Carbohydrate Metabolism, Inborn Errorsalpha-MannosidosisMannosidasesTwinsDiseases in TwinsDisaccharidasesTwins, MonozygoticMannoseTwins, ConjoinedTwins, Dizygoticalpha-MannosidaseSwainsonineCat DiseasesCattle DiseasesOligosaccharidesLysosomesTwin Studies as TopicCobaltPregnancy, TwinChromatography, Thin LayerEdetic AcidCattleIsoelectric Focusingalpha 1-AntitrypsinReceptors, Adrenergic, alphaHypoxia-Inducible Factor 1, alpha SubunitPregnancy, Multiplealpha7 Nicotinic Acetylcholine ReceptorIntegrin alpha3beta1Integrin alpha4Integrin alpha6Integrin alpha5beta1Fetofetal TransfusionPregnancyIntegrin alpha4beta1Interleukin-1alphaIntegrin alpha2beta1Receptors, Adrenergic, alpha-1Integrin alpha5Integrin alpha1beta1Receptors, Adrenergic, alpha-2Base SequenceIntegrin alpha6beta1Integrin alpha6beta4Integrin alpha ChainsTripletsIntegrinsAlpha RhythmIntegrin alpha1Molecular Sequence DataIntegrin alpha3Protein Bindingalpha 1-Antitrypsin DeficiencyReceptors, NicotinicAdrenergic alpha-AgonistsPPAR alphaDinoprostRecombinant ProteinsAdrenergic alpha-AntagonistsBinding SitesHepatocyte Nuclear Factor 1-alphaTransfectionGene Expression RegulationSignal TransductionKineticsalpha 1-AntichymotrypsinTransforming Growth Factor alphaTranscription FactorsGestational AgeEnvironmentAdrenergic alpha-1 Receptor AntagonistsPregnancy Reduction, Multifetalalpha KaryopherinsMacromolecular SubstancesTumor Necrosis Factor-alphaPhenotypePrazosin
Patients1
- CONCLUSIONS: The application of both HPLC-FLD and NMR in quantification of oligosaccharide biomarkers is a suitable approach for monitoring of therapy efficacy in alpha-mannosidosis patients. (bvsalud.org)