CitrullineOrnithineArginineOrnithine CarbamoyltransferaseHydrolasesArginine VasopressinArginine KinaseCitrullusGlutamineArginaseNitrogen IsotopesAmino AcidsKineticsArgininosuccinate LyaseCarbamyl PhosphateNitric Oxide SynthaseMolecular Sequence DataNitric OxideProlineUreaAmmoniaCitrullinemiaCarbon IsotopesProtein BiosynthesisAmino Acid SequenceArgininosuccinic AcidAmino Acid OxidoreductasesMutationRNA, MessengerEscherichia coliCarbamoyl-Phosphate Synthase (Ammonia)Cells, CulturedBase SequenceLeucineOrotic AcidAmino Acid Transport Systems, BasicGlutamatesLiverStereoisomerismProtein Synthesis InhibitorsCell LineAgmatineMolecular StructureLysineShort Bowel SyndromeCatecholamine Plasma Membrane Transport ProteinsMouth AbnormalitiesNitrogenDNAPhenylglyoxalTime FactorsNitritesAmino Acids, DiaminoMitochondria, LiverNitratesEnterocytesBiopterinCycloheximideCatalysisIsotope LabelingOrnithine Carbamoyltransferase Deficiency DiseaseBacterial ProteinsArgininosuccinate SynthaseIntestinesCarbon RadioisotopesDNA ReplicationOrnithine-Oxo-Acid TransaminaseTranscription, GeneticEnzyme InductionSubstrate SpecificityArgininosuccinic AciduriaBinding SitesTritiumCyclizationSwineEnzyme InhibitorsRecombinant ProteinsRenal AminoaciduriasStructure-Activity RelationshipHydrogen-Ion ConcentrationPhenylbutyratesKidneyCanavaninePhenylalanineCationic Amino Acid Transporter 1RNAMagnetic Resonance SpectroscopyRats, Inbred StrainsHomoarginineCloning, MolecularMethylationIntestine, SmallProtein BindingChromatography, High Pressure LiquidNitric Oxide Synthase Type IICulture MediaParenteral NutritionUracilCell-Free SystemNitric Oxide Synthase Type III