Motor NeuronsCranial NervesHexamethoniumSpinal CordMotor Neuron DiseaseNeuronsSurvival of Motor Neuron 1 ProteinNeurons, AfferentMotor CortexSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorAmyotrophic Lateral SclerosisMuscular Atrophy, SpinalMotor ActivityAxonsSMN Complex ProteinsAction PotentialsNerve Tissue ProteinsMolecular Motor ProteinsElectric StimulationNerve DegenerationSynapsesNeuromuscular DiseasesGanglia, InvertebrateElectrophysiologyInterneuronsSynaptic TransmissionMovementCholinergic NeuronsCells, CulturedAplysiaMice, TransgenicDopaminergic NeuronsSuperoxide DismutaseElectromyographyAnterior Horn CellsNeuromuscular JunctionDendritesSensory Receptor CellsBulbar Palsy, ProgressiveGanglia, SpinalNeural InhibitionGABAergic NeuronsPatch-Clamp TechniquesImmunohistochemistryModels, NeurologicalBrain