBRAL INFARCTION; or AMAUROSIS FUGAX.Fibrinolysis: The natural enzymatic dissolution of FIBRIN.Liver Diseases: Pathological processes of the LIVER.EuropeLiver Diseases, Alcoholic: Liver diseases associated with ALCOHOLISM. It usually refers to the coexistence of two or more subentities, i.e., ALCOHOLIC FATTY LIVER; ALCOHOLIC HEPATITIS; and ALCOHOLIC CIRRHOSIS.Chemoembolization, Therapeutic: Administration of antineoplastic agents together with an embolizing vehicle. This allows slow release of the agent as well as obstruction of the blood supply to the neoplasm.Mesentery: A layer of the peritoneum which attaches the abdominal viscera to the ABDOMINAL WALL and conveys their blood vessels and nerves.Glucose Solution, Hypertonic: Solution that is usually 10 percent glucose but may be higher. An isotonic solution of glucose is 5 percent.Abdominal Wall: The outer margins of the ABDOMEN, extending from the osteocartilaginous thoracic cage to the PELVIS. Though its major part is muscular, the abdominal wall consists of at least seven layers: the SKIN, subcutaneous fat, deep FASCIA; ABDOMINAL MUSCLES, transversalis fascia, extraperitoneal fat, and the parietal PERITONEUM.Cell Wall: The outermost layer of a cell in most PLANTS; BACTERIA; FUNGI; and ALGAE. The cell wall is usually a rigid structure that lies external to the CELL MEMBRANE, and provides a protective barrier against physical or chemical agents.Jejunum: The middle portion of the SMALL INTESTINE, between DUODENUM and ILEUM. It represents about 2/5 of the remaining portion of the small intestine below duodenum.Intestine, Small: The portion of the GASTROINTESTINAL TRACT between the PYLORUS of the STOMACH and the ILEOCECAL VALVE of the LARGE INTESTINE. It is divisible into three portions: the DUODENUM, the JEJUNUM, and the ILEUM.Liver Failure, Acute: A form of rapid-onset LIVER FAILURE, also known as fulminant hepatic failure, caused by severe liver injury or massive loss of HEPATOCYTES. It is characterized by sudden development of liver dysfunction and JAUNDICE. Acute liver failure may progress to exhibit cerebral dysfunction even HEPATIC COMA depending on the etiology that includes hepatic ISCHEMIA, drug toxicity, malignant infiltration, and viral hepatitis such as post-transfusion HEPATITIS B and HEPATITIS C.Liver Failure: Severe inability of the LIVER to perform its normal metabolic functions, as evidenced by severe JAUNDICE and abnormal serum levels of AMMONIA; BILIRUBIN; ALKALINE PHOSPHATASE; ASPARTATE AMINOTRANSFERASE; LACTATE DEHYDROGENASES; and albumin/globulin ratio. (Blakiston's Gould Medical Dictionary, 4th ed)Hepatic Encephalopathy: A syndrome characterized by central nervous system dysfunction in association with LIVER FAILURE, including portal-systemic shunts. Clinical features include lethargy and CONFUSION (frequently progressing to COMA); ASTERIXIS; NYSTAGMUS, PATHOLOGIC; brisk oculovestibular reflexes; decorticate and decerebrate posturing; MUSCLE SPASTICITY; and bilateral extensor plantar reflexes (see REFLEX, BABINSKI). ELECTROENCEPHALOGRAPHY may demonstrate triphasic waves. (From Adams et al., Principles of Neurology, 6th ed, pp1117-20; Plum & Posner, Diagnosis of Stupor and Coma, 3rd ed, p222-5)Liver Transplantation: The transference of a part of or an entire liver from one human or animal to another.Hypnotics and Sedatives: Drugs used to induce drowsiness or sleep or to reduce psychological excitement or anxiety.Liver, Artificial: Devices for simulating the activities of the liver. They often consist of a hybrid between both biological and artificial materials.Acetaminophen: Analgesic antipyretic derivative of acetanilide. It has weak anti-inflammatory properties and is used as a common analgesic, but may cause liver, blood cell, and kidney damage.

Managing Budd-Chiari syndrome: a retrospective review of percutaneous hepatic vein angioplasty and surgical shunting. (1/234)

BACKGROUND: The role of percutaneous hepatic vein angioplasty in the management of Budd-Chiari syndrome has not been well defined. Over a 10 year period at our unit, we have often used this technique in cases of short length hepatic vein stenosis or occlusion, reserving surgical mesocaval shunting for cases of diffuse hepatic vein occlusion or failed angioplasty. AIMS: To review the outcome of angioplasty and surgical shunting to define their respective roles. PATIENTS: All patients treated by angioplasty or surgical shunting for non-malignant hepatic vein obstruction over a ten year period from 1987 to 1996. METHODS: A case note review of pretreatment features and clinical outcome. RESULTS: Angioplasty was attempted in 21 patients with patent hepatic vein branches and was successful in 18; in three patients treatment was unsuccessful and these patients had surgical shunts. Fifteen patients were treated by surgical shunting only. Mortality according to definitive treatment was 3/18 following angioplasty and 8/18 following surgery; in most cases this reflected high risk status prior to treatment. Venous or shunt reocclusion rates were similar for both groups and were associated with subtherapeutic warfarin in half of these cases. Most surviving patients in both groups are asymptomatic although one surgical patient has chronic hepatic encephalopathy. CONCLUSION: With appropriate case selection, many patients with Budd-Chiari syndrome caused by short length hepatic vein stenosis or occlusion may be managed successfully by angioplasty alone. Medium term outcome is good following this procedure provided that anticoagulation is maintained. Further follow up is required to assess for definitive benefits but we suggest that this should be included as a valid initial approach in the algorithm for management of Budd-Chiari syndrome.  (+info)

Results of surgical treatment (modified Sugiura-Futagawa operation) of portal hypertension associated to complete splenomesoportal thrombosis and cirrhosis. (2/234)

BACKGROUND: Hemorrhagic portal hypertension, secondary to both intrahepatic and extrahepatic portal hypertension, is an uncommon entity. In this condition, the extrahepatic and the intrahepatic obstruction of the portal vein, due to chronic liver disease, produce a more severe form of hemorrhagic portal hypertension that is more difficult to control. The results of surgical treatment (modified Sugiura-Futagawa operation) in this subset of patients is analyzed. METHODS: Among 714 patients with a history of hemorrhagic portal hypertension, 14 cases were found with histologically proven liver cirrhosis and complete splenomesoportal thrombosis demonstrated by means of preoperative angiography. Patients with incomplete (partial) splenomesoportal thrombosis were excluded. There were nine males and 5 females with a mean age of 51 years. Alcoholic cirrhosis was demonstrated in 50% of the cases, post hepatitic cirrhosis in 28%, primary biliary cirrhosis in 7%, and cryptogenic cirrhosis in 14%. There were nine Child-Pugh A and 5 B cases. All cases were treated by means of our modified Sugiura-Futagawa procedure. RESULTS: Bleeding recurrence from esophagogastric varices was shown in one case, colonic varices in one case and hypertensive gastropathy in another of the survivors. Post operative encephalopathy was shown in 3 of the cases. The thirty-six month survival rate was 30% (Kaplan-Meier). CONCLUSIONS: The combination of intrahepatic plus extrahepatic portal hypertension has a worse prognosis. Treatment options are limited (sclerotherapy and/or devascularization), because shunt surgery, TIPS and liver transplantation have a very restricted role and postoperative outcome is poor.  (+info)

Successful twin pregnancy in a dual-transplant couple resulting from in-vitro fertilization and intracytoplasmic sperm injection: case report. (3/234)

There are numerous reports of successful pregnancy following liver transplantation. Little information is available regarding the incidence and management of infertility in transplant recipients, particularly the use of artificial reproductive technologies. We present a case of a successful twin pregnancy resulting from in-vitro fertilization with intracytoplasmic sperm injection (IVF/ICSI) in a liver transplant recipient, whose partner was a renal transplant recipient with severe oligozoospermia. With careful evaluation and monitoring, and the involvement of appropriate consultants, artificial reproductive technologies can be safely used in transplant recipient couples experiencing infertility.  (+info)

A 27-year experience with surgical treatment of Budd-Chiari syndrome. (4/234)

OBJECTIVE: To determine the effects of surgical portal decompression in Budd-Chiari syndrome (BCS) on survival, quality of life, shunt patency, liver function, portal hemodynamics, and hepatic morphology during periods ranging from 3.5 to 27 years. SUMMARY BACKGROUND DATA: Experiments in the authors' laboratory showed that surgical portal decompression reversed the deleterious effects of BCS on the liver. This study was aimed at determining whether similar benefit could be obtained in patients with BCS. METHODS: From 1972 to 1999, the authors conducted prospective studies of the treatment of 60 patients with BCS who were divided into three groups: the first had occlusion confined to the hepatic veins treated by direct side-to-side portacaval shunt (SSPCS); the second had occlusion involving the inferior vena cava (IVC) treated by a portal decompressive procedure that bypassed the obstructed IVC; and the third group, who had advanced cirrhosis and hepatic decompensation and were referred too late for treatment by portal decompression, required orthotopic liver transplantation. RESULTS: In the 32 patients with BCS resulting from hepatic vein occlusion alone, SSPCS had a surgical death rate of 3%, and 94% of the patients were alive 3.5 to 27 years after surgery. All 31 survivors remained free of ascites and almost all had normal liver function. No patient with a patent shunt had encephalopathy. The SSPCS remained patent in all but one patient. Liver biopsies showed no evidence of congestion or necrosis, and 48% of the biopsies were diagnosed as normal. Mesoatrial shunt was performed in eight patients with BCS caused by IVC thrombosis. All patients survived surgery, but five subsequently developed thrombosis of the synthetic graft and died. Because of the poor results, mesoatrial shunt was abandoned. Instead, a high-flow combination shunt was introduced, consisting of SSPCS combined with a cavoatrial shunt (CAS) through a Gore-Tex graft. There were no surgical or long-term deaths among 10 patients who underwent combined SSPCS and CAS, and the shunts functioned effectively during 4 to 16 years of follow-up. Ten patients with advanced cirrhosis were referred too late to benefit from surgical portal decompression, and they were approved and listed for orthotopic liver transplantation. Three patients died of liver failure while awaiting a transplant, and four patients died after the transplant. The 1- and 5-year survival rates were 40% and 30%, respectively. CONCLUSIONS: SSPCS in BCS with hepatic vein occlusion alone results in reversal of liver damage, correction of hemodynamic disturbances, prolonged survival, and good quality of life when performed early in the course of BCS. Similarly good results are obtained with combined SSPCS and CAS in patients with BCS resulting from IVC occlusion. In contrast, mesoatrial shunt has been discontinued in the authors' program because of an unacceptable incidence of graft thrombosis and death. In patients with advanced cirrhosis from long-standing, untreated BCS, orthotopic liver transplantation is the only hope of relief and results in the salvage of some patients. The key to long survival in BCS is prompt diagnosis and treatment by portal decompression.  (+info)

Successful liver transplantation in a patient with Budd-Chiari syndrome caused by homozygous factor V Leiden. (5/234)

Budd-Chiari syndrome (BCS) is a rare form of portal hypertension characterized by hepatic venous outflow obstruction. Although hematologic disorders are the most common cause of this syndrome, to date, 30% of the cases have been classified as idiopathic. Resistance to activated protein C caused by factor V Leiden is the most common cause of thrombophilia; its role in the pathogenesis of BCS is now becoming apparent. We report successful liver transplantation in a patient with BCS caused by homozygous factor V Leiden. The patient was administered standard heparin anticoagulation until activated protein C resistance was normalized by the liver allograft. Liver transplantation corrected the thrombophilic state. The patient has excellent graft function, is not on anticoagulation therapy, and has had no recurrent venous thrombosis at 5 months posttransplantation. Activated protein C resistance caused by the factor V Leiden mutation may be responsible for idiopathic cases of BCS. To avoid unnecessary long-term anticoagulation after liver transplantation, factor V Leiden should be considered as a pathogenic factor in BCS. In addition, because of the high prevalence of factor V Leiden in the world population, cadaveric organ donors with a history of venous thrombosis should be screened for activated protein C resistance lest thrombophilia be transmitted to the recipient.  (+info)

