Prion DiseasesPrionsPrPSc ProteinsPrPC ProteinsCreutzfeldt-Jakob SyndromeScrapieMice, TransgenicEndopeptidase KInsomnia, Fatal FamilialGerstmann-Straussler-Scheinker DiseaseEncephalopathy, Bovine SpongiformWasting Disease, ChronicKuruBrainAmyloidDeerInfectious Disease Incubation PeriodMesocricetusProtein FoldingSheepMice, Inbred C57BLCricetinaePlants, Genetically ModifiedDisease Models, AnimalRats, TransgenicAnimals, Genetically ModifiedTransgenesQuinacrinePrP 27-30 ProteinNeurodegenerative DiseasesMutationProteostasis DeficienciesBlotting, WesternCattleMolecular Sequence DataProtein ConformationPhenotypeNeuronsBentoniteImmunohistochemistryBrain ChemistryRuminantsDendritic Cells, FollicularProtein IsoformsAmyloidogenic ProteinsCopperLibyaAmino Acid SequenceSlow Virus DiseasesNerve DegenerationPeptide FragmentsMice, KnockoutTime FactorsSpecies SpecificityRecombinant ProteinsGene ExpressionCodonGlycosylphosphatidylinositolsBase SequencePentosan Sulfuric PolyesterMicrogliaGreen Fluorescent ProteinsPlaque, AmyloidProtein BindingGene Expression RegulationProtein Structure, SecondaryNeuroblastomaAlzheimer DiseaseRepetitive Sequences, Amino AcidDisease SusceptibilityCells, CulturedGlycosylationGliosisProtein Structure, TertiaryRecombinant Fusion ProteinsPromoter Regions, GeneticCongo RedCell LineRNA, MessengerCircular DichroismSpleen14-3-3 ProteinsBiological AssayMutant Proteins