Motor NeuronsMotor Neuron DiseaseNeuronsMuscular Atrophy, SpinalSurvival of Motor Neuron 1 ProteinNeurons, AfferentCell SurvivalSurvival of Motor Neuron 2 ProteinMotor CortexSurvival RateEvoked Potentials, MotorSpinal CordAmyotrophic Lateral SclerosisMotor ActivityNerve Tissue ProteinsAxonsSMN Complex ProteinsCyclic AMP Response Element-Binding ProteinAction PotentialsDisease-Free SurvivalTime FactorsSurvivalCells, CulturedRNA-Binding ProteinsSpinal Muscular Atrophies of ChildhoodNerve DegenerationMolecular Motor ProteinsMice, TransgenicElectric StimulationSynapsesImmunohistochemistryNeuromuscular DiseasesGanglia, InvertebrateSurvival AnalysisElectrophysiologyDisease Models, AnimalCholinergic NeuronsInterneuronsSynaptic TransmissionGraft SurvivalMovementSuperoxide DismutaseMutationNeuromuscular JunctionDEAD Box Protein 20Ribonucleoproteins, Small NuclearAnterior Horn CellsAplysiaDopaminergic NeuronsElectromyographyAnimals, NewbornBrainDendritesSensory Receptor CellsGanglia, SpinalMice, Inbred C57BLBulbar Palsy, ProgressivePatch-Clamp TechniquesGABAergic NeuronsNeural InhibitionModels, NeurologicalCoiled BodiesAnimals, Genetically ModifiedCerebral CortexSignal TransductionHippocampusFacial NerveMembrane PotentialsMice, KnockoutMotor Skills DisordersBrain StemCell Countgamma-Aminobutyric AcidNeuropeptidesCentral Nervous SystemAxonal TransportGreen Fluorescent ProteinsTreatment OutcomeCell DifferentiationAnalysis of VarianceMuscle, SkeletalGene Expression Regulation, DevelopmentalCholine O-AcetyltransferaseBehavior, AnimalNeural ConductionCell DeathGangliaNeurofilament ProteinsGrasshoppersLocomotionNerve NetApoptosisNeurons, EfferentRats, Sprague-DawleyNerve Growth FactorsReaction TimeNeuronal PlasticityMedulla OblongataExcitatory Postsynaptic PotentialsMolecular Sequence Data