Cystic Fibrosis Transmembrane Conductance RegulatorCystic FibrosisChloride ChannelsChloridesMice, Inbred CFTRMutationIon Channel GatingCell LineIon TransportMembrane ProteinsEpithelial CellsIodidesColforsinAminophenolsMolecular Sequence DataRespiratory MucosaCyclic AMPNasal MucosaGold CompoundsPatch-Clamp TechniquesCell MembraneMembrane Potentialsortho-AminobenzoatesAdenosine TriphosphateAnionsCricetinaeAmino Acid SequenceProtein Structure, TertiaryElectric ConductivityCyclic AMP-Dependent Protein KinasesBicarbonates4,4'-Diisothiocyanostilbene-2,2'-Disulfonic Acid1-Methyl-3-isobutylxanthineChlorineTransfectionCHO CellsNitrobenzoatesTracheaElectrophysiologyBronchiEosine I BluishSweatEpithelial Sodium ChannelsAmilorideMesylatesOocytesGlyburideEpitheliumBase SequenceAdenylyl ImidodiphosphateGenisteinCells, CulturedRecombinant ProteinsProtein BindingProtein FoldingBiotinylationEndoplasmic ReticulumThiazolidinesMutagenesis, Site-DirectedKineticsIon ChannelsBinding SitesProtein TransportSequence DeletionXenopus laevisSodium-Hydrogen AntiporterVas DeferensXenopusRNA, MessengerRecombinant Fusion ProteinsProtein Structure, SecondaryBiological TransportChloride-Bicarbonate AntiportersPhosphorylationCOS CellsLungPancreatic DuctsExocrine GlandsAmino Acid SubstitutionGene ExpressionSweat GlandsHSC70 Heat-Shock ProteinsSodium ChannelsAntiportersGene Expression RegulationModels, BiologicalMutation, MissenseNucleotidesModels, MolecularPoint MutationTetramisoleSequence Homology, Amino AcidCyanatesRespiratory SystemSignal TransductionCell PolarityEpithelial Sodium Channel BlockersPhenotypeATP-Binding Cassette TransportersEndocytosis