Leigh DiseaseSpisulaCytochrome-c Oxidase DeficiencyBivalviaMitochondrial ProteinsElectron Transport Complex IVMembrane ProteinsParacoccus denitrificansProteinsMeiosisMitochondrial DiseasesOocytesProtein SubunitsCharcot-Marie-Tooth DiseaseHemeConsanguinitySeawaterMutationMitochondriaHomozygoteFibroblastsPhenotypeRNA SplicingMolecular Sequence DataElectrophoresis, Polyacrylamide GelMuscle, SkeletalAmino Acid SequenceProtein BindingOxidation-ReductionBacterial Proteins