Acyl-CoA Dehydrogenase, Long-ChainLipid Metabolism, Inborn ErrorsAcyl-CoA DehydrogenasesCarnitineMitochondrial DiseasesMuscular DiseasesAcyl-CoA DehydrogenaseBezafibrateAcyl Coenzyme AFatty Acid DesaturasesFatty AcidsMitochondria, LiverChromosomes, Human, Pair 17Oxidation-ReductionDNA, ComplementaryDNA PrimersMitochondriaFibroblastsTissue DistributionMolecular Sequence DataMuscle, SkeletalMutationBase SequenceInfant, NewbornMice, KnockoutAmino Acid SequenceCloning, Molecular