Muscular Atrophy, SpinalMotor NeuronsSpinal Muscular Atrophies of ChildhoodSurvival of Motor Neuron 1 ProteinSpinal CordSMN Complex ProteinsAtrophySurvival of Motor Neuron 2 ProteinNerve DegenerationNeuronsMuscular AtrophyMotor Neuron DiseaseAmyotrophic Lateral SclerosisRetinal DegenerationDisease Models, AnimalDysautonomia, FamilialNerve Tissue ProteinsMuscular Disorders, AtrophicSubstantia NigraParkinson DiseaseBulbo-Spinal Atrophy, X-LinkedSpinal Cord InjuriesDopaminergic NeuronsAnterior Horn CellsNeuronal Apoptosis-Inhibitory ProteinMutationCyclic AMP Response Element-Binding ProteinMice, TransgenicMacular DegenerationNeurons, AfferentDopamineRNA-Binding ProteinsRetinitis PigmentosaAxonsMotor CortexEvoked Potentials, MotorMice, KnockoutImmunohistochemistryMotor ActivityMice, Inbred C57BLRetinaCells, CulturedDisease ProgressionSpinal Cord DiseasesCell DeathWallerian DegenerationNeuromuscular DiseasesMolecular Sequence DataRibonucleoproteins, Small NuclearOptic AtrophyDEAD Box Protein 20Spinal Nerve RootsBulbar Palsy, ProgressiveMuscle, SkeletalElectromyographyAction PotentialsBrainExonsNeuromuscular JunctionSpinal NervesTime FactorsGanglia, SpinalNeural ConductionSynapsesInjections, SpinalCoiled BodiesPhenotypeChromosomes, Human, Pair 5Electric StimulationMultiple System AtrophyPedigreeSpinal DiseasesAnimals, NewbornIntervertebral Disc DegenerationsnRNP Core ProteinsSuperoxide DismutaseRats, Sprague-DawleyMagnetic Resonance ImagingInterneuronsElectrophysiologyNeurofilament ProteinsReceptors, AndrogenAnimals, Genetically ModifiedFrontotemporal Lobar DegenerationSynaptic TransmissionMolecular Motor ProteinsAnesthesia, SpinalMusclesInclusion BodiesMovementCentral Nervous SystemSpinal Cord CompressionSpinal Cord NeoplasmsSpinal CanalCerebral CortexGanglia, InvertebratePeripheral NervesSciatic NerveCharcot-Marie-Tooth DiseaseCholinergic Neurons