CystinuriaCystineAmino Acids, DiaminoAmino Acid Transport Systems, BasicAmino AcidsAmino Acid Transport SystemsBiological TransportAmino Acid SequenceLysineArginineSequence Homology, Amino AcidMolecular Sequence DataAmino Acid SubstitutionCystinosisAbsorptionCloning, MolecularBiological Transport, ActiveAmino Acids, EssentialKineticsKidney Tubules, ProximalSodiumMutationBase SequenceSequence AlignmentAmino Acids, SulfurEscherichia coliKidney TubulesBinding SitesAmino Acid Transport System y+Amino Acid MotifsCystine Knot MotifsHydrogen-Ion ConcentrationKidneyCarrier ProteinsMutagenesis, Site-DirectedProtein ConformationLeucineKidney Tubules, DistalModels, MolecularRecombinant ProteinsDNA, ComplementaryCysteineMembrane Transport ProteinsCell LinePeptide FragmentsProtein BindingStructure-Activity RelationshipNeutral RedSequence Homology, Nucleic AcidProtein Structure, TertiaryAmino Acids, Branched-ChainSubstrate SpecificityAmino Acids, AromaticIon TransportMolecular WeightPeptidesBacterial ProteinsAmino Acid Transport Systems, NeutralProtein TransportRNA, MessengerCell MembraneMethionineDNAAlanineProteinsBicarbonatesAmino Acids, NeutralElectrophoresis, Polyacrylamide GelChromatography, High Pressure LiquidNephronsRecombinant Fusion ProteinsPhylogenyAxonal TransportInulinNeutral CeramidaseLoop of HenleMembrane ProteinsRestriction MappingProtein Structure, SecondaryCysteamineSpecies SpecificitySequence Analysis, DNACattleGenes, BacterialRabbitsPlasmidsDNA PrimersFanconi SyndromeConserved SequenceGlomerular Filtration RateGlutamineIsoleucineGlycineSodium ChloridePotassiumProlineCells, CulturedGlucoseWater-Electrolyte BalanceSymporters