Muscular Atrophy, SpinalSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinAtrophySMN Complex ProteinsMuscular AtrophySurvival of Motor Neuron 2 ProteinSpinal CordMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinMotor NeuronsAnterior Horn CellsRNA-Binding ProteinsNerve Tissue ProteinsSpinal Cord DiseasesOptic AtrophyMotor Neuron DiseaseRibonucleoproteins, Small NuclearDisease Models, AnimalDEAD Box Protein 20Chromosomes, Human, Pair 5ExonsSpinal Nerve RootsInjections, SpinalSpinal NervesSeverity of Illness IndexCoiled BodiesMultiple System AtrophyAnesthesia, SpinalReceptors, AndrogensnRNP Core ProteinsSpinal Cord NeoplasmsSpinal CanalPedigreeSpinal DiseasesSpinal Cord CompressionMuscle, SkeletalSpinal NeoplasmsPhenotypeMice, TransgenicBulbar Palsy, ProgressiveSpinal StenosisSpinal FusionMutationElectromyographyNerve DegenerationCharcot-Marie-Tooth DiseaseMuscle WeaknessHeterozygote DetectionMagnetic Resonance ImagingGene DeletionContractureOlivopontocerebellar AtrophiesNeuromuscular DiseasesAxonsGlycine-tRNA LigaseArthrogryposisHomozygoteNeural ConductionVocal Cord ParalysisSpinal InjuriesGyrate AtrophyNeuromuscular JunctionTrinucleotide Repeat ExpansionNeuromuscular Junction DiseasesRNA SplicingTime FactorsAmyotrophic Lateral SclerosisMolecular Sequence DataDisease ProgressionSpinal Cord IschemiaGanglia, SpinalGenes, RecessiveAge of OnsetSural NerveGeographic AtrophyBrainGenetic LinkageGene DosageTrinucleotide RepeatsPolymerase Chain ReactionMice, KnockoutIntranuclear Inclusion BodiesGenes, DominantMyelographyMice, Inbred C57BLMotor ActivityMutation, MissenseBase SequenceGenotypeInclusion BodiesParaplegiaFasciculationMyoclonic Epilepsies, ProgressiveInfant, NewbornChemistry, AnalyticSpine