alpha 1-Antitrypsin Deficiencyalpha 1-AntitrypsinPulmonary EmphysemaEmphysemaPhenotypeLiver DiseasesPulmonary Disease, Chronic ObstructiveTrypsin Inhibitorsalpha 1-AntichymotrypsinForced Expiratory VolumePancreatic ElastaseLung DiseasesHeterozygoteHomozygoteProteostasis DeficienciesBronchiectasisLiverAllelesHepatitisLiver CirrhosisMutationSerpinsSmokingGenotypeLung