Hearing Loss, SensorineuralDeafnessHypoparathyroidismSyndromeHearing Loss, BilateralPedigreeBulbar Palsy, ProgressiveJervell-Lange Nielsen SyndromeAtaxiaGenes, RecessiveEar, InnerHearing LossAbnormalities, MultipleCochleaConsanguinityVestibular DiseasesNephritis, HereditaryAnemia, MegaloblasticHearing Loss, SuddenWaardenburg SyndromeConnexinsMutationAudiometry, Pure-ToneGenes, DominantGenetic LinkageMutation, MissenseAudiometryIntellectual DisabilityThiaminePhenotypeEvoked Potentials, Auditory, Brain StemChromosome MappingDNA Mutational AnalysisLod ScoreChromosomes, Human, Pair 1Hearing TestsAuditory ThresholdDNA, MitochondrialHearing Loss, UnilateralHearing Loss, ConductiveSpiral GanglionLabyrinth DiseasesHeterozygoteCochlear NerveMembrane Transport ProteinsVestibular AqueductGenetic MarkersHearingTemporal BoneHearing AidsHair Cells, AuditoryHearing Loss, High-FrequencyInfant, NewbornCochlear ImplantsCochlear ImplantationMolecular Sequence DataHearing DisordersOrgan of CortiStria VascularisHearing Loss, CentralRound Window, EarBase SequenceTinnitusOtosclerosisUsher SyndromesCochlear DuctOtoacoustic Emissions, SpontaneousBone ConductionPresbycusisAudiometry, Evoked ResponseMeniere DiseaseSpeech PerceptionWolfram SyndromeAcoustic Impedance TestsVertigoLabyrinthitisAcoustic StimulationPersons With Hearing ImpairmentsSpeech Discrimination TestsVestibulocochlear Nerve DiseasesHearing Loss, Noise-InducedTympanic MembraneAudiologySpeech Reception Threshold TestFacial ParalysisKCNQ Potassium ChannelsHair Cells, Auditory, InnerVestibule, LabyrinthKeratoderma, PalmoplantarVibrationNoiseOtolaryngologyVestibular Function TestsHomozygoteEar, MiddlePetrous BoneIchthyosisAlstrom SyndromeEar DiseasesHair Cells, Auditory, Outer