Metabolism, Inborn ErrorsAmino Acid Metabolism, Inborn ErrorsAmino AcidsAmino Acids, SulfurAmino Acids, Branched-ChainSequence Homology, Amino AcidAmino Acid SequenceLipid Metabolism, Inborn ErrorsAmino Acids, EssentialLiverLipid MetabolismNeonatal ScreeningAmino Acids, AromaticPurine-Pyrimidine Metabolism, Inborn ErrorsMutationMetabolomeSteroid Metabolism, Inborn ErrorsEnergy MetabolismFatty AcidsLeucineMolecular Sequence DataCarbohydrate Metabolism, Inborn ErrorsAmino Acid SubstitutionMetabolic Networks and PathwaysNitrogenCloning, MolecularMetabolomicsGlutamineBase SequenceMethionineAlanineUrea Cycle Disorders, InbornAmmoniaBrain Diseases, Metabolic, InbornKineticsGlucoseArgininosuccinic AciduriaHyperammonemiaUreaSequence AlignmentPhenylalanineCarbon IsotopesTransaminasesMaple Syrup Urine DiseaseBacterial ProteinsKeto AcidsPhenylketonuriasGas Chromatