Metabolism, Inborn ErrorsKidney TubulesAmino Acid Metabolism, Inborn ErrorsAmino AcidsAbsorptionKidney Tubules, ProximalInulinGlomerular Filtration RateKidneyAmino Acids, SulfurAmino Acids, Branched-ChainAminohippuric AcidsSodiumChlorothiazideDiuresisKidney Tubules, DistalSequence Homology, Amino AcidFanconi SyndromeNephronsNatriuresisCalcium Metabolism DisordersPhosphatesAmino Acid SequenceLipid Metabolism, Inborn ErrorsKidney Concentrating AbilityLiverSodium ChlorideCephapirinAmino Acids, EssentialPuncturesLipid MetabolismMutationNeonatal ScreeningAmino Acids, AromaticBicarbonatesGlucosePurine-Pyrimidine Metabolism, Inborn ErrorsMetabolomeSteroid Metabolism, Inborn ErrorsEnergy MetabolismDibekacinHypophosphatemia, FamilialFatty AcidsLeucineMolecular Sequence DataNephrocalcinosisLow Density Lipoprotein Receptor-Related Protein-2Carbohydrate Metabolism, Inborn ErrorsAmino Acid SubstitutionPotassiumMetabolic Networks and PathwaysMetabolic Clearance RateProbenecidGlycosuriaNitrogenCloning, MolecularDogsBase SequenceNetilmicinMetabolomicsGlutamineHypophosphatemiaAmmoniaMethionineKineticsParathyroid HormoneAlanineUrea Cycle Disorders, InbornRats, Inbred StrainsUreaLithiumBrain Diseases, Metabolic, InbornRenal CirculationKidney GlomerulusFurosemideKidney Function TestsArgininosuccinic AciduriaPhosphorusBiological TransportUrineCarbon IsotopesHyperammonemiaPhenylalanineExtracellular SpaceSequence AlignmentDietary ProteinsTransaminasesModels, BiologicalHomeostasisMaple Syrup Urine DiseaseCalciumBacterial ProteinsKeto AcidsSymportersPhenylketonuriasOsmolar ConcentrationGas Chromatography-Mass SpectrometryEscherichia coliGene Expression ProfilingRNA, Messenger