Thymus HormonesGangliosidosesLipidosesHexosaminidase AHexosaminidase BHexosaminidasesbeta-N-AcetylhexosaminidasesTay-Sachs DiseaseG(M2) GangliosideSandhoff DiseaseG(M2) Activator ProteinMolecular Sequence DataAcetylglucosaminidaseAmino Acid SequenceInterleukin-1betaChromosomes, Human, 4-5Molecular WeightSphingolipid Activator Proteinsbeta 2-MicroglobulinBase SequenceIsoenzymesMacromolecular SubstancesElectrophoresis, Polyacrylamide GelHymecromoneGangliosidoses, GM2KineticsElectrophoresis, Starch GelCell LineReceptors, Adrenergic, betaIntegrin beta3Polymerase Chain ReactionPeptidesSaposinsChromosomes, Human, 13-15Cloning, MolecularProtein ConformationRNA, MessengerAcetylglucosamineLysosomesCells, CulturedIsoelectric FocusingPancreatic PolypeptideMutationPeptide FragmentsReceptors, Antigen, T-Cell, alpha-betaHeterozygote DetectionTransforming Growth Factor betaGenesRecombinant ProteinsBinding SitesChromatography, Ion Exchange