• Cardiac surgeons frequently deal with transposition of the great arteries (TGA) and total anomalous pulmonary enous Cocnnection (TAPVC), common cyanotic congenital heart diseases (CHD). (figshare.com)
  • Total Anomalous Pulmonary Venous Connection (TAPVC) is a rare form of congenital heart disease (CHD) in which all pulmonary veins connect to the systemic veins, right atrium or the coronary sinus. (biomedcentral.com)
  • The total anomalous pulmonary venous communication [TAPVC] is a rare cyanotic congenital cardiac defect accounting for 1.5-3% of the congenital heart disease, in which pulmonary venous [PV] blood drains directly into the right side of the heart or into the systemic veins. (jaccr.com)
  • In a remarkable medical achievement, a 9-month-old baby boy diagnosed with a rare congenital heart condition called Supracardiac Total Anomalous Pulmonary Venous Connection (TAPVC) has been successfully treated through a complex surgery conducted at a renowned city hospital in Nagpur. (nagpurtoday.in)
  • TAPVC is a complex congenital heart defect characterized by abnormal connections of the pulmonary veins responsible for carrying oxygen-rich blood from the lungs to the heart. (nagpurtoday.in)
  • He stated that TAPVC occurs in only 0.5 to 0.9 cases per 100,000 live births and accounts for 1% of all congenital heart defects. (nagpurtoday.in)
  • These are all supracardiac, infracardiac, mixed type and intracardiac TAPVC with pulmonary venous stenosis. (medpharmres.com)
  • Of those, fourteen (82.4%) cases were supracardiac TAPVC and 3 (17.6%) cases were infracardiac TAPVC. (medpharmres.com)
  • Twenty-eight consecutive 1 day to 7 month-old infants with TAPVC (14 supracardiac, six intracardiac and eight infracardiac type) had surgical repair with intraoperative TEE monitoring. (qxmd.com)
  • The described patient is a 23-year male who presented with self - limiting single episode of chest pain, palpitations and dyspnea, diagnosed as supracardiac unobstructed TAPVC with ostium secundum atrial septal defect [OS - ASD] and PAH, who underwent successful intracardiac repair under cardiopulmonary bypass [CPB]. (jaccr.com)
  • In the case of Supracardiac TAPVC, the abnormal connection occurs between the veins that drain blood into the heart, leading to severe heart-lung complications that can be life-threatening. (nagpurtoday.in)
  • citation needed] TAPVC can occur with obstruction, which occurs when the anomalous vein enters a vessel at an acute angle and can cause pulmonary venous hypertension and cyanosis because blood cannot enter the new vein as easily. (wikipedia.org)
  • Total (or partial) anomalous pulmonary venous connection (TAPVC) - when the four veins that take oxygenated blood from the lungs to the left side of the heart are all connected to the right side of the heart. (milaap.org)
  • Total anomalous pulmonary venous connection (TAPVC) may cause clinical signs and symptoms of resistant to treatment respiratory distress syndrome (RDS) in the full-term newborn. (lupinepublishers.com)
  • Particularly the obstructive type of total anomalous pulmonary venous connection (TAPVC), in which pulmonary veins drain into systemic venous structures or directly into right atrium without having any direct connection to left atrium, cause RDS by leading to severe pulmonary congestion. (lupinepublishers.com)
  • Total anomalous pulmonary venous connection (TAPVC) is a rare condition. (medpharmres.com)
  • Recently, it had been adopted for primary TAPVC to prevent postoperative pulmonary venous obstruction, a leading cause of death. (medpharmres.com)
  • But the use of TEE in infants with total anomalous pulmonary venous connection (TAPVC) remains unclear. (qxmd.com)
  • TEE probe insertion in TAPVC patients may pose a potential risk of compression of pulmonary venous confluence resulting in hemodynamic instability. (qxmd.com)
  • In this study we looked at the prevalence and pattern of TAPVC and Partial Anomalous Pulmonary Venous Connection (PAPVC) in Indian patients with CHD. (biomedcentral.com)
  • Patients with Anomalous Pulmonary Venous Connection (APVC) were classified into TAPVC and PAPVC. (biomedcentral.com)
  • Total anomalous pulmonary venous connection (TAPVC) with direct connection of the pulmonary veins to the morphologically right atrium is exceedingly rare other than in the setting of isomerism of the right atrial appendages. (revportcardiol.org)
  • Excluding measures are TAPVC with single ventricle, isomerism or heterotaxy. (medpharmres.com)
  • In this report it is reemphasized that obstructive TAPVC should be searched for an etiology of treatment resistant respiratory distress in the full-term newborn. (lupinepublishers.com)
  • Neonates with obstructive TAPVC may present with cyanosis, metabolic acidosis, respiratory failure, and shock. (jaccr.com)
  • A subset of patients with unobstructed TAPVC may remain symptoms free and attain adulthood, or present with pulmonary congestion, pulmonary arterial hypertension [PAH]. (jaccr.com)
  • In TAPVC without obstruction, surgical redirection can be performed within the first month of life. (wikipedia.org)
  • Including criteria consists of patients with primary TAPVC. (medpharmres.com)
  • Therefore, we suggest that the use of TEE in such TAPVC patients appears to be safer after sternotomy. (qxmd.com)
  • Patients with TAPVC were sub-classified into supra-cardiac, cardiac, infra-cardiac and mixed type based on the site of drainage. (biomedcentral.com)
  • Of these, 411 (10.3%) patients had APVC, 232 (6%) had TAPVC and 172 (4.3%) had PAPVC. (biomedcentral.com)
