Prion DiseasesPrionsPrPC ProteinsPrPSc ProteinsScrapieCreutzfeldt-Jakob SyndromeEndopeptidase KEncephalopathy, Bovine SpongiformAmyloidWasting Disease, ChronicDeerMesocricetusBrainProtein FoldingPrP 27-30 ProteinSheepCricetinaeInsomnia, Fatal FamilialKuruSaccharomyces cerevisiae ProteinsMice, TransgenicProtein ConformationInfectious Disease Incubation PeriodSaccharomyces cerevisiaeProtein Structure, TertiaryCattleDendritic Cells, FollicularGlutathione PeroxidaseCopperAmino Acid SequenceBrain ChemistryAmyloidogenic ProteinsSpecies SpecificityPeptide FragmentsBlotting, WesternMolecular Sequence DataGlycosylphosphatidylinositolsBentoniteProtein IsoformsProtein Structure, QuaternaryMutationRepetitive Sequences, Amino AcidGuanidineCircular DichroismNeurodegenerative DiseasesNeuronsGPI-Linked ProteinsRecombinant ProteinsProteostasis DeficienciesProtein BindingProtein DenaturationMice, Inbred C57BLHeat-Shock ProteinsModels, MolecularGlycosylationRuminantsPentosan Sulfuric PolyesterBiological AssayNeuroblastomaImmunohistochemistryFungal ProteinsPhenotypeCodonCongo RedSpectroscopy, Fourier Transform InfraredNuclear Magnetic Resonance, BiomolecularDetergentsGoatsGoat DiseasesTime FactorsHSP40 Heat-Shock ProteinsTongue DiseasesDisease SusceptibilitySarcosineProtein StabilitySolubilityPeptidesRecombinant Fusion ProteinsSordarialesQuinacrineLibyaMicroscopy, Electron, Scanning TransmissionSheep DiseasesModels, BiologicalPeptide HydrolasesNerve DegenerationDisease Models, AnimalDecontaminationHSP70 Heat-Shock ProteinsMice, KnockoutCell LinePolymorphism, GeneticMutant ProteinsProtein MultimerizationImmunoblotting