Wegener GranulomatosisLymphomatoid GranulomatosisScleromyxedemaMastocytosis, CutaneousHistiocytosis, Langerhans-CellVulvar DiseasesSkin DiseasesAntibodies, Antineutrophil CytoplasmicMyeloblastinAmyloidosisBiopsyVasculitisMicroscopic PolyangiitisGranulomatosis, OrofacialSkinChurg-Strauss SyndromePolyarteritis NodosaSarcoidosisGranulomaScleritisCryopyrin-Associated Periodic SyndromesNose Deformities, AcquiredImmunosuppressive AgentsSerine EndopeptidasesAnti-Neutrophil Cytoplasmic Antibody-Associated VasculitisLung DiseasesBronchial DiseasesLaryngostenosisSyndromePrednisoloneCyclophosphamideBehcet SyndromePeroxidaseOrbital DiseasesSarcoidosis, PulmonaryArteritisEosinophilic GranulomaFatal OutcomeNose DiseasesAutoantibodiesVasculitis, Leukocytoclastic, CutaneousGranuloma, Respiratory TractSystemic VasculitisLip DiseasesPseudoxanthoma ElasticumTomography, X-Ray ComputedTreatment OutcomeGlomerulonephritisRecurrenceAllostasisAutoantigensEye DiseasesCranial Nerve DiseasesMyotonic DisordersIleal DiseasesMyotonic DystrophyPrednisoneRetrospective StudiesAlagille SyndromeSkin ManifestationsMultiple TraumaNeutrophilsAntibodies, Monoclonal, Murine-DerivedGranuloma, Lethal MidlineMethylprednisoloneRemission InductionOphthalmoplegiaFocal Dermal HypoplasiaHorner SyndromeGlycogen Storage Disease Type IIbOtorhinolaryngologic DiseasesAdrenal Cortex HormonesFacial ParalysisFluorescent Antibody Technique, IndirectLymphangioleiomyomatosisTalcMouth DiseasesHobbiesKidneys, ArtificialGlucocorticoidsCongenital Disorders of GlycosylationTuberous SclerosisAzathioprineLupus Erythematosus, SystemicAutoimmune DiseasesDe Lange SyndromeImmunoglobulin GMagnetic Resonance ImagingLungParanasal SinusesMutationPlasma ExchangeLeukocyte ElastasePurpura, Schoenlein-HenochTracheal DiseasesLaryngeal DiseasesTrimethoprim-Sulfamethoxazole Combination