  • The most common type of TAPVC was supra-cardiac in 106 (46%), followed by cardiac in 55 (24%) and mixed type of TAPVC in 51 (22%) patients. (biomedcentral.com)
  • The objective of this case report and review is to recognize the spectrum of various clinical presentations in TAPVC, and to describe the diagnosis and perioperative management of TAPVC. (jaccr.com)
  • Sutureless technique could be a safe option for primary TAPVC repair. (medpharmres.com)
  • We reviewed the safety and efficacy of intraoperative TEE during TAPVC repair. (qxmd.com)
  • However, the association of TGA with TAPVC is rare. (figshare.com)
  • Mortality of TAPVC has improved dramatically in the present. (medpharmres.com)
  • Infra-cardiac TAPVC was present in 20 (8%) cases. (biomedcentral.com)
  • We present an interesting case of TAPVC in a patient with situs solitus that connected to the right atrium via a broad-mouthed common chamber. (revportcardiol.org)
  • The anesthetic management of either obstructed TAPVC or unobstructed with PAH can be quite challenging. (jaccr.com)
  • This technique had gradually applied at our institute for primary TAPVC since 2018. (medpharmres.com)
  • Seventeen TAPVC cases were enrolled in this study from 06/2019-12/2020 at Children's Hospital 1. (medpharmres.com)
  • Total anomalous pulmonary venous connection (TAPVC) consists of an abnormality of blood flow in which all four pulmonary veins drain into systemic veins or the right atrium with or without pulmonary venous obstruction. (medscape.com)
  • This study identified risk factors associated with prolonged postoperative intensive care unit (ICU) stay in children with total anomalous pulmonary venous connection (TAPVC). (biomedcentral.com)
  • Background: Obstructed total anomalous pulmonary venous connection (TAPVC) typically present with severe cardiovascular decompensation and requires urgent surgical management. (bvsalud.org)
  • Purpose : Surgical risk of total anomalous pulmonary venous connection(TAPVC) is high, especially in patients with early presentation resulting from pulmonary venous obstruction or with advanced pulmonary vascular obstructive disease(PVOD). (e-cep.org)
  • The medical records of 85 patients who underwent surgical repair of TAPVC were retrospectively analyzed. (biomedcentral.com)
  • In this study, we analyzed the medical records of patients who underwent TAPVC surgery in the past five years to identify the risk factors associated with prolonged ICU stay to further improve clinical outcomes, decrease medical costs, and save medical resources. (biomedcentral.com)
  • The medical records of patients who underwent surgical repair of TAPVC at our hospital between June 2016 and September 2020 were retrospectively analyzed. (biomedcentral.com)
  • This particular single-center, retrospective cohort examine ended up being carried out in sequential singled out TAPVC individuals whom underwent neonatal surgery in between January One, Last year as well as Jan One particular, 2022. (notes.io)
  • Total anomalous pulmonary venous return (TAPVR) (pronounced TOHT-l uh-NOM-uh-luh-s PUHL-muh-ner-ee VEE-nuh-s ri-TURN), or connection (TAPVC) is a birth defect of the heart in which the veins bringing blood back from the lungs ( pulmonary veins ) don't connect to the left atrium like usual. (cdc.gov)
  • In TAPVC without obstruction, surgical redirection can be performed within the first month of life. (wikipedia.org)
  • The outcomes of surgical repair of TAPVC have improved over the years. (biomedcentral.com)
  • We reviewed our experience of primary correction of TAPVC and examined the surgical outcome and risk factors. (e-cep.org)
  • The L . a . datasets in TAPVC people ended up assessed prior to surgical procedure (n = 28) as well as follow-ups with 1-2 (n = 24) as well as 5-7 years (n = 13) and also compared with that regarding age-matched healthy handles (January 2009-2022). (notes.io)
  • citation needed] TAPVC can occur with obstruction, which occurs when the anomalous vein enters a vessel at an acute angle and can cause pulmonary venous hypertension and cyanosis because blood cannot enter the new vein as easily. (wikipedia.org)
  • Total (or partial) anomalous pulmonary venous connection (TAPVC) - when the four veins that take oxygenated blood from the lungs to the left side of the heart are all connected to the right side of the heart. (milaap.org)
  • Individuals underwen Full anomalous lung venous connection (TAPVC) is often a exceptional congenital coronary disease of newborns seen as reduced remaining ventricle progress along with diastolic dysfunction. (notes.io)
  • Material and Method: After ethical committee approval, the study was conducted over a period of 3 years in 80 patients with obstructed TAPVC repair. (bvsalud.org)
  • Conclusion: Most of the patients with obstructed TAPVC had severe PAH. (bvsalud.org)
  • We gathered whole exome sequencing (WES) data for Group 1 consisting of patients with PA ( n = 78), TOF ( n = 20), TAPVC ( n = 78), and PDA ( n = 40), and 100 healthy children as control group. (nih.gov)
  • Many of us hypothesized how the individuals together with TAPVC diminished the flow of blood in the still left center prenatally make a difference remaining atrium (LA) not simply development nevertheless operate. (notes.io)
  • Lower preoperative SpO 2 , higher intraoperative plasma lactate levels, and prolonged postoperative mechanical ventilation were independent risk factors for prolonged ICU stay in children with TAPVC. (biomedcentral.com)
  • However, TAPVC remains a critical cardiac disease with the low prenatal detection rates. (biomedcentral.com)