2-Oxoisovalerate Dehydrogenase (Acylating)
Methylmalonate-Semialdehyde Dehydrogenase (Acylating)
An enzyme that plays a role in the VALINE; LEUCINE; and ISOLEUCINE catabolic pathways by catalyzing the oxidation of 2-methyl-3-oxopropanate to propanoyl-CoA using NAD+ as a coenzyme. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated BETA-ALANINE and 3-hydropropionic acid.
2-oxoisovalerate dehydrogenase (acylating)
... acylating) (EC 1.2.1.25) is an enzyme that catalyzes the chemical reaction 3-methyl-2-oxobutanoate + CoA + NAD+ ⇌ {\ ... and alpha-ketoisovalerate dehydrogenase. This enzyme participates in valine, leucine and isoleucine degradation. Namba Y, ... and nicotinamide adenine dinucleotide-dependent branched chain alpha-keto acid dehydrogenase. I. Purification and properties of ... The systematic name of this enzyme class is 3-methyl-2-oxobutanoate:NAD+ 2-oxidoreductase (CoA-methyl-propanoylating). Other ...
List of MeSH codes (D08)
... methylmalonate-semialdehyde dehydrogenase (acylating) MeSH D08.811.682.657.163.835 - retinal dehydrogenase MeSH D08.811.682.657 ... malate dehydrogenase MeSH D08.811.682.047.748 - malate dehydrogenase (nadp+) MeSH D08.811.682.047.892 - xanthine dehydrogenase ... acetoin dehydrogenase MeSH D08.811.682.047.070 - alcohol dehydrogenase MeSH D08.811.682.047.150 - carbohydrate dehydrogenases ... acylating) MeSH D08.811.682.657.350.875 - pyruvate dehydrogenase (lipoamide) MeSH D08.811.682.657.350.937 - pyruvate oxidase ...
Code System Concept
DeCS
Acylating) * Pyruvate Dehydrogenase (Lipoamide) [D08.811.682.657.350.875] Pyruvate Dehydrogenase (Lipoamide) ... Dehydrogenase, alpha-Ketoisovalerate. alpha Ketoisovalerate Dehydrogenase. alpha-Ketoisovalerate Dehydrogenase. Tree number(s): ... Acylating) - Preferred Concept UI. M0077427. Scope note. An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2- ... Dehydrogenase, 2-Oxoisovalerate Dehydrogenase, alpha-Ketoisovalerate alpha Ketoisovalerate Dehydrogenase alpha-Ketoisovalerate ...
DeCS 2011 - December 22, 2011 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
BiGG Gene 12039
... acylating; 4-methyl-2-oxopentaoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ... acylating; 3-methyl-2-oxobutanoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ... acylating; 3-methyl-2-oxopentanoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ...
DeCS 2008 - May 16, 2008 version
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
DeCS 2014 - December 16, 2014 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2011 - December 22, 2011 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2014 - December 16, 2014 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2011 - December 22, 2011 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2016 - July 28, 2016 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2008 - May 16, 2008 version
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
DeCS 2009 - February 20, 2009 version
3 beta-Hydroxy-delta-5-Steroid Dehydrogenase use Progesterone Reductase 3-beta-Hydroxysteroid Dehydrogenase use 3- ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ...
DeCS 2010 - February 12, 2010 version
5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2-Amino-5-phosphonovaleric Acid use 2-Amino-5-phosphonovalerate 2-Amino-6-(1,2,3-trihydroxypropyl)-4(3H)-pteridinone use ...
DeCS 2009 - February 20, 2009 version
3 beta-Hydroxy-delta-5-Steroid Dehydrogenase use Progesterone Reductase 3-beta-Hydroxysteroid Dehydrogenase use 3- ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ...
DeCS 2013 - July 15, 2013 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2013 - December 17, 2013 version
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
DeCS 2008 - May 16, 2008 version
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
Difference between revisions of "Task 3: odba human Sequence-based predictions" - Bioinformatikpedia
GOPET predicts for our Protein multiple exclusive categories of dehydrogenases so we would assume that the protein in fact has ... GOPET predicts for our Protein multiple exclusive categories of dehydrogenases so we would assume that the protein in fact has ... Without further information about the protein it would be hard to decide which of the predicted dehydrogenase categories it ... Without further information about the protein it would be hard to decide which of the predicted dehydrogenase categories it ...
SMPDB
oxoisovalerate. dehydrogenase. subunit alpha,. mitochondrial. Dihydrolipoyl. dehydrogenase,. mitochondrial. ... dehydrogenase. [acylating],. mitochondrial. Propionyl-CoA. carboxylase. alpha chain,. mitochondrial. Propionyl-CoA. carboxylase ... dehydrogenase,. mitochondrial. Isobutyryl-CoA. dehydrogenase,. mitochondrial. Medium-chain. specific. acyl-CoA. dehydrogenase, ... oxoisovalerate. dehydrogenase. Lipoamide. acyltransferase. component of. branched-chain. alpha-keto acid. dehydrogenase. ...
PathBank
oxoisovalerate. dehydrogenase. subunit alpha,. mitochondrial. Dihydrolipoyl. dehydrogenase. Hydroxymethylglutaryl-. CoA lyase, ... dehydrogenase. [acylating],. mitochondrial. Pyruvate. carboxylase,. mitochondrial. Propionyl-CoA. carboxylase. beta chain,. ... 2. O. O. 2. Methylmalonic. acid. Hydrogen. peroxide. NAD. H. 2. O. NADH. H. 2. O. Acetoacetyl-CoA. H. 2. O. CoA. CoA. Succinyl- ... 2. O. ATP. Hydrogen. carbonate. 3-Methylglutaconyl-CoA. ADP. Dihydrolipoamide. NAD. NADH. H. +. CoA. Isobutyryl-CoA. CO. 2. CO ...