An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2-oxobutanoate to 2-methylpropanoyl-CoA. It plays a role in the degradation of VALINE; LEUCINE; and ISOLEUCINE.
The addition of an organic acid radical into a molecule.
An enzyme that plays a role in the VALINE; LEUCINE; and ISOLEUCINE catabolic pathways by catalyzing the oxidation of 2-methyl-3-oxopropanate to propanoyl-CoA using NAD+ as a coenzyme. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated BETA-ALANINE and 3-hydropropionic acid.
... acylating) (EC 1.2.1.25) is an enzyme that catalyzes the chemical reaction 3-methyl-2-oxobutanoate + CoA + NAD+ ⇌ {\ ... and alpha-ketoisovalerate dehydrogenase. This enzyme participates in valine, leucine and isoleucine degradation. Namba Y, ... and nicotinamide adenine dinucleotide-dependent branched chain alpha-keto acid dehydrogenase. I. Purification and properties of ... The systematic name of this enzyme class is 3-methyl-2-oxobutanoate:NAD+ 2-oxidoreductase (CoA-methyl-propanoylating). Other ...
... methylmalonate-semialdehyde dehydrogenase (acylating) MeSH D08.811.682.657.163.835 - retinal dehydrogenase MeSH D08.811.682.657 ... malate dehydrogenase MeSH D08.811.682.047.748 - malate dehydrogenase (nadp+) MeSH D08.811.682.047.892 - xanthine dehydrogenase ... acetoin dehydrogenase MeSH D08.811.682.047.070 - alcohol dehydrogenase MeSH D08.811.682.047.150 - carbohydrate dehydrogenases ... acylating) MeSH D08.811.682.657.350.875 - pyruvate dehydrogenase (lipoamide) MeSH D08.811.682.657.350.937 - pyruvate oxidase ...
... acylating) Active Synonym false false 3721199012 2-oxoisovalerate dehydrogenase (acylating) Active Synonym false false ... 2-oxoisovalerate dehydrogenase (acylating) (substance). Code System Preferred Concept Name. 2-oxoisovalerate dehydrogenase ( ...
Acylating) * Pyruvate Dehydrogenase (Lipoamide) [D08.811.682.657.350.875] Pyruvate Dehydrogenase (Lipoamide) ... Dehydrogenase, alpha-Ketoisovalerate. alpha Ketoisovalerate Dehydrogenase. alpha-Ketoisovalerate Dehydrogenase. Tree number(s): ... Acylating) - Preferred Concept UI. M0077427. Scope note. An NAD+ dependent enzyme that catalyzes the oxidation 3-methyl-2- ... Dehydrogenase, 2-Oxoisovalerate Dehydrogenase, alpha-Ketoisovalerate alpha Ketoisovalerate Dehydrogenase alpha-Ketoisovalerate ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
... acylating; 4-methyl-2-oxopentaoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ... acylating; 3-methyl-2-oxobutanoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ... acylating; 3-methyl-2-oxopentanoate), mitochondrial. (13171 and (12040 and 12039) and 13382) or (13171 and 13382 and (12040 and ...
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
3 beta-Hydroxy-delta-5-Steroid Dehydrogenase use Progesterone Reductase 3-beta-Hydroxysteroid Dehydrogenase use 3- ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ...
5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2-Amino-5-phosphonovaleric Acid use 2-Amino-5-phosphonovalerate 2-Amino-6-(1,2,3-trihydroxypropyl)-4(3H)-pteridinone use ...
3 beta-Hydroxy-delta-5-Steroid Dehydrogenase use Progesterone Reductase 3-beta-Hydroxysteroid Dehydrogenase use 3- ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-DiHETE use Leukotriene ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ... Acylating) 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 5,10-Methylenetetrahydrofolate-Reductase (NADH) use Methylenetetrahydrofolate Dehydrogenase (NAD+) 5,12-diHETE use Leukotriene ... 5-alpha-Reductase, Testosterone use 3-Oxo-5-alpha-Steroid 4-Dehydrogenase ...
Dehydrogenase (Acylating). 2-Oxoisovalerate Dehydrogenase (Lipoamide) use 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide) ... 3-Keto-5-alpha-Steroid delta-4-Dehydrogenase use Testosterone 5-alpha-Reductase ... 2H-Benzo(a)quinolizin-2-ol, 2-Ethyl-1,3,4,6,7,11b-hexahydro-3-isobutyl-9,10-dimethoxy- ... 3-Pyridinecarboxylic acid, 1,4-dihydro-2,6-dimethyl-5-nitro-4-(2-(trifluoromethyl)phenyl)-, Methyl ester ...
GOPET predicts for our Protein multiple exclusive categories of dehydrogenases so we would assume that the protein in fact has ... GOPET predicts for our Protein multiple exclusive categories of dehydrogenases so we would assume that the protein in fact has ... Without further information about the protein it would be hard to decide which of the predicted dehydrogenase categories it ... Without further information about the protein it would be hard to decide which of the predicted dehydrogenase categories it ...
oxoisovalerate. dehydrogenase. subunit alpha,. mitochondrial. Dihydrolipoyl. dehydrogenase,. mitochondrial. ... dehydrogenase. [acylating],. mitochondrial. Propionyl-CoA. carboxylase. alpha chain,. mitochondrial. Propionyl-CoA. carboxylase ... dehydrogenase,. mitochondrial. Isobutyryl-CoA. dehydrogenase,. mitochondrial. Medium-chain. specific. acyl-CoA. dehydrogenase, ... oxoisovalerate. dehydrogenase. Lipoamide. acyltransferase. component of. branched-chain. alpha-keto acid. dehydrogenase. ...
oxoisovalerate. dehydrogenase. subunit alpha,. mitochondrial. Dihydrolipoyl. dehydrogenase. Hydroxymethylglutaryl-. CoA lyase, ... dehydrogenase. [acylating],. mitochondrial. Pyruvate. carboxylase,. mitochondrial. Propionyl-CoA. carboxylase. beta chain,. ... 2. O. O. 2. Methylmalonic. acid. Hydrogen. peroxide. NAD. H. 2. O. NADH. H. 2. O. Acetoacetyl-CoA. H. 2. O. CoA. CoA. Succinyl- ... 2. O. ATP. Hydrogen. carbonate. 3-Methylglutaconyl-CoA. ADP. Dihydrolipoamide. NAD. NADH. H. +. CoA. Isobutyryl-CoA. CO. 2. CO ...

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