Cystic FibrosisCystic Fibrosis Transmembrane Conductance RegulatorFibrosisPseudomonas InfectionsPseudomonas aeruginosaSweatSputumMice, Inbred CFTRBurkholderia InfectionsBurkholderia cepaciaChloridesEndomyocardial FibrosisIdiopathic Pulmonary FibrosisLungExocrine Pancreatic InsufficiencyLiver CirrhosisChloride ChannelsForced Expiratory VolumeNasal MucosaRespiratory MucosaTobramycinRespiratory Function TestsNeonatal ScreeningPancreatinRetroperitoneal FibrosisBurkholderia cepacia complexRespiratory SystemBronchiectasisPancreatic ExtractsLung DiseasesMutationSeverity of Illness IndexEpithelial CellsAnti-Bacterial AgentsBronchiMucusLung TransplantationHeterozygote DetectionExpectorantsTime FactorsMeconiumAlginatesTreatment OutcomeBleomycinPancrelipaseDisease Models, AnimalTracheaChronic DiseaseAchromobacter denitrificansVital CapacityMucociliary ClearanceDepressionSymptom AssessmentPhenotypeSweat GlandsRespiratory Tract InfectionsBurkholderia cenocepaciaAdministration, InhalationQuestionnairesProspective StudiesAminophenolsGenotypeAspergillosis, Allergic BronchopulmonaryIon TransportLeukocyte ElastaseOral Submucous FibrosisCell LineGenetic TestingLiver Cirrhosis, ExperimentalInfant, NewbornRetrospective StudiesAmilorideEpitheliumFollow-Up StudiesCells, CulturedDisease ProgressionDrainage, PosturalHexuronic AcidsMolecular Sequence DataPrevalenceColistinStenotrophomonas maltophiliaGlucuronic AcidBiopsyCross-Sectional StudiesHydroxyprolinePolymerase Chain ReactionMice, Inbred C57BLExocrine GlandsQuality of LifeMucinsCoughRespiratory TherapyBronchoalveolar Lavage FluidBiological MarkersBurkholderiaBreath TestsMembrane ProteinsColforsinHepatic Stellate Cells