Cysteine DioxygenaseCysteineSulfur CompoundsTaurineDioxygenasesCarboxy-LyasesSulfatesPyruvate KinaseGlutathionePyruvate Dehydrogenase ComplexPyruvic AcidPyruvatesPyruvate DecarboxylasePyruvate OxidaseCysteine EndopeptidasesEnergy MetabolismPyruvate Dehydrogenase (Lipoamide)Cysteine ProteasesLipid MetabolismGlucoseMolecular Sequence DataOxidation-ReductionAmino Acid SequenceKineticsLactatesPyruvate Dehydrogenase (Lipoamide)-PhosphataseLiverGlycolysisCysteine Proteinase InhibitorsCysteine SynthaseLactic AcidCitric Acid CycleMetabolismPhosphoenolpyruvateCarbon IsotopesDisulfidesAcetatesMalatesThiamine PyrophosphateEscherichia coliDichloroacetic AcidSulfhydryl CompoundsPyruvate Dehydrogenase Complex Deficiency DiseaseMutationOxaloacetic AcidAdenosine TriphosphateBase SequenceOxygen ConsumptionDihydrolipoyllysine-Residue AcetyltransferaseBinding SitesMagnetic Resonance SpectroscopyMutagenesis, Site-DirectedMitochondriaNADChromatography, High Pressure LiquidHydrogen-Ion ConcentrationGluconeogenesisFatty AcidsOxaloacetatesSequence Homology, Amino AcidAlanineRecombinant ProteinsCystineMetabolic Networks and PathwaysCarbon RadioisotopesCarbon DioxideKetoglutaric AcidsL-Lactate DehydrogenaseKetone OxidoreductasesSubstrate SpecificityBiotransformationRats, Inbred StrainsInsulinModels, BiologicalCloning, MolecularAnaerobiosisDecarboxylationModels, MolecularStarvationSulfurCoenzyme AKeto AcidsCathepsinsCulture MediaIsoenzymesCarbonProtein BindingCitratesProtein ConformationBacterial ProteinsAcetoacetatesAcetyltransferasesTime FactorsMicrosomes, LiverCytochrome P-450 Enzyme SystemCells, CulturedHydroxybutyratesSulfhydryl ReagentsCystatinsProtein Structure, Tertiary