Motor Neuron DiseaseMuscular Atrophy, SpinalMotor NeuronsNeuromuscular DiseasesSpinal Muscular Atrophies of ChildhoodBulbar Palsy, ProgressiveSurvival of Motor Neuron 1 ProteinSMN Complex ProteinsSpinal CordSurvival of Motor Neuron 2 ProteinAmyotrophic Lateral SclerosisMuscular AtrophyAtrophyGene SilencingNeuronsMuscular Disorders, AtrophicBulbo-Spinal Atrophy, X-LinkedAnterior Horn CellsNerve DegenerationNerve Tissue ProteinsMutationSpinal Cord InjuriesAxonsSpinal Cord DiseasesTranscription, GeneticSuperoxide DismutaseFasciculationNeuronal Apoptosis-Inhibitory ProteinCyclic AMP Response Element-Binding ProteinDNA MethylationDEAD Box Protein 20RNA-Binding ProteinsElectromyographyDisease Models, AnimalMotor CortexArgonaute ProteinsNeurons, AfferentMice, TransgenicNeurofilament ProteinsGaggingNeural ConductionTDP-43 ProteinopathiesRNA, Small InterferingInclusion BodiesFrontotemporal Lobar DegenerationFrontotemporal DementiaHeterochromatinRNA InterferenceArabidopsisMotor ActivityMolecular Sequence DataPromoter Regions, GeneticEvoked Potentials, MotorSpinal Nerve RootsArabidopsis ProteinsProton-Phosphate SymportersMuscle, SkeletalPhenotypeToxascariasisbeta-Hexosaminidase beta ChainNeuromuscular JunctionRNA-Binding Protein FUSBrainRiluzoleUlnar NerveGene Expression RegulationPharyngostomyPyrrolidonecarboxylic AcidElectric InjuriesDeglutition DisordersPick Disease of the BrainRNA, PlantPeripheral NervesBase SequenceTransgenesBrain Injury, ChronicAction PotentialsLathyrismMuscle WeaknessGene Expression Regulation, PlantDNA-Binding ProteinsPedigreeTranscription FactorsEpigenesis, GeneticNeurologic ExaminationRibonucleoproteins, Small NuclearRNA, AntisenseReceptors, AndrogenSandhoff DiseaseMusclesCells, CulturedRats, TransgenicMarchiafava-Bignami DiseaseParalysisTime FactorsDementiaImmunohistochemistryAxonal TransportAge of OnsetElectric Stimulation