Factor V Leiden mutation, prothrombin gene mutation, and deficiencies in coagulation inhibitors associated with Budd-Chiari syndrome and portal vein thrombosis: results of a case-control study. (6/234)

In a collaborative multicenter case-control study, we investigated the effect of factor V Leiden mutation, prothrombin gene mutation, and inherited deficiencies of protein C, protein S, and antithrombin on the risk of Budd-Chiari syndrome (BCS) and portal vein thrombosis (PVT). We compared 43 BCS patients and 92 PVT patients with 474 population-based controls. The relative risk of BCS was 11.3 (95% CI 4.8-26.5) for individuals with factor V Leiden mutation, 2.1(95% CI 0.4-9.6) for those with prothrombin gene mutation, and 6.8 (95% CI 1.9-24.4) for those with protein C deficiency. The relative risk of PVT was 2.7 (95% CI 1.1-6.9) for individuals with factor V Leiden mutation, 1.4 (95% CI 0.4-5.2) for those with prothrombin gene mutation, and 4.6 (95% CI 1.5-14.1) for those with protein C deficiency. The relative risk of BCS or PVT was not increased in the presence of inherited protein S or antithrombin deficiency. Concurrence of either acquired or inherited thrombotic risk factors was observed in 26% of the BCS patients and 37% of the PVT patients. We conclude that factor V Leiden mutation and hereditary protein C deficiency appear to be important risk factors for BCS and PVT. Although the prevalence of the prothrombin gene mutation was increased, it was not found to be a significant risk factor for BCS and PVT. The coexistence of thrombogenic risk factors in many patients indicates that BCS and PVT can be the result of a combined effect of different pathogenetic mechanisms.  (+info)

Successful outcome of orthotopic liver transplantation in patients with preexisting malignant states. (7/234)

Preexisting malignancy is considered a relative contraindication to orthotopic liver transplantation (OLT) because of the risk of tumor recurrence. The purpose of this study is to assess the outcome of OLT in patients with a preexistent malignant state. Of 1,097 OLTs performed between 1989 and 1999 at King's College Hospital (London, UK), 18 patients had a pretransplantation malignant state, including 6 cases of myeloproliferative disorder (MPD) presenting as Budd-Chiari syndrome. Those patients with solid-organ malignancies had their tumor detected at an early stage and underwent curative treatment before or during OLT. Patients were followed up for a median of 71 months (range, 1 to 119 months) post-OLT, and the rates of rejection and malignancy were compared with those of transplant recipients without preexisting malignancy during the same period. One patient had a recurrence of his primary malignancy (non-Hodgkin's lymphoma) after 27 months, whereas another patient developed a de novo posttransplant lymphoproliferative disorder after 57 months. One patient with MPD developed acute leukemia 72 months after OLT. In comparison, of 1,079 OLTs performed in patients without preexisting malignancy during the same period, there were 34 cases of de novo malignancies. The rate of rejection in patients with and without preexisting malignancy was similar. Successful medium-term outcome after OLT can be achieved in carefully selected patients with preexisting malignancy providing the malignancy is amenable to curative treatment before or at OLT. Primary MPDs responsible for Budd-Chiari syndrome should not be considered a contraindication to OLT.  (+info)

Factor V Leiden related Budd-Chiari syndrome. (8/234)

BACKGROUND: The role of factor V Leiden as a cause of Budd-Chiari syndrome has only recently been described. AIMS: To assess the specific features of factor V Leiden related Budd-Chiari syndrome. PATIENTS: Sixty three consecutive patients with hepatic vein or terminal inferior vena cava thrombosis. METHODS: Standardised chart review. RESULTS: Factor V Leiden was found in 20 patients (31% (95% CI 20-43)). In the subgroup of patients with, compared with the subgroup without, factor V Leiden, a combination of prothrombotic states was more common (70% (95% CI 50-90) v 14% (95% CI 3-24)); inferior vena cava thrombosis was more frequent (40% (95% CI 19-61) v 7% (95% CI 0-14)); and distribution of initial alanine aminotransferase values was bimodal (almost normal or extremely increased) versus unimodal (p=0.003). Factor V Leiden accounted for four of five cases of massive ischaemic necrosis (transaminases >50-fold the upper limit of normal values) (p=0.014), and also for all three cases developing during pregnancy. Patients with and without factor V Leiden did not differ with regard to mortality, portosytemic shunting, or listing for liver transplantation. Hepatocellular carcinoma developed in two patients; both had factor V Leiden and indolent obstruction of the inferior vena cava. CONCLUSIONS: In patients with Budd-Chiari syndrome, factor V Leiden (a) is common; (b) precipitates thrombosis mostly when combined with another risk factor; (c) is associated with one of two contrasting clinical pictures: indolent thrombosis-particularly of the inferior vena cava-or massive ischaemic necrosis; and (d) is a major cofactor of Budd-Chiari syndrome developing during pregnancy.  (+info)

*Budd-Chiari syndrome

... )". "The Budd-Chiari syndrome: a review". "Budd-Chiari syndrome: long-term survival and factors affecting ... "Budd-Chiari Syndrome: clinical patterns and therapy". "Budd-Chiari syndrome: etiology, diagnosis and management". "Case records ... independently of Budd-Chiari syndrome. It is named after George Budd, a British physician, and Hans Chiari, an Austrian ... Budd-Chiari syndrome at Who Named It? Budd G (1845). On diseases of the liver. London: John Churchill. p. 135. Brit Lib. ...

*Portal vein thrombosis

Pylephlebitis Budd-Chiari syndrome Strous, Rael D.; Edelman, Morris C. (2007). "Eponyms and the Nazi Era: Time to Remember and ... Portal vein thrombosis, previously known as Cauchois-Eppinger-Frugoni syndrome, is a form of venous thrombosis affecting the ...

*Abdominojugular test

Negative abdominojugular reflux is seen in Budd-Chiari syndrome. A positive result is variously defined as either a sustained ...

*May-Thurner syndrome

Budd-Chiari syndrome - Venous compression or obstruction in the liver. Nutcracker syndrome - Compression of the left renal vein ... In medicine, May-Thurner syndrome (MTS), also known as the iliac vein compression syndrome, is a rare condition in which ... Venography will demonstrate the classical syndrome when causing deep venous thrombosis. May-Thurner syndrome in the broader ... This syndrome frequently manifests as pain when the limb is dependent (hanging down the edge of a bed/chair) and/or significant ...

*List of pathologists

Hans Chiari (1851-1916), Austrian pathologist (see Arnold-Chiari malformation, Budd-Chiari syndrome). Jacob Churg (1910-2005), ... I. N. Dubin (born 1913), American pathologist (see Dubin-Johnson syndrome). Cuthbert Dukes (1890-1977), English physician and ... John Bruce Beckwith (born 1933), American pathologist (see Beckwith-Wiedemann syndrome). Franz Best (1878-1920), German ... Lotte Strauss (1913-1985), American pathologist (see Churg-Strauss syndrome). Sunao Tawara (1873-1952), Japanese pathologist, ...

*Hepatic veins

Budd-Chiari syndrome is a condition caused by blockage of the hepatic veins. It presents with a "classical triad" of abdominal ... The formation of a blood clot within the hepatic veins can lead to Budd-Chiari syndrome. It occurs in 1 out of a million ... The syndrome can be fulminant, acute, chronic, or asymptomatic. The hepatic veins may be connected with the portal veins in a ...

*Hepatic veno-occlusive disease

Budd-Chiari syndrome (large liver vein obstruction due to thrombosis) Helmy A (January 2006). "Review article: updates in the ... The name sinusoidal obstruction syndrome is now preferred if VOD happens as a result of chemotherapy or bone marrow ... DeLeve LD, Shulman HM, McDonald GB (February 2002). "Toxic injury to hepatic sinusoids: sinusoidal obstruction syndrome (veno- ... sinusoidal obstruction syndrome) following haematopoietic stem cell transplantation". British Journal of Haematology. 163 (4): ...

*Liver

Budd-Chiari syndrome is a condition caused by blockage of the hepatic veins (including thrombosis) that drain the liver. It ... "Budd-Chiari syndrome in Sweden: epidemiology, clinical characteristics and survival - an 18-year experience". Liver ... There are also many pediatric liver diseases, including biliary atresia, alpha-1 antitrypsin deficiency, alagille syndrome, ...

*Liver disease

Budd-Chiari syndrome is the clinical picture caused by occlusion of the hepatic vein. Liver disease can occur through several ... "Hepatic vein obstruction (Budd-Chiari): MedlinePlus Medical Encyclopedia". www.nlm.nih.gov. Retrieved 2015-06-20. "Chronic ... Gilbert's syndrome, a genetic disorder of bilirubin metabolism found in a small percent of the population, can cause mild ... "Gilbert syndrome". Genetics Home Reference. Retrieved 2015-06-20. "Cirrhosis: MedlinePlus Medical Encyclopedia". www.nlm.nih. ...

*Wallace Souza

Souza, who suffered from Budd-Chiari syndrome, died on 27 July 2010 of a heart attack. He died in a hospital in Sao Paulo, ...

*George Budd

... and described what is now known as Budd-Chiari syndrome, already noticed in 1842 by Carl von Rokitansky. It was followed by ... 1886). "Budd, George (1808-1882)". Dictionary of National Biography. 7. London: Smith, Elder & Co. "Budd, George (BT827G)". A ... which Budd contributed to Alexander Tweedie's Library of Practical Medicine, vol. iv.; vol. v. contained his "Scurvy". Budd ... George Budd M.D. (23 February 1808 - 14 March 1882) was an English physician, medical writer and academic. He was born at North ...

*Tenderness (medicine)

Budd-Chiari syndrome Budd-Chiari syndrome is a rare liver condition, symptoms include pain, swelling, and vomiting blood. ... Toxic shock syndrome Toxic shock syndrome is a serious bacterial infection and causes fever, low blood pressure, a rash, and ... Irritable bowel syndrome Irritable bowel syndrome is a common condition that causes painful spasms and cramping in the large ...

*Cirrhosis

Ultrasound may also screen for hepatocellular carcinoma, portal hypertension, and Budd-Chiari syndrome (by assessing flow in ... The hepatorenal syndrome is defined as a urine sodium less than 10 mmol/L and a serum creatinine > 1.5 mg/dl (or 24 hour ... Acute kidney injury (particularly hepatorenal syndrome) Liver cirrhosis has many possible causes; sometimes more than one cause ...

*Thrombosis

Budd-Chiari syndrome is the blockage of a hepatic vein or of the hepatic part of the inferior vena cava. This form of ... paraneoplastic syndrome), by external compression on a blood vessel when a solid tumor is present, or (more rarely) extension ...

*Chiari malformation

... or Arnold-Chiari malformation should not be confused with Budd-Chiari syndrome, a hepatic condition also ... tethered spinal cord syndrome, and connective tissue disorders such as Ehlers-Danlos syndrome and Marfan syndrome. Chiari ... "Code 453.0: Budd-Chiari Syndrome". 2008 ICD-9-CM Diagnosis. "Spontaneous Spinal Cerebrospinal Fluid Leaks: Diagnosis". Alessia ... Some cases of Chiari are associated with platybasia (flattening of the skull base). The history of Chiari malformation is ...

*Serum-ascites albumin gradient

... such as the Budd-Chiari syndrome, heart failure, or liver cirrhosis) that increase the hydrostatic pressure in the circulatory ... Budd-Chiari syndrome, portal vein thrombosis, and idiopathic portal fibrosis. A low gradient (< 1.1 g/dL, ...

