Motor NeuronsNerve DegenerationNeuronsMotor Neuron DiseaseRetinal DegenerationAmyotrophic Lateral SclerosisDysautonomia, FamilialSubstantia NigraSpinal CordParkinson DiseaseDisease Models, AnimalDopaminergic NeuronsSurvival of Motor Neuron 1 ProteinMacular DegenerationDopamineNeurons, AfferentNerve Tissue ProteinsMutationRetinitis PigmentosaMotor CortexMice, TransgenicSurvival of Motor Neuron 2 ProteinEvoked Potentials, MotorRetinaMice, KnockoutCell DeathImmunohistochemistryWallerian DegenerationMice, Inbred C57BLAxonsMuscular Atrophy, SpinalMotor ActivityCells, CulturedDisease ProgressionSMN Complex ProteinsAction PotentialsMolecular Sequence DataIntervertebral Disc DegenerationSynapsesNeuromuscular DiseasesElectric StimulationBrainMolecular Motor ProteinsTime FactorsGanglia, InvertebrateElectrophysiologyFrontotemporal Lobar DegenerationSuperoxide DismutaseSynaptic TransmissionInterneuronsCholinergic NeuronsMovementBulbar Palsy, ProgressiveNeuromuscular JunctionAnterior Horn CellsElectromyographyDendritesAnimals, Genetically ModifiedCerebral CortexGanglia, SpinalAnimals, NewbornAplysiaSensory Receptor CellsPatch-Clamp TechniquesCell CountHippocampusModels, NeurologicalAxonal TransportNeural InhibitionWet Macular DegenerationGABAergic NeuronsNeurofilament ProteinsRats, Sprague-DawleyFacial NerveBrain StemNeural ConductionMuscle, SkeletalMembrane PotentialsPhotoreceptor Cells, VertebrateCentral Nervous SystemGreen Fluorescent ProteinsMotor Skills DisordersBehavior, Animalgamma-Aminobutyric AcidSupranuclear Palsy, ProgressiveCholine O-AcetyltransferaseNeurogliaCerebellumNeuropeptidesAnalysis of VarianceCell SurvivalRetrograde DegenerationAxotomyGene Expression Regulation, DevelopmentalRats, WistarCatsLocomotionAstrocytesGangliaNerve Net