Amyotrophic Lateral SclerosisSuperoxide DismutaseSpinal CordMotor Neuron DiseaseMotor NeuronsRNA-Binding Protein FUSMultiple SclerosisDNA Repeat ExpansionFrontotemporal DementiaGuamRiluzoleFrontotemporal Lobar DegenerationInclusion BodiesMice, TransgenicDisease Models, AnimalNerve DegenerationNeurodegenerative DiseasesMutationFasciculationAnterior Horn CellsSpinal Cord InjuriesTDP-43 ProteinopathiesSclerosisBulbar Palsy, ProgressiveNeurofilament ProteinsDisease ProgressionRats, TransgenicBrainAge of OnsetNeuronsTuberous SclerosisAstrocytesMutation, MissenseLithium CarbonateMicrogliaCycasNeuroprotective AgentsPyramidal TractsExcitatory Amino Acid Transporter 2DNA-Binding ProteinsAxonsPseudobulbar PalsyMutant ProteinsSialorrheaRotarod Performance TestMuscular Atrophy, SpinalAxonal TransportNoninvasive VentilationAmino Acid SubstitutionRibonuclease, PancreaticInjections, SpinalNeuromuscular DiseasesAnimals, Genetically ModifiedCase-Control StudiesElectromyographyMuscle WeaknessMagnetic Resonance ImagingMitochondriaAmino Acids, DiaminoSpinal Nerve RootsParalysisCell DeathNerve Tissue ProteinsNeurogliaCentral Nervous SystemPeripherinsPhenotypeProtein FoldingScleroderma, SystemicNeuromuscular JunctionLaughterDementiaMice, Inbred C57BLGlial Fibrillary Acidic ProteinMuscle, SkeletalImmunohistochemistryPedigreeParkinson DiseaseGliosisGlutamic AcidCommunication Aids for DisabledCopperTracheostomyItalyAtrophyMotor CortexTime FactorsSpinal Cord DiseasesUbiquitinChromosomes, Human, Pair 9Spinal NervesGlycineGenetic Predisposition to DiseaseRespiratory InsufficiencyNervous System DiseasesPyrazolonesOxidative StressCell SurvivalMotor ActivityAnesthesia, Spinal