*Deep vein thrombosis

... and Budd-Chiari syndrome-are separate diseases excluded from the scope of this definition. Third-generation combined oral ... Post-thrombotic syndrome is a significant contributor to DVT follow-up costs. Annual DVT costs in the U.S. are an estimated $5 ... This may reduce the risk of post-thrombotic syndrome by a third, and possibly reduce the risk of leg ulcers, but is associated ... Distal DVT itself is hardly if ever associated with post-thrombotic syndrome or PE. Untreated lower extremity DVT has a 3% PE- ...

*Vein

Budd Chiari syndrome) or compression from tumours or tuberculosis lesions. When the pressure increases in the portal veins, a ... May-Thurner syndrome Nutcracker syndrome Thoracic outlet syndrome Albert, consultants Daniel (2012). Dorland's illustrated ... Postphlebitic syndrome is venous insufficiency that develops following deep vein thrombosis. Deep vein thrombosis is a ... ISBN 0-13-981176-1. www.radiopaedia.org/ Kahn SR (August 2006). "The post-thrombotic syndrome: progress and pitfalls". British ...

*Zeynel Mungan

Anticoagulant therapy and Budd-Chiari syndrome : is it successful ? Hepatogastroenterology 58:900-3 (2011) 54. Ermis F, Akyuz F ... Irritable bowel syndrome (IBS), acid-peptic diseases and gastrointestinal motility. Dr. Mungan is also in the editorial board ... Hepatopulmonary syndrome in noncirrhotic portal hypertensive patients. Dig Dis Sci, 48:556-60 (2003) 17. Mungan Z, Akyuz F, ... treatment in obstructive sleep apnea syndrome: An esophageal impedance-pHmetry study. Hepatogastroenterology 58:110-1 (2011) 55 ...

*Lobes of liver

Budd-Chiari syndrome, caused by occlusion of hepatic venous outflow, can lead to hypertrophy of the caudate lobe due to its own ...

*King's College Criteria

Budd-Chiari syndrome, other medications (including halothane, hormonal contraception, and isoniazid), recreational drugs ( ...

*Inferior vena cava syndrome

... dialysis and other invasive procedures in the vicinity Budd-Chiari syndrome Epidemiological data is elusive owing to the wide ... Inferior vena cava syndrome (IVCS) is a result of obstruction of the inferior vena cava. It can be caused by invasion or ... Supine hypotensive syndrome Obstruction by deep vein thrombosis or tumors (most commonly renal cell carcinoma) Compression ... Symptoms of late pregnancy inferior vena cava syndrome consist of intense pain in the right hand side, muscle twitching, drop ...

*Ascites

Budd-Chiari syndrome or veno-occlusive disease Constrictive pericarditis Kwashiorkor (childhood protein-energy malnutrition) ... as well as detecting Budd-Chiari syndrome (thrombosis of the hepatic vein) and portal vein thrombosis. Additionally, the ... Serositis Nephrotic syndrome Hereditary angioedema Other rare causes: Meigs syndrome Vasculitis Hypothyroidism Renal dialysis ...

*ICD-10 Chapter IX: Diseases of the circulatory system

Budd-Chiari syndrome (I82.1) Thrombophlebitis migrans (I82.2) Embolism and thrombosis of vena cava (I82.3) Embolism and ... Postphlebitic syndrome (I87.1) Compression of vein Superior vena cava syndrome (I87.2) Venous insufficiency (chronic)( ... Postcardiotomy syndrome (I98) Other disorders of circulatory system in diseases classified elsewhere (I99) Other and ... Coeliac artery compression syndrome (I77.5) Necrosis of artery (I77.6) Arteritis, unspecified (I77.8) Other specified disorders ...

*Hot quadrate sign

... of the liver shows preferential enhancement or radiotracer accumulation with hepatic vein occlusion in Budd Chiari syndrome. In ... The appearance is an indirect reflection of the collateralized flow of SVC syndrome, in which occlusion of the superior vena ...

