Acidosis, LacticAcidosisMELAS SyndromeAcidosis, RespiratoryAcidosis, Renal TubularPhenforminRNA, Transfer, LeuLactatesLactic AcidMitochondrial EncephalomyopathiesAcid-Base EquilibriumDichloroacetic AcidPyruvate Dehydrogenase Complex Deficiency DiseaseSodium BicarbonateDiabetic KetoacidosisMetforminMitochondrial MyopathiesBicarbonatesHydrogen-Ion ConcentrationAlkalosisMERRF SyndromeDNA, MitochondrialMitochondrial DiseasesLeigh DiseaseCarbon DioxideThiamine DeficiencyStavudineAmmonium ChlorideHyperglycemic Hyperosmolar Nonketotic ComaThyroid CrisisBiguanidesPyruvate Dehydrogenase (Lipoamide)Fatal OutcomeBarth SyndromeHypoglycemic AgentsCytochrome-c Oxidase DeficiencyMitochondria, MuscleRhabdomyolysis