*List of syndromes

... syndrome Bruck syndrome Brugada syndrome Brunner syndrome Budd-Chiari syndrome Burning feet syndrome Burning mouth syndrome ... syndrome Wende-Bauckus syndrome Werner syndrome Wernicke-Korsakoff syndrome West syndrome Westerhof syndrome Wet lung syndrome ... syndrome Chiari-Frommel syndrome Chiasmal syndrome Chilaiditi syndrome Child sexual abuse accommodation syndrome CHILD syndrome ... syndrome Hero syndrome Heyde's syndrome High-rise syndrome HIV/AIDS Holiday heart syndrome Holt-Oram syndrome Hopkins syndrome ...
When Budd-Chiari syndrome is suspected, measurements are made of liver enzyme levels and other organ markers (creatinine, urea, electrolytes, LDH). Budd-Chiari syndrome is diagnosed using ultrasound studies of the abdomen, although occasionally more invasive methods have to be used (retrograde angiography). Liver biopsy is sometimes necessary to differentiate between Budd-Chiari syndrome and other causes of hepatomegaly and ascites, such as galactosemia or Reyes syndrome. ...
OBJECTIVE The purpose of this study was to determine the CT and MR imaging appearance of large regenerative nodules arising in livers with vascular disorders and to correlate these findings with the clinical and pathologic findings. CONCLUSION Large regenerative nodules are a characteristic feature of Budd-Chiari syndrome and other hepatic vascular disorders. CT and MR imaging show consistent features of the nodules and the surrounding liver that may allow distinction of Budd-Chiari nodules from other types of hypervascular hyperplastic or dysplastic nodules.
The Budd-Chiari syndrome, or Chiaris syndrome, is the disease complex which follows hepatic vein occlusion. It is a moderately well popularized secondary abdominal response to several disease processes, but the number of reported cases remains remarkably small. During the past 32 months seven autopsy-proved cases and four presumptive cases have been observed. This appears to be a large experience with the syndrome, perhaps explained by the fact that a large tumor center was the source of material. From 1910 to 1939 at the Mayo Clinic 20 instances were encountered.1 Only five were found during 11,979 autopsies at Stanford University.2. Lambron ...
We studied the role of the recently identified CALR mutations in 141 patients with Budd-Chiari Syndrome (BCS) or portal vein thrombosis (PVT) in a large multinational cohort. A CALR mutation was present in one of the 141 patients (0.7%). This patient was previously diagnosed with primary myelofibrosis. This results in CALR positivity in one out of 44 (2.3%) patients with myeloproliferative neoplasm (MPN), and in one of 11 (9.1%) JAK2V617F negative patients diagnosed with MPN. We suggest that analysis of CALR mutations should be performed in JAK2V617F negative BCS and PVT patients.. BCS and non-malignant, non-cirrhotic PVT are rare vascular liver diseases. The etiology of these diseases encompasses both inherited and acquired risk factors, of which MPN are the most common with a prevalence ranging between 20%-50%.1-3 Detecting presence of MPN in patients with BCS and PVT is important, given the prognostic and potential therapeutic implications regarding anticoagulant therapy.4,5 However, ...
TY - JOUR. T1 - Hepatocellular Carcinoma Containing Sarcomatous Lesions in a Normal Liver, Accompanied by Secondary Budd-Chiari Syndrome [1]. AU - Kishino, Tomonori. AU - Mori, Hideaki. AU - Nishikawa, Kaori. AU - Ishiyama, Narihiro. AU - Yasui, Hideaki. AU - Sugiyama, Masanori. AU - Atomi, Yutaka. AU - Sakamoto, Michiie. AU - Saito, Shozo. AU - Ishida, Hitoshi. AU - Takahashi, ShinIchi. AU - Watanabe, Takashi. PY - 2004/3. Y1 - 2004/3. UR - http://www.scopus.com/inward/record.url?scp=10744233167&partnerID=8YFLogxK. UR - http://www.scopus.com/inward/citedby.url?scp=10744233167&partnerID=8YFLogxK. U2 - 10.1097/00004836-200403000-00019. DO - 10.1097/00004836-200403000-00019. M3 - Article. C2 - 15128080. AN - SCOPUS:10744233167. VL - 38. SP - 296. EP - 297. JO - Journal of Clinical Gastroenterology. JF - Journal of Clinical Gastroenterology. SN - 0192-0790. IS - 3. ER - ...
The flowchart of Budd-Chiari Syndrome (BCS) management is not evidence-based and relies to experts opinion. The aim of this chapter is to enlighten the controversies about BCS management. Guidelines...
A case of Budd-Chiari syndrome in a young woman, which started probably in the last trimester of pregnancy, is described. The diagnosis was made clinically and was confirmed by inferior venacavography and on exploratory laparotomy. The possible connection of the syndrome with the pregnancy is discussed.. ...
A 6.5-year-old, female spayed German short-haired pointer dog was presented with a two-week history of ascites. The dog was depressed with a severely distended abdomen. Peritoneal fluid analysis revealed a modified transudate. A metallic linear foreign body was identified cranial to the pyloric antrum by advanced imaging. A fibrous tract of tissue extending from the pyloric antrum to the hilar region of the right medial liver lobe was dissected surgically. The foreign body was removed by dissection of the fibrous tract, which relieved visible compression of the caudal vena cava and all hepatic veins. By three days postoperatively, ascites had not resolved and a caudal cavagram confirmed narrowing of the thoracic caudal vena cava at the diaphragm. Eight days postoperatively, a caudal vena caval stent was placed, relieving the pressure gradient across the narrowing and resulting in complete resolution of clinical signs. ...
Hepatic vein thrombosis (HVT) is an obstruction in the veins of the liver caused by a blood clot. This condition blocks blood flow from the liver to the heart.
1. Li T, Zhang W, Bai W, Zhai X, Pang Z. Warfarin Anticoagulation Prior to Angioplasty Relieves Thrombus Burden in Budd-Chiari Syndrome Caused by Inferior Vena Cava Anatomic Obstruction. J Vasc Surg 2010 (in press).. 2. Zhang W, Killeen JD, Chiriano J, Bianchi C, Teruya TH, Abou-Zamzam AM. Management of Symptomatic Spontaneous and Isolated Dissection of Visceral Artery: Is emergent intervention mandatory? Ann Vasc Surg 2009, 23(1):90-4.. 3. Li TX, Zhai ST, Pang ZG, Ma XX, Cao HC, Bai WX, Wang ZL, Zhang W. Feasibility and Mid-term Outcomes of Percutaneous Transhepatic Balloon Angioplasty for Symptomatic Budd-Chiari Syndrome Secondary to Hepatic Venous Obstruction. J Vasc Surg 2009, 50:1079-84.. 4. Zhang W, Abou-Zamzam AM, Hashisho M, Killeen JD, Bianchi C, Teruya TH. Staged Endovascular Stent Grafts for Mobile/Unstable Thrombi of Thoracic and Abdominal Aorta Causing Recurrent Spontaneous Distal Embolization. J Vasc Surg 2008; 47(1):193-6.. 5. Zhang W, Hasaniya WN, Premaratne S, McNamara JJ. ...
1. Li T, Zhang W, Bai W, Zhai X, Pang Z. Warfarin Anticoagulation Prior to Angioplasty Relieves Thrombus Burden in Budd-Chiari Syndrome Caused by Inferior Vena Cava Anatomic Obstruction. J Vasc Surg 2010 (in press).. 2. Zhang W, Killeen JD, Chiriano J, Bianchi C, Teruya TH, Abou-Zamzam AM. Management of Symptomatic Spontaneous and Isolated Dissection of Visceral Artery: Is emergent intervention mandatory? Ann Vasc Surg 2009, 23(1):90-4.. 3. Li TX, Zhai ST, Pang ZG, Ma XX, Cao HC, Bai WX, Wang ZL, Zhang W. Feasibility and Mid-term Outcomes of Percutaneous Transhepatic Balloon Angioplasty for Symptomatic Budd-Chiari Syndrome Secondary to Hepatic Venous Obstruction. J Vasc Surg 2009, 50:1079-84.. 4. Zhang W, Abou-Zamzam AM, Hashisho M, Killeen JD, Bianchi C, Teruya TH. Staged Endovascular Stent Grafts for Mobile/Unstable Thrombi of Thoracic and Abdominal Aorta Causing Recurrent Spontaneous Distal Embolization. J Vasc Surg 2008; 47(1):193-6.. 5. Zhang W, Hasaniya WN, Premaratne S, McNamara JJ. ...
Budd-Chiari syndrome is a rare problem that results from blood clotting in the veins flowing out of the liver (hepatic veins). The high pressure of blood in these veins leads to an enlarged liver, and to an accumulation of fluid in the abdomen, called ascites. The liver, the largest internal organ in the human body, is responsible for many vital physiologic processes. Blood flow through the liver nourishes the liver, carries in substances that the liver will process, and carries away substances that the liver has produced. When blood cannot flow out freely from the liver, blood pressure rises in the veins of the liver, leading to blood clots within the liver. Also, some of the blood plasma can leak through the walls of the veins and accumulate within the abdomen (ascites). ICD-10 I82.0 ICD-9 453.0 OMIM 600880 DiseasesDB 1735 eMedicine med/2694 ped/296 radio/121 MeSH D006502 ...
Budd-Chiari syndrome is a rare problem that results from blood clotting in the veins flowing out of the liver (hepatic veins). The high pressure of blood in these veins leads to an enlarged liver, and to an accumulation of fluid in the abdomen, called ascites. The liver, the largest internal organ in the human body, is responsible for many vital physiologic processes. Blood flow through the liver nourishes the liver, carries in substances that the liver will process, and carries away substances that the liver has produced. When blood cannot flow out freely from the liver, blood pressure rises in the veins of the liver, leading to blood clots within the liver. Also, some of the blood plasma can leak through the walls of the veins and accumulate within the abdomen (ascites). ICD-10 I82.0 ICD-9 453.0 OMIM 600880 DiseasesDB 1735 eMedicine med/2694 ped/296 radio/121 MeSH D006502 ...
RESULTS: The etiology of BCS was identified in 38 cases. Ph- MPN was found as the most common risk factor (50%, N.=22), especially polycythemia vera. JAK2V617F mutation was detected in the most of 22 MPN cases (82.5%). The second most common etiologic factor was inherited thrombophilia (18%, N.=8). In the non-covered (bare) stent group, a primary patency rates 52.9% in 1 year and 20% in 5 years after TIPS (Portasystemic Shunt, Transjugular Intrahepatic) creation. In the covered stent group the 1-year and 5-year primary patency rates were was 80% and 33.3% respectively. The average 5-year re-intervention rate per patient was 1.65 procedures in the bare stent group and 0.67 in the covered stent group. Re-interventions were more frequent in MPN patients. All patients were anticoagulated with heparin at the beginning, switched to vitamin K antagonist. On top of TIPS, anticoagulant and a vigorous therapy of underlying disorder are necessary ...
Linköping University, Department of Clinical and Experimental Medicine, Gastroenterology and Hepatology. Linköping University, Faculty of Health Sciences. Östergötlands Läns Landsting, Centre for Medicine, Department of Endocrinology and Gastroenterology UHL. ...
Noida, 11 March 2015: In a rare case of clinical excellence, Fortis Hospital, Noida, saved the life of a 47 year old patient, George Ikuje Obe, from Nigeria, suffering from the Budd-Chiari Syndrome (BCS) since the last 12 years. The surgery was led by Dr. Vivek Vij, Director, Liver Transplant at Fortis Hospital Noida along with a team of eight surgeons and 14 doctors including anesthetist and cardiac thoracic surgeon. The 14 hour long surgery comprised of joining the liver with the heart through a passage created from the vein of the liver along with conducting the liver transplant. This is the first such surgery in India and only three to four such surgeries have been conducted in the world. The patient is doing well and will remain on anti-coagulation drug for life to prevent any blockages in the future.. Budd-Chiari syndrome is a condition caused by blockage of the hepatic veins that drains the liver. It presents with the classical set of symptoms such as abdominal pain, ascites and liver ...
Free, official information about 2012 (and also 2013-2015) ICD-9-CM diagnosis code 453.0, including coding notes, detailed descriptions, index cross-references and ICD-10-CM conversion.
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Results: Ten patients were men (40.0%). Median age of recipients at transplantation was 29.0 (17-51) years. Eighteen patients (72%) had evidence of myeloproliferation, 1 had paroxysmal nocturnal hemoglobinuria, and 6 had idiopathic disease. In 55.5% of cases eventually diagnosed with myeloproliferative neoplasms, Budd-Chiari syndrome was their initial presentation. All patients were maintained on long-term post-transplant anticoagulation protocol. The median follow-up time was 58.8 months. Four patients (16%) died during follow-up. Acute graft rejection occurred in 16% of cases. During the observation period, 5 patients had recurrent thrombotic events. The 5-year patient and graft survival rate was 84%. No case of transformation to acute leukemia was seen ...
PURPOSE: To compare different imaging characteristics between hepatic benign regenerative nodules and hepatocellular carcinomas (HCCs) associated with Budd-Chiari syndrome (BCS) by contrast enhanced ultrasound (CEUS). MATERIALS AND METHODS: A total o
Budd-Chiari syndrome, a posthepatic cause, is characterized by the following. Hypertension affects approximately 75 million adults in the United States and is a major risk factor for stroke, myocardial infarction, vascular disease, and chronic. Neel Jr. Selexipag for the Treatment of Pulmonary Arterial Hypertension. , Richard Channick, M. One of these meds may be the problem. Provides up-to-date, selected information on renal disorders and their treatment, hemodialysis, peritoneal dialysis, and about hypertension, dialysis, and clinical. January 2 2017. Monthly publication by the American Heart Association focusing what is the cause of hypertension on blood pressure regulation and pathophysiological mechanisms underlying what is the cause of hypertension hypertensive diseases. D. The link between salt and high blood pressure is especially compelling High blood pressure - Comprehensive overview covers symptoms, treatment and prevention of hypertension Hypertension, or high blood pressure, happens ...
Once, she taught aerobics classes. Now, after months of losing muscle mass to Budd-Chiari Syndrome, her first workout in years is a lesson in self-awareness and strength.
Diagnosed case of : Budd-Chiari Syndrome (Liver Cirrhosis in Childs) (लहान मुलांमधील लिवर सिरोसीस). Reports before Modern Homeopathy treatment. Report I : Before treatment on dated April ...
The journey was very tough, where parents were constantly living under the fear of destiny of their child, questions arising time and again on the childs survival. Even a doctor telling them that nothing could be done and leave it all to the God. Jasmines mother recalls various instances where she saw her child in pain because of disease as well as procedures, but kept her will power strong, full family supporting each other in decision making, taking crucial decisions on treatment after consulting experts. Jasmines mother was always there whenever she was allowed to be with her child, holding her hand during the procedures.. Jasmine was born on September 2003, younger of the two siblings, in a family residing at central Mumbai. Her mother said that the problem became obvious at one and half years of age, when Jasmine could not stand properly, hers legs and head shook and she could only speak few words. Pediatricians were consulted and it was taken as a case of delayed growth, which would ...
Despite having made only one cytoreductive surgery and after of drainage of the ascitic fluid accumulated in the abdominal cavity the animal improved in the first 48 hours after surgery. Within this 48 hours the animal was more active, had eaten some food and tolerated it and had minimal edema in the limbs. Postoperative chemotherapy with doxorubicin (Doxocris 50, LKM, Buenos Aires, Argentina), 30 mg/m2 IV was initiated immediately after surgery. The dog deteriorated 2 weeks after treatment and died. A complete necropsy (excluding the central nervous system) was performed. The right accessory lung lobe was replaced by a large tumor (11 x 6 x 4 cm) previously diagnosed as a papillary pulmonary adenocarcinoma (Fig. 2 B). Due to the large size of the tumor, the CVC was almost completely compressed. The spleen had multiple red-brown nodules (Fig. 1 C) ranging from 0.5 to 1.3 cm in diameter; these splenic masses were histopathologically diagnosed as chronic splenitis (Fig. 2 C). The liver had ...
A 63-year-old woman was admitted to our cancer center in 2015, complaining of right upper abdominal pain. Otherwise she was healthy with good general condition. From radiologic evaluations in other hospital, she was diagnosed with primary HCC associated with hepatitis B virus and liver cirrhosis. Additional computed tomography (CT) and magnetic resonance (MR) imaging for staging workup showed that over 16 cm mass at the right hepatic lobe with tumor thrombus in the right portal and main portal vein (Fig. 1). Right hepatic vein and suprahepatic inferior vena cava were also involved. Multiple portocaval and para-aortic lymph nodes were enlarged. At the time of initial visit, her alpha fetoprotein (AFP) level was ,4,340 ng/mL (normal range [NR], 0.1 to 9.0 ng/mL), and the results of liver function tests are aspartate transaminase (AST) 298 IU/L (NR, 0 to 35 IU/L), alanine transaminase (ALT) 31 IU/L (NR, 0 to 35 IU/L), alkaline phosphatase 299 IU/L (NR, 30 to 120 IU/L), and total bilirubin 1.1 mg/dL ...
Welcome to Hope Whispers. Im Kim. In 2008 I was diagnosed with Budd Chiari Syndrome and life has never been the same. I started this blog to share my life and to share hope. Life isnt always easy. Life with multiple chronic illnesses, 2 wild boys, dogs, and a husband who still chooses to love me, well, sometimes, it can get a little messy. But that doesnt mean Im not going to make the most out of it. It might not always be perfect, but it will always real ...
Welcome to Hope Whispers. Im Kim. In 2008 I was diagnosed with Budd Chiari Syndrome and life has never been the same. I started this blog to share my life and to share hope. Life isnt always easy. Life with multiple chronic illnesses, 2 wild boys, dogs, and a husband who still chooses to love me, well, sometimes, it can get a little messy. But that doesnt mean Im not going to make the most out of it. It might not always be perfect, but it will always real ...
Caliste XA, Clark AL, Doyle AJ, Cullen JP, Gillespie DL. "The incidence of contralateral iliac venous thrombosis after stenting across the iliocaval confluence in patients with acute or chronic venous outflow obstruction". J Vasc Surg: Venous and Lymphatic Disorders. 2014; .. 9/ ...
INTRODUCTION: Suprahepatic caval resection and replacement of inferior vena cava (IVC) is standard procedure in deceased donor liver transplantation for patients with Budd-Chiari syndrome (BCS). However, replacement of IVC in living donor liver transplantation (LDLT) is difficult. We report a case of BCS successfully treated by LDLT without replacement of IVC. PRESENTATION OF CASE: A 52-years-old female with a primary BCS due to IVC thrombosis. A vena cava (VC) stent placed after angioplasty without improvement of the hepatic, portal venous flow and liver functions, Transjugular intrahepatic portosystemic shunt was considered and the patient had a rapid deterioration and increased ascites ...
Hepatic venous outflow block caused by short-length hepatic vein stenoses. - D Valla, A Hadengue, M el Younsi, N Azar, G Zeitoun, M J Boudet, G Molas, J Belghiti, S Erlinger, J M Hay, J P Benhamou
In the present series, 8.4% of patients were found to have splanchnic vein thrombosis at evaluation. This proportion probably underestimates the true incidence of splanchnic vein thrombosis during end stage cirrhosis. Indeed, a significant proportion of patients with extensive thrombosis may not have been referred to our centre because they were not considered as suitable candidates for transplantation and therefore were not taken into account for analysis. None the less, eight of 230 (3.2%) patients who did not have thrombosis at evaluation developed thrombosis while on the waiting list. Importantly, the majority of these patients (6/8) only had partial portal vein thrombosis. Although pretransplantation Doppler-US screening was performed at three month intervals, nine additional patients were found to have thrombosis at the time of surgery. Again, eight of these nine patients had only partial thrombosis and transplantation was technically feasible in all cases.. Multivariate analysis showed ...
TY - JOUR. T1 - Long-Term Outcome of Splanchnic Vein Thrombosis in Cirrhosis. AU - for the IRSVT study investigators. AU - Senzolo, Marco. AU - Riva, Nicoletta. AU - Dentali, Francesco. AU - Rodriguez-Castro, Kryssia. AU - Sartori, Maria Teresa. AU - Bang, Soo Mee. AU - Martinelli, Ida. AU - Schulman, Sam. AU - Alatri, Adriano. AU - Beyer-Westendorf, Jan. AU - Di Minno, Matteo Nicola Dario. AU - Ageno, Walter. PY - 2018/8/1. Y1 - 2018/8/1. N2 - Introduction: Little is known about the long-term outcome of cirrhotic patients with splanchnic vein thrombosis (SVT). This prospective cohort study aimed to describe the clinical presentation, bleeding incidence, thrombotic events, and mortality in patients with SVT associated with cirrhosis. Methods: Among 604 consecutive patients with SVT enrolled over 2 years, 149 had cirrhosis. Major bleeding, thrombotic events, and all-cause mortality were recorded during a 2-year follow-up. In a subgroup, the degree of recanalization with or without anticoagulation ...
The latest issue of the Alimentary Pharmacology & Therapeutics reports good clinical outcomes following transjugular intrahepatic portosystemic stent-shunts in Budd Chiari syndrome.. ...
Build: Wed Jun 21 18:33:50 EDT 2017 (commit: 4a3b2dc). National Center for Advancing Translational Sciences (NCATS), 6701 Democracy Boulevard, Bethesda MD 20892-4874 • 301-435-0888. ...
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You could make the case that -- echoing the infamous 1987 case of Pennsylvania Treasurer R. Budd Dwyer -- the NRA called a press conference Friday... - Will Bunch, Philadelphia Daily News
Looking for online definition of hepatic vein thrombosis syndrome in the Medical Dictionary? hepatic vein thrombosis syndrome explanation free. What is hepatic vein thrombosis syndrome? Meaning of hepatic vein thrombosis syndrome medical term. What does hepatic vein thrombosis syndrome mean?
A 46-year-old man presented with swelling of the lower limbs of 1-year duration. The patient was diagnosed Budd-Chiari syndrome, with a web in the inferior vena cava (IVC) in 1996 (A), treated with percutaneous transluminal angioplasty with Inoue balloon (B). Examination revealed edema and varicosities of both legs, with ascites (D). Abdominal computed tomography (C) and IVC angiography (E, Online Video 1) showed a calcified web with a pseudoaneurysm. Through the right femoral vein, a 6-F multipurpose catheter was passed into the IVC, the lesion was crossed with a Terumo guidewire (Terumo, Leuven, Belgium), and the web was dilated with a 24-cm3 Inoue balloon (Online Video 2). Post-percutaneous transluminal angioplasty shoot showed a residual lesion with a pseudoaneurysm. A PS-5014 stent mounted on 20/40-mm Atlas balloon (Bard Peripheral Vascular, Inc., Tempe, Arizona) was positioned across the web. When the proximal end of the stent was released, the stent migrated into the right atrium (E, ...
Vascular diseases of the liver are a heterogeneous group of rare and if untreated fatal disorders that include portal vein thrombosis, Budd-Chiari syndrome, non-cirrhotic portal hypertension, sinusoidal obstruction syndrome, hereditary hemorrhagic teleangiectasia and others.. Current knowledge about patients suffering from these disorders is insufficient and no biological samples are available to study the mechanisms of these diseases and the effects of treatments.. Therefore, with the support of a grant from EASL, we are running this cohort study by including and following up patients on the platform redcap.ctu.unibe.ch. If you are member of VALDIG you can request a password and username (contact [email protected]) to participate to this study by including patients from your center into the database (a complete set of data) or into the registry (a limited set of data).. ...
In our prospective study cohort, membranous obstruction was demonstrated in 92 (68.6%) of 134 cases of hydrocephalus with the use of 3D-CISS at 3T. Intraventricular membranous obstruction is the most common pathologic finding to cause noncommunicating hydrocephalus (85/114 total noncommunicating cases). However, except in the cerebral aqueduct region, conventional images are insensitive in detection of obstructive membranes in the CSF pathway. In this study, they were only demonstrated in 57 (36.3%) of 157 obstruction sites with the use of conventional imaging. In choosing the most appropriate treatment technique and to assess the prognosis in hydrocephalus, the classification of hydrocephalus and demonstration of obstruction, if it exists, are of significant importance.20,33 The terminology and the classification of hydrocephalus are still a matter of debate and are not the aims of our study. However, it is obvious that we need accurate neuroimaging techniques to demonstrate CSF pathways ...
Proceedings of the distinction between proximal and axial muscles extraocular muscles and parasympathetic divisions. Of course, other regions with one or more drinks on the endothelium are destroyed. Yi, h williams, g. V stahl, h-d. The rate of adult primates. 931 7. 2. Dendritic cellsthe existence and function have evolved, with modalities such as medications. If she has known pud, has been defined as the brain stem sensory information into the chest. Stage-specific surface antigens which have been asked to choose is unclear, early-stage ipsid has been deeply appreciated, perinatal loss155endings tend to be compromised in at least one lineage are suddenly at risk. The standard endoscopic treatment (band ligation) to radiological interventions (placement of a healthy person (figure 3-10b ) shows squamous and colonic peaks) have been observed now in numerous conditions including endometritis, ovaritis, sterility, dysmenorrhea, and afterbirth pain, among others. Megakaryocytes derive from neural ...
About 60% of patients with portal hypertension without clinical signs of porto-systemic encephalopathy (PSE) and with normal EEG show substantial cerebral functional impairments1,2,3,4,5
Lesen Sie Runners World Running on Air The Revolutionary Way to Run Better by Breathing Smarter von Budd Coates mit Rakuten Kobo. Renowned running coach Budd Coates presents a revolutionary yet simple training method based on rhythmic breathing to he...
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Your donation will count towards the teams fundraising total. In addition, please give credit to the person that asked for your support to recognize them for their efforts in creating a world without type 1 diabetes (T1D). ...
The BCS® XP System is the result of a partnership with our customers. Designed with your needs in mind, and knowing that space is often an issue, our team of experts designed the BCS XP to have the smallest footprint in its class. In addition, the BCS XP menu incorporates the most requested assays.. ...
Systemic arterial vasodilatation has been implicated in the pathogenesis of sodium retention in cirrhosis. Hydrophobic bile acids, which have vasodilatory actions, may be involved. Ursodeoxycholic acid, a hydrophilic bile acid, could potentially decrease systemic arterial vasodilatation, possibly due to its antioxidant effects, and improve sodium handling in cirrhosis. The effects of ursodeoxycholic acid on systemic, renal and forearm haemodynamics, liver function and renal sodium handling were assessed in vasodilated cirrhotic patients with refractory ascites treated with a transjugular intrahepatic porto-systemic shunt (TIPS). Eight cirrhotic patients with refractory ascites without TIPS placement served as controls for the sodium handling effects of ursodeoxycholic acid. From 1 month post TIPS, seven patients were studied before, after 1 month of treatment with ursodeoxycholic acid (15 mg·day-1·kg-1) and at 1 month follow-up. Lipid peroxidation products were used as indices of its ...
The treatment of BCS is best done by a team involving a pediatric gastroenterologist, interventional radiologist, pediatrician and a liver surgeon. The treatment can be divided into supportive and definitive management:. Supportive care: The nutrition of the patient is improved. Large ascites can cause difficulty in breathing. This condition requires removal of fluid from the abdomen by inserting a needle (paracentesis) only if there is difficulty in breathing or for the sake of testing the fluid. In order to decrease the hypercoagulable state, patients are usually started on oral anticoagulants. The common drug used is Warfarin.. Definitive management:. Radiological intervention: During hepatic venogram (study of venous blood flow of liver), the anatomy and pressure in the hepatic veins and their caliber is noted. Depending upon the diameter of the hepatic veins, either angioplasty (balloon dilatation of the vein), hepatic vein stenting (a stent is passed into the hepatic vein) or TIPSS is done ...
PCLD1 is a disorder characterized by the presence of multiple fluid filled cysts throughout the liver. The cysts are of biliary epithelial origin and result in abdominal distention, back pain, dyspnea and early satiety. In rare cases, infection, rupture or haemorrhage of cysts may occur or hepatic venous outflow may be obstructed. Other anomalies may include lower triglycerides and total cholesterol, and higher levels of total bilirubin and serum alkaline phosphatase. The disease does not extend to the kidneys and patients do not have renal cysts. The disorder has an overall incidence of 1 in 100,000 individuals. It disproportionately affects females compared to males. Also, affected women are seen to have a larger number of cysts than affected men. The disorder has an onset after 40 years of age and increases in severity over time. However, some affected individuals may remain asymptomatic and do not require any treatment.. Diagnosis is made based on ultrasound and MRI imaging studies. The ...
First introduced about two decades ago as a bailout technique for suboptimal or failed iliac angioplasty, peripheral vascular stenting gradually emerged as a valuable and versatile tool for a variety of primary and adjuvant applications within non-coronary vasculature. First introduced about two decades ago as a bailout technique for suboptimal or failed iliac angioplasty, peripheral vascular stenting gradually emerged as a valuable and versatile tool for a variety of primary and adjuvant applications within non-coronary vasculature. Today, peripheral vascular stenting techniques are commonly employed in the management of the most prevalent occlusive circulatory disorders and other pathologies affecting abdominal and thoracic aortic tree and lower extremity arterial bed. Stents are also increasingly used in the management of the debilitating conditions like venous outflow obstruction associated with deep venous thrombosis and chronic venous insufficiency. Peripheral vascular systems include ...
RESULTS: Cranial venous outflow obstruction and ONS hydrops were the most valid signs indicating IH with a sensitivity of 94% and 92% and a specificity of 100% and 89%, respectively. Sensitivities and specificities were 56% and 97% for reduced pituitary height, 64% and 78% for flattening of the posterior sclera, 31% and 97% for widening of the superior ophthalmic veins, 33% and 100% for optic disc protrusion, 14% and 100% for optic nerve edema, and 6% and 100% for elongation of the optic nerve. At least 2 MR imaging findings could be demonstrated in each patient but in none of the controls. The number of positive MR imaging findings correlated with CSF pressure (r = 0.62, P = .01). ...
When I got home, Budd was lying on the sofa, reading "The New Yorker." Sitting down, I said I thought hed be interested in what I found out at the library. He lowered the magazine, but avoided any eye contact. A signal that I was still among The Unforgiven. It struck me for the first time that this exquisitely urbane man would seem strangely at home in an old-fashioned Western. He possessed that same implacable sense of moral balance. The good inevitably silences the evil. And it was Budd himself who painted the hard-edged line that starkly divided the world into those two regions: a black area and a white one. And it was Budd himself who decided which ideas and which people rightly belonged inside either the black or the white region. Not so different from the way Id grown up, now that I thought about it. There were rigid boundaries enforced in the fundamentalist sect of Plymouth Brethren, too, but their faith held that God himself had drawn the map, laying His plan out in the Bible so that ...
1. Irregular, spasmodic, involuntary movements of the limbs or facial muscles, often accompanied by hypotonia. The location of the responsible cerebral lesion is not known. ...
بخت خود را برای انتشار در مجله‌های بین‌المللی کارشناسی‌شده افزایش دهید. فهرستی از نویسندگان در اینجا هست که نوشته‌های خود را در مجله‌های بین‌المللی دارای SCI به چاپ رسانیده‌اند. این مقالات توسط IVC ویرایش شده‌اند و دامنه‌ی گسترده‌ای از زمینه‌های موضوعی از علوم فیزیکی گرفته تا پزشکی و علوم زیستی، هنر و اقتصاد را به نمایش می‌گذارند.
The researchers ensured that the groups were individually matched 1:1 according to age, sex, Child-Turcotte-Pugh class, and cause of cirrhosis. A stratified Cox model was used by the researchers to assess risk of hepatocelullar carcinoma development.. The investigators found that he median time of follow-up was similar in transjugular intrahepatic portosystemic shunt and non- transjugular intrahepatic portosystemic shunt cohorts; 30.3 and 31.4 months, respectively. The researchers also showed that the probability of developing hepatocelullar carcinoma at 1, 3, and 5 years was 3%, 24%, and 34% for the transjugular intrahepatic portosystemic shunt cohort and 1%, 6%, and 25%, for the control, respectively, with a hazard ratio of 1.52.. Hepatitis C virus infection and age were independent predictors of hepatocelullar carcinoma development in patients without transjugular intrahepatic portosystemic shunt. Dr Ba ares concluded, Patients with cirrhosis who are treated with transjugular intrahepatic ...
Saxon RR, Mendel-Hartvig J, Corless CL, Rabkin J, Uchida BT, Nishimine K, et al. Bile duct injury as a major cause of stenosis and occlusion in transjugular intrahepatic portosystemic shunts: comparative histopathologic analysis in humans and swine. J Vasc Interv Radiol 1996; 7: 487-497 ...
Objectives The aim of this study was to prospectively evaluate effective dose (E) of operators performing transjugular intrahepatic portosystemic shunts (TIPS) in a single centre. Patients radiation...
Care guide for Transjugular Intrahepatic Portosystemic Shunt (Inpatient Care). Includes: possible causes, signs and symptoms, standard treatment options and means of care and support.
MalaCards based summary : Sagittal Sinus Thrombosis, also known as thrombosis of superior longitudinal sinus, is related to hyperthyroidism and budd-chiari syndrome. An important gene associated with Sagittal Sinus Thrombosis is SERPINC1 (Serpin Family C Member 1), and among its related pathways/superpathways are Response to elevated platelet cytosolic Ca2+ and Collagen chain trimerization. Affiliated tissues include brain, myeloid and b cells, and related phenotype is embryo ...
... Intervention:Transjugular intrahepatic portosystemic shunt ICD-10 code: ICD-9 code: 39.1 Other codes: A
Gratuit Tip Plus BMX Distribution Tip Plus BMX Distribution is BMXs leading distributor of complete bikes, parts, accessories, footwear, and apparel to retail stores across the United States. Tip ... TIPS Training for Intervention ProcedureS TIPS (Training for Intervention ProcedureS) is the global leader in education and training for the responsible service, sale, and consumption of alcohol. Individual TIPS In Depth TIPS In Depth How TIPS Are Tied to Inflation . Treasury Inflation Protected Securities (TIPS) are marketable securities whose principal is adjusted by ... Transjugular intrahepatic portosystemic shunt (TIPS ... Transjugular intrahepatic portosystemic shunt (TIPS) is a procedure to create new connections between two blood vessels in your liver. You may need this procedure if ... P3 Tips The P3 platform enables the public to share information anonymously with Crime Stoppers programs, Law Enforcement entities, schools, and large corporations around the ... finance.yahoo.com ...
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TY - JOUR. T1 - Subclavian steal syndrome secondary to Takayasu Arteritis in a young female Caucasian patient. AU - Tsivgoulis, Georgios. AU - Heliopoulos, Ioannis. AU - Vadikolias, Konstantinos. AU - Birbilis, Theodosios. AU - Piperidou, Charitomeni. PY - 2010/9/15. Y1 - 2010/9/15. N2 - Subclavian steal syndrome (SSS) is most frequently described in Caucasians aged over 50 years because of increased incidence of atherosclerosis in this population. Non-atherosclerotic etiologies of SSS are rare in Caucasians. We present a case of Subclavian Steal Syndrome secondary to Takayasu Arteritis (TA) in a 26 year-old female Caucasian patient. The present case underscores that despite the very low incidence of TA in Caucasians (0.8/1,000,000), this large-vessel vasculitis of unknown etiology should always be considered in the differential diagnosis of subclavian steal syndrome in Caucasian women aged less than 40 years.. AB - Subclavian steal syndrome (SSS) is most frequently described in Caucasians aged ...
Due to propensity for arising in the retroperitoneum, close to or in association with the inferior vena cava, leiomyosarcomas may cause obstruction of the IVC with Budd-Chiari (upper IVC), renal failure (middle IVC) or lower limb oedema (lower IVC). More commonly it present with a mass lesion. Local recurrence and distant metastases are common with retroperitoneal sites; superficial sites are often curable due to smaller size at presentation; and those arising in deep tissues are of intermediate behaviour.. ...
Free Online Library: Adrenal suppression and Cushings syndrome secondary to ritonavir and budesonide.(Scientific Letters, Letter to the editor) by South African Medical Journal; Health, general Budesonide Complications and side effects Dosage and administration Cushing syndrome Development and progression Risk factors HIV infection Drug therapy Prognosis HIV infections Ritonavir
For years, millions of Americans suffering from either fibromyalgia or chronic fatigue syndrome, two illnesses that can leave people in too much pain or too tired to lead productive lives, have been searching for an antidote. Complementary therapies such as massage and acupuncture have helped many, as have steady regimens of nutritional supplements and gentle or "graded" exercise programs. In recent months, however, radical surgical procedures have been in the news, raising hopes among those who suffer from these debilitating conditions. The operations, in which the surgeon removes a portion of the lower rear skull, or widens the spinal column at the neck, are not new. Neurosurgery, as a treatment for either fibromyalgia or CFS, is very new, however. Some Say a Too-Big Brain May Be Cause for Concern Chiari syndrome and spinal stenosis are well known to surgeons. Chiari syndrome, in particular, was recognized a century ago. It is a congenital malformation in which the rear skull, or occipital ...
Looking for hepatic vein? Find out information about hepatic vein. A blood vessel that drains blood from the liver into the inferior vena cava Explanation of hepatic vein
Dr. George T Budd, MD, rated 3.6/5 by patients. 6 reviews, Phone number & practice locations, Medical Oncologist in Cleveland, OH.
budd root Comic Art Member Gallery Results - Page 1. All Comic Art shown is owned or created by our Gallery Owners at ComicArtFans.com.
Budd Lynch, a veteran radio broadcaster who spent more than 60 years working for the Detroit Red Wings and became the teams public voice, died Tuesday. He was 95.
Kelleys Textbook of Rheumatology, 8th Edition | Gary S. Firestein MD, Ralph C. Budd MD, Edward D. Harris Jr. MD, Iain B. McInnes, Shaun Ruddy MD, John S. Sergent MD | download | B-OK. Download books for free. Find books
Dallas, TX (PRWEB) November 05, 2012 -- Once again, the national mesothelioma law firm of Baron and Budd has been selected to the prestigious Legal 500 list of
TIPS dysfunction is defined as a loss of decompression of the portal venous system due to occlusion or stenosis of the TIPS. Although there is no consistency between investigators as to the exact criteria that should be used to define TIPS dysfunction in reference to degree of stenosis, a value of 50% is frequently used. In addition, a rise in the HVPG to greater than 12 mm Hg or a recurrence of the complication of portal hypertension for which the TIPS was performed indicates TIPS dysfunction.33 Occlusion of the TIPS can either be due to thrombosis or hyperplasia of the intima. Thrombosis of the TIPS usually occurs early and can happen within 24 hours of TIPS creation. The frequency of this complication is on the order of 10% to 15%.34, 35 The cause of the thrombosis may be leakage of bile into the shunt, hypercoagulable syndromes, or inadequate coverage of the TIPS tract with sufficient stents.36, 37 Thrombosis of the TIPS is identified using Doppler ultrasound, and patency is re-established ...
Two 18-G peripheral intravenous catheters and a 20-G right radial arterial catheter were placed, and standard ASA monitoring was performed in the angiography suite. Further invasive monitoring was not necessary because of the stability of the patients chest pain with nitroglycerin patch, normal electrocardiography results, no history of congestive heart failure or arrhythmia, and the relatively hemodynamic stability of the TIPS procedure. Sedation was achieved with 50 micro gram *symbol* kg sup -1 *symbol* min sup -1 propofol, 2 mg midazolam in 0.5-mg increments, and 100 micro gram fentanyl in 25-micro gram boluses intravenously. Two hours after the start of the procedure, the patients systolic blood pressure decreased from 110 to 60 mmHg with an increase in heart rate to 110 beats/min. No ST-T changes were noted on electrocardiogram monitoring. This coincided with dilation of the Wallstent device. As the patient lost consciousness, ventilation was supported with 100% Oxygen2via mask followed ...
TY - JOUR. T1 - Exogenous and endogenous nitric oxide but not iNOS inhibition improves function and survival of ischemically injured livers. AU - Rivera-Chavez, F. A.. AU - Toledo-Pereyra, L. H.. AU - Dean, R. E.. AU - Crouch, L.. AU - Ward, P. A.. PY - 2001/11/20. Y1 - 2001/11/20. N2 - The role of nitric oxide (NO) in liver ischemia/reperfusion (I/R) injury remains controversial and few works have shed more information regarding the effect of exogenous (EX) and/or endogenous NO (EN) under conditions of I/R of the liver. We investigated the role of exogenous and endogenous NO and inducible nitric oxide synthase (iNOS) inhibition in liver function, neutrophil infiltration, and animal survival after liver I/R. Sprague-Dawley rats were subjected to total hepatic ischemia for 90 min using an extracorporeal porto-systemic shunt. The animals were divided into five groups, including the sham porto-systemic shunt with no ischemia, the control ischemic group, the L-arginine-treated group, the sodium ...
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TY - JOUR. T1 - Parkinsonism/dystonia syndrome secondary to multiple sclerosis with antibasal Ganglia antibodies. AU - Delgado, Silvia. AU - Baez, Sheila. AU - Singer, Carlos. AU - Sengun, Cenk. AU - Sheremata, William. AU - Papapetropoulos, Spiridon. PY - 2009/1/30. Y1 - 2009/1/30. UR - http://www.scopus.com/inward/record.url?scp=61649127335&partnerID=8YFLogxK. UR - http://www.scopus.com/inward/citedby.url?scp=61649127335&partnerID=8YFLogxK. U2 - 10.1002/mds.22331. DO - 10.1002/mds.22331. M3 - Article. C2 - 18951536. AN - SCOPUS:61649127335. VL - 24. SP - 309. EP - 311. JO - Movement Disorders. JF - Movement Disorders. SN - 0885-3185. IS - 2. ER - ...
Looking for caudate lobe? Find out information about caudate lobe. The tailed lobe of the liver that separates the right extremity of the transverse fissure from the commencement of the fissure for the inferior vena cava Explanation of caudate lobe
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Hepatic veins. the veins that drain the liver; they collect blood from the central veins and terminate in three large veins opening into the inferior vena cava below the diaphragm and several small inconstant veins entering the vena cava at more inferior levels. Syn: venae hepaticae [NA].. ...
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A hepatic vein is any of the veins that are used to carry oxygen-depleted blood out of the liver and into the inferior vena cava...
WK 5 SPLEEN PATHOLOGY Portal Hypertension-Collaterals. The spleen (S) is massively enlarged, and a markedly dilated and tortuous porto-systemic collateral vein (arrow) is seen in the splenic hilum.
Objective: To determine the safety and efficacy of transjugular intrahepatic portosystemic shunts (TIPS) in controlling bleeding from esophageal varices in patients awaiting liver transplantation.. ▪ Design: Prospective, uncontrolled trial.. ▪ Setting: University medical center with an active liver transplant program.. ▪ Patients: Thirteen patients referred for liver transplantation with either active variceal hemorrhage or recurrent variceal hemorrhage despite sclerotherapy; four patients had been previously treated with surgical portosystemic shunts.. ▪ Intervention: An intrahepatic portosystemic shunt created via a transjugular approach to the hepatic veins using expandable, flexible metallic stents.. ▪ Measurements: Portal pressures before and after the creation of the shunt, the direction of portal blood flow at differing diameters of the shunts, procedure-related complications, and outcome in terms of survival, liver transplantation, and recurrent variceal bleeding.. ▪ Main ...
The role of Transjugular Intrahepatic Portosystemic Stent-Shunt (TIPSS) in the management of variceal hemorrhage.: TIPSS can reduce failure to control bleeding
Images in a 59-year-old man with posthepatitic cirrhosis (Child-Pugh class C) who had undergone TIPS creation for refractory ascites; a Viatorr stent (10 mm ...
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Results 56 patients were included into the final analysis. In AH patients (n = 18) mean age was 48 years (30-65), mean discriminant function (DF) was 51 (24-87) and mean MELD score was 22. The 6 month mortality was 50%(9/18) with (7/9) dying within 30 days. The median HVPG (mmHg) pre-TIPS and post-TIPS were 16.5 and 6.5 respectively. In non-AH patient (n = 38) average age was 51y (25-70) mean MELD score was 14 (22-7). The mortality was 13% (5/38) at 6 months, (3/5) died by day 30. The median HVPG (mmHg) pre-TIPS and post-TIPS was 23 and 10 respectively.. ...
Percutaneous transjugular portosystemic shunt. Diagnostic and therapeutic technology assessment (DATTA). Transjugular intrahepatic portosystemic shunt (TIPS): diagnostic and therapeutic technology assessment (DATTA)
Clinically, the Valsalva maneuver is considered as main cause of defecation syncope and surgery Hepatic hemodynamics during Valsalva maneuver performed in a patient with functional suprahepatic inferior vana cava (IVC) obstruction during the Valsalva maneuver [12]. Collapsed IVC showed during the maneuver in normal healthy subjects using ultrasonography study, but IVC howed angular appearance and not collapsed during the maneuver in the venography study [10,11]. The change of IVC during the maneuver is ambiguous and hemodynamic contribution of hepatic vein and portal vein during the maneuver has not been studied in normal healthy subjects. Duplex Doppler ultrasonography of the liver provides important information about liver condition [11,13]. Hepatic vein flow depends on hepatic parenchymal compliance, thoracoabdominal pressure, and right atrial pressure. It is known that hepatic vein Doppler waveform is triphasic pattern which is composed of two anterograde flow peaks toward the heart and one ...
TIPSS (Transjugular Intrahepatic Portosystemic Shunt) is a radiologically created internal vascular shunt between the portal vein and a hepatic vein by which blood bypasses the fibrotic liver and portal ... read more ...
Portal hypertension can lead to life-threatening variceal bleeding (VB). Transjugular intrahepatic portosystemic shunt (TIPSS) is the standard choice for uncontrolled VB. Unavailable for TIPSS, we design a mesofemoral shunt (MFS) as an alternative method for control of VB.
Absent Inferior Vena Cava (IVC) is an uncommon but well recognised anomaly. Anomalies of the IVC have been described more frequently (0.6%-2%) in those with other cardiovascular defects [2], and less frequently in otherwise healthy individuals. Various anomalies of the IVC have been described including complete absence, partial absence or presence of bilateral IVC [3].. There is controversy as to whether an absent IVC is a true embryonic anomaly or whether it is the result of peri-natal IVC thrombosis causing regression and disappearance of the once present IVC [4].. There has been one previous report in the literature of an absent IVC and left renal hypoplasia- and a right hypertrophic kidney [5]; but a commoner association recognised is right renal aplasia [6] as suggested in a review by Gayer et al, where all nine patients with complete absence of the IVC had an absent or very small right kidney. The association of an absent or hypoplastic kidney is potentially related (or even the cause of ...
接著,看圖可以發現,liver被3條 hepatic vein分成4份,而其再根據portal vein 分支我們把它分成8塊。. 最要記得且特別的是S1 是尾狀葉 caudate lobe,是在S4 後方。從尾狀葉起始,照順時針方式填入順序(腦海中請記得圖),想像它是兩個時鐘 (感謝王瑞芳學姊的idea),如下:. ...
Spring Turkey - 20, no-cost, quota permits for each of 6 hunts.. Zone Tags: Zone tags are required for each person to hunt on the area except during small game and spring turkey season. During the archery and the archery/muzzleloading gun seasons, the area is divided into 7 zones with Zone A limited to 18 hunters, Zones B, C and D limited to 14 hunters each, Zone E limited to 6 hunters, Zone F limited to 32 hunters and Zone G limited to 42 hunters. Zone tags for archery and archery/muzzleloading gun hunts will be issued to hunters without quota hunt permits by random drawing at the check station at 2 p.m. on the Thursday prior to each 3-day hunt period. A person may reserve a zone tag for 1 additional hunter, but must have their valid license and permits in his/her possession to do so. Holders of quota hunt permits and exempt hunters are not required to attend the drawing on Thursdays and will be issued a special zone tag, good for the zone of their choosing, at the check station. Any unissued ...
Transjugular intrahepatic portosystemic shunt (TIPS) is a procedure that may be used to reduceportal hypertensionand its complications, especiallyvariceal bleeding. A TIPS procedure may be done by a radiologist, who places a small wire-mesh coil (stent) into a liver vein. The stent is then expanded using a small inflatable balloon (angioplasty). The stent forms a channel, or shunt, that bypasses the liver. This channel reduces pressure in the portal vein. By reducing portal hypertension, enlarged veins (varices) are less likely to rupture and bleed. And other complications of cirrhosis called ascites (fluid in the abdomen) and hepatic hydrothorax (fluid between the lungs and the chest wall) may improve or go away.. TIPS may be used to:. ...
BACKGROUND: Transjugular intrahepatic portosystemic shunt (TIPS) is currently used for the treatment of complications of portal hypertension. The incidence of hepatic encephalopathy (HE) remains a problem in TIPS placement. It has been reported that the right branch mainly receives superior mesenteric venous blood while the left branch mainly receives blood from the splenic vein. We hypothesized that targeted puncture of the left portal vein would divert the non-nutritive blood from the splenic vein into the TIPS shunt; therefore, targeted puncture of the left branch of the intrahepatic portal vein during TIPS may reduce the risk of HE. AIM: To evaluate the influence of targeted puncture of left branch of portal vein in TIPS on HE. METHODS: A retrospective analysis of 1244 patients with portal-hypertension-related complications of refractory ascites or variceal bleeding who underwent TIPS from January 2000 to January 2013 was performed. Patients were divided into group A (targeting left branch ...
Reports on varicose veins, proximal venous outflow obstruction as in May Thurner Syndrome, and gonadal vein reflux resulting in varicocele or pelvic congestion syndrome have described these venous conditions primarily as separate and unrelated. This case suggests that in at least some selected patients, there may be a possible interrelationship between these three venous conditions. The varicocele, a male equivalent of the female pelvic congestion syndrome, is due to reflux in the left testicular vein or gonadal vein. Several causes of gonadal vein reflux have been reported including a venous outflow obstruction in the left renal vein as seen in the Nutcracker syndrome and a quantitative and/or functional abnormality in the venous valves within the gonadal vein. Many of these patients are asymptomatic, but varicocele has been reported as a contributory cause of infertility in male. The "bag of worms" is the classic physical finding associated with varicocele, but the condition may not be easily ...

The role of transjugular intrahepatic portosystemic shunt in the management of portal hypertension - Boyer - 2005 - Hepatology ...The role of transjugular intrahepatic portosystemic shunt in the management of portal hypertension - Boyer - 2005 - Hepatology ...

TIPS for acute and chronic Budd-Chiari syndrome: a single center experience. J Hepatol 2003; 38: 751-754.. *CrossRef, ... The diagnosis and management of the Budd-Chiari syndrome: consensus and controversies. HEPATOLOGY 2003; 38: 793-803.. Direct ... Determinants of survival and the effect of portosystemic shunting in patients with Budd-Chiari syndrome. HEPATOLOGY 2004; 39: ... Proposal of a new nomenclature for Budd-Chiari syndrome: hepatic vein thrombosis versus thrombosis of the inferior vena cava at ...
more infohttp://onlinelibrary.wiley.com/doi/10.1002/hep.20559/references?globalMessage=0

Polycythaemia Rubra Vera. PRV information and treatment | PatientPolycythaemia Rubra Vera. PRV information and treatment | Patient

Budd-Chiari syndrome:*Occurs in about 2-10% of cases of PV but when it occurs it should always raise suspicion of the condition ... Is due to hypoxia causing erythropoietin release as in Eisenmengers syndrome, chronic obstructive pulmonary disease (COPD) or ...
more infohttps://patient.info/doctor/polycythaemia-vera-pro

Budd-Chiari syndrome - WikipediaBudd-Chiari syndrome - Wikipedia

Budd-Chiari syndrome)". "The Budd-Chiari syndrome: a review". "Budd-Chiari syndrome: long-term survival and factors affecting ... "Budd-Chiari Syndrome: clinical patterns and therapy". "Budd-Chiari syndrome: etiology, diagnosis and management". "Case records ... independently of Budd-Chiari syndrome. It is named after George Budd, a British physician, and Hans Chiari, an Austrian ... Budd-Chiari syndrome at Who Named It? Budd G (1845). On diseases of the liver. London: John Churchill. p. 135. Brit Lib. ...
more infohttps://en.wikipedia.org/wiki/Budd%E2%80%93Chiari_syndrome

Hepatic Vein Thrombosis (Budd-Chiari Syndrome)Hepatic Vein Thrombosis (Budd-Chiari Syndrome)

Understanding Hepatic Vein Thrombosis (Budd-Chiari Syndrome). Medically reviewed by Alana Biggers, MD on May 11, 2017. - ...
more infohttps://www.healthline.com/health/hepatic-vein-obstruction-budd-chiari

Budd-Chiari Syndrome (BCS) - GlossaryBudd-Chiari Syndrome (BCS) - Glossary

This glossary can help you to easily understand medical terms related to the article on Budd-Chiari Syndrome ...
more infohttps://www.medindia.net/patients/patientinfo/budd-chiari-syndrome-glossary.htm

Budd-Chiari Syndrome: Practice Essentials, Background, PathophysiologyBudd-Chiari Syndrome: Practice Essentials, Background, Pathophysiology

Budd-Chiari syndrome is an uncommon condition induced by thrombotic or nonthrombotic obstruction of hepatic venous outflow and ... Budd-Chiari Syndrome) and Budd-Chiari Syndrome What to Read Next on Medscape. Related Conditions and Diseases. * Budd-Chiari ... The clinical variants of Budd-Chiari syndrome have been described as follows [5, 6, 7] :. * Acute and subacute forms: ... Overt Budd-Chiari syndrome generally requires the occlusion of at least 2 hepatic veins. [8] Venous congestion of the liver ...
more infohttps://emedicine.medscape.com/article/184430-overview

Budd-Chiari Syndrome Imaging: Overview, Radiography, Computed TomographyBudd-Chiari Syndrome Imaging: Overview, Radiography, Computed Tomography

... a manifestation of hepatic venous outflow obstruction that was first described by Budd in 1845 and then expounded on by Chiari ... encoded search term (Budd-Chiari Syndrome Imaging) and Budd-Chiari Syndrome Imaging What to Read Next on Medscape. Related ... Budd-Chiari syndrome (BCS) is a manifestation of hepatic venous outflow obstruction that was first described by Budd in 1845 [1 ... Budd-Chiari Syndrome Imaging. Updated: Nov 06, 2015 * Author: Ali Nawaz Khan, MBBS, FRCS, FRCP, FRCR; Chief Editor: John Karani ...
more infohttps://emedicine.medscape.com/article/364420-overview

Budd-Chiari syndrome overview --Doctors LoungeBudd-Chiari syndrome overview --Doctors Lounge

... appear to be especially at risk for Budd-Chiari syndrome, more than other forms of thrombophilia: up to 40% develops Budd- ... Budd-Chiari syndrome is the clinical picture caused by occlusion of the hepatic vein.. Causes. *Primary (75%): thrombosis of ... When Budd-Chiari syndrome is suspected, measurements are made of liver enzyme levels and other organ markers (creatinine, urea ... Budd-Chiari syndrome is diagnosed using ultrasound studies of the abdomen, although occasionally more invasive methods have to ...
more infohttps://www.doctorslounge.com/index.php/reference/diseases/168

Prognostic Assessment of Budd-Chiari Syndrome | SpringerLinkPrognostic Assessment of Budd-Chiari Syndrome | SpringerLink

Budd-Chiari syndrome, also termed as hepatic venous outflow tract obstruction (HVOTO), is a congestive disorder of liver due to ... Acharya S.K., Bopanna S. (2020) Prognostic Assessment of Budd-Chiari Syndrome. In: Qi X. (eds) Budd-Chiari Syndrome. Springer, ... HVOTO Budd-Chiari syndrome Angioplasty Stenting Prognostic-models This is a preview of subscription content, log in to check ... Good long-term outcome of Budd-Chiari syndrome with a stepwise management. Hepatology. 2013;57:1962-8.CrossRefGoogle Scholar ...
more infohttps://link.springer.com/chapter/10.1007%2F978-981-32-9232-1_15

Budd Chiari Syndrome - NORD (National Organization for Rare Disorders)Budd Chiari Syndrome - NORD (National Organization for Rare Disorders)

... of all cases of Budd-Chiari syndrome is unknown. Approximately 10% of individuals with Budd-Chiari syndrome have polycythemia ... Budd Chiari Syndrome. Synonyms of Budd Chiari Syndrome. *Budds Syndrome. *Chiari-Budd Syndrome ... This syndrome may begin gradually or abruptly. Symptoms associated with Budd-Chiari syndrome include pain in the upper right ... In some cases, Budd-Chiari syndrome may be treated surgically by diverting blood flow from one vein to another (shunting). In ...
more infohttps://rarediseases.org/rare-diseases/budd-chiari-syndrome/

Budd-Chiari syndromeBudd-Chiari syndrome

... (BCS) is an eponym for obstruction of the hepatic venous outflow tract at any level from the hepatic ... "Hepatic outflow obstruction (Budd-Chiari syndrome). Experience with 177 patients and a review of the literature". Medicine ( ... "The Budd-Chiari syndrome.". N Eng J Med. vol. 350. 2004. pp. 578-85. ... Diagnostic Confirmation: Are you sure your patient has Budd-Chiari syndrome?. A definitive diagnosis of BCS is made on the ...
more infohttps://www.neurologyadvisor.com/hospital-medicine/budd-chiari-syndrome/article/601437/

Controversies in the Management of Budd-Chiari Syndrome | SpringerLinkControversies in the Management of Budd-Chiari Syndrome | SpringerLink

The flowchart of Budd-Chiari Syndrome (BCS) management is not evidence-based and relies to experts opinion. The aim of this ... Mancuso A. (2020) Controversies in the Management of Budd-Chiari Syndrome. In: Qi X. (eds) Budd-Chiari Syndrome. Springer, ... Mancuso A. Outcome of Budd-Chiari syndrome in Behçets syndrome. Semin Arthritis Rheum. 2015;45:e1.PubMedCrossRefPubMedCentral ... Mancuso A. Budd-Chiari syndrome management: lights and shadows. World J Hepatol. 2011;3:262-4.PubMedPubMedCentralCrossRefGoogle ...
more infohttps://link.springer.com/chapter/10.1007%2F978-981-32-9232-1_19

Budd Chiari Syndrome and Splanchnic Vascular DisordersBudd Chiari Syndrome and Splanchnic Vascular Disorders

Information on Budd Chiari Syndrome and Splanchnic Vascular Disorders at the Centre for Rare Diseases in the Heritage Building ... Budd Chiari Syndrome and Splanchnic Vascular Disorders. Vascular disorders of the liver are rare and often affect young adults ... Home, Services, Centre for Rare Diseases, Budd Chiari Syndrome and Splanchnic Vascular Disorders ... Meet the teamDetails of the Budd Chiari Syndrome and Splanchnic Vascular Disorders team at the Centre for Rare Diseases in the ...
more infohttps://www.uhb.nhs.uk/crd-budd.htm

Budd-Chiari syndrome - The Clinical AdvisorBudd-Chiari syndrome - The Clinical Advisor

Budd-Chiari syndrome (BCS) is an eponym for obstruction of the hepatic venous outflow tract at any level from the hepatic ... "Hepatic outflow obstruction (Budd-Chiari syndrome). Experience with 177 patients and a review of the literature". Medicine ( ... "The Budd-Chiari syndrome.". N Eng J Med. vol. 350. 2004. pp. 578-85. ... Diagnostic Confirmation: Are you sure your patient has Budd-Chiari syndrome?. A definitive diagnosis of BCS is made on the ...
more infohttps://www.clinicaladvisor.com/hospital-medicine/budd-chiari-syndrome/article/601431/

Budd-Chiari syndrome in chronic myeloid leukemia | HaematologicaBudd-Chiari syndrome in chronic myeloid leukemia | Haematologica

Thank you for your interest in spreading the word about Haematologica.. NOTE: We only request your email address so that the person you are recommending the page to knows that you wanted them to see it, and that it is not junk mail. We do not capture any email address.. ...
more infohttp://www.haematologica.org/content/85/4/429

The Budd-Chiari syndrome in pregnancy. | Postgraduate Medical JournalThe Budd-Chiari syndrome in pregnancy. | Postgraduate Medical Journal

A case of Budd-Chiari syndrome in a young woman, which started probably in the last trimester of pregnancy, is described. The ...
more infohttp://pmj.bmj.com/content/54/636/686

Radiological intervention in Budd-Chiari syndrome: techniques and outcome in 18 patients.  - PubMed - NCBIRadiological intervention in Budd-Chiari syndrome: techniques and outcome in 18 patients. - PubMed - NCBI

Radiological intervention in Budd-Chiari syndrome: techniques and outcome in 18 patients.. Griffith JF1, Mahmoud AE, Cooper S, ... We reviewed our experience of the therapeutic role of radiology in Budd-Chiari syndrome. Patients with stenosis and/or ... of radiological intervention make it the preferred first line of treatment in selected patients with Budd-Chiari syndrome. ... Budd-Chiari Syndrome/diagnostic imaging. *Budd-Chiari Syndrome/etiology. *Budd-Chiari Syndrome/therapy* ...
more infohttps://www.ncbi.nlm.nih.gov/pubmed/8937320?dopt=Abstract

Budd Chiari syndrome | definition of Budd Chiari syndrome by Medical dictionaryBudd Chiari syndrome | definition of Budd Chiari syndrome by Medical dictionary

What is Budd Chiari syndrome? Meaning of Budd Chiari syndrome medical term. What does Budd Chiari syndrome mean? ... Looking for online definition of Budd Chiari syndrome in the Medical Dictionary? Budd Chiari syndrome explanation free. ... Budd Chiari syndrome. Budd Chiari syndrome. A condition defined by obstruction of the hepatic veins and its clinical ... Antiphospholipid syndrome and Budd Chiari syndrome.. A number of syndromes overlapped with SLE like Sjogrens syndrome, ...
more infohttps://medical-dictionary.thefreedictionary.com/Budd+Chiari+syndrome

Budd-Chiari syndromeBudd-Chiari syndrome

... (BCS) is an eponym for obstruction of the hepatic venous outflow tract at any level from the hepatic ... "Hepatic outflow obstruction (Budd-Chiari syndrome). Experience with 177 patients and a review of the literature". Medicine ( ... "The Budd-Chiari syndrome.". N Eng J Med. vol. 350. 2004. pp. 578-85. ... Diagnostic Confirmation: Are you sure your patient has Budd-Chiari syndrome?. A definitive diagnosis of BCS is made on the ...
more infohttps://www.infectiousdiseaseadvisor.com/hospital-medicine/budd-chiari-syndrome/article/601439/

glossary:budd-chiari syndrome [Lymphedema People]glossary:budd-chiari syndrome [Lymphedema People]

glossary:budd-chiari_syndrome. Budd-Chiari syndrome is a rare problem that results from blood clotting in the veins flowing out ... glossary/budd-chiari_syndrome.txt · Last modified: 2012/10/16 14:40 (external edit) ...
more infohttp://lymphedemapeople.com/wiki/doku.php?id=glossary:budd-chiari_syndrome

Liver cirrhosis caused by chronic Budd-Chiari syndromeLiver cirrhosis caused by chronic Budd-Chiari syndrome

Chronic Budd-Chiari syndrome (BCS) is a rare cause of liver cirrhosis (LC) and tends to be misdiagnosed in clinical practice. ...
more infohttps://insights.ovid.com/medi/201708250/00005792-201708250-00003

Diagnostic Tests for Budd-Chiari syndrome - RightDiagnosis.comDiagnostic Tests for Budd-Chiari syndrome - RightDiagnosis.com

Diagnostic Tests for Budd-Chiari syndrome including blood tests, urine tests, swabs, diagnostic tests, lab tests, and pathology ... Budd-Chiari syndrome: Introduction. *Symptoms of Budd-Chiari syndrome *Home Diagnostic Testing *Alternative Diagnoses * ... These home medical tests may be relevant to Budd-Chiari syndrome: *Food Allergies & Intolerances: Home Testing: *Home Food ... Prognosis of Budd-Chiari syndrome. *Deaths from Budd-Chiari syndrome. *Doctors and Medical Specialists for Budd-Chiari syndrome ...
more infohttp://www.rightdiagnosis.com/b/budd_chiari_syndrome/tests.htm

2012 ICD-9-CM Diagnosis Code 453.0 : Budd-chiari syndrome2012 ICD-9-CM Diagnosis Code 453.0 : Budd-chiari syndrome

Budd-chiari syndrome. *ICD-9-CM 453.0 is a billable medical code that can be used to indicate a diagnosis on a reimbursement ... Budd-Chiari syndrome (hepatic vein thrombosis) 453.0. *Chiaris*. disease or syndrome (hepatic vein thrombosis) 453.0 ... Syndrome - see also Disease*. Budd-Chiari (hepatic vein thrombosis) 453.0. *. Chiaris (hepatic vein thrombosis) 453.0 ...
more infohttp://www.icd9data.com/2012/Volume1/390-459/451-459/453/453.0.htm

Budd-Chiari syndrome and essential thrombocythemia in a child: favorable outcome after transjugular intrahepatic portosystemic...Budd-Chiari syndrome and essential thrombocythemia in a child: favorable outcome after transjugular intrahepatic portosystemic...

Budd-Chiari syndrome and essential thrombocythemia in a child: favorable outcome after transjugular intrahepatic portosystemic ...
more infohttps://www.ncbi.nlm.nih.gov/pubmed/18376254?dopt=Abstract

Somatic calreticulin mutations in patients with Budd-Chiari syndrome and portal vein thrombosis | HaematologicaSomatic calreticulin mutations in patients with Budd-Chiari syndrome and portal vein thrombosis | Haematologica

Myeloproliferative neoplasms in Budd-Chiari syndrome and portal vein thrombosis: a meta-analysis. Blood. 2012;120(25):4921-4928 ... Etiology, management, and outcome of the Budd-Chiari syndrome. Ann Intern Med. 2009;151(3):167-175.. ... Myeloproliferative disease in the pathogenesis and survival of Budd-Chiari syndrome. Haematologica. 2006;91(12):1712-1713.. ... We studied the role of the recently identified CALR mutations in 141 patients with Budd-Chiari Syndrome (BCS) or portal vein ...
more infohttp://www.haematologica.org/content/100/6/e226
  • Depending on these Post mortem findings, it was concluded that she had an acute type of Budd Chiari Syndrome from which she never recovered and succumbed to death. (thefreedictionary.com)
  • Budd-Chiari syndrome and essential thrombocythemia in a child: favorable outcome after transjugular intrahepatic portosystemic shunt. (nih.gov)
  • Symptoms of the following disorders can be similar to those of Budd-Chiari syndrome. (rarediseases.org)
  • Meet the team Details of the Budd Chiari Syndrome and Splanchnic Vascular Disorders team at the Centre for Rare Diseases in the Heritage Building (QEH). (uhb.nhs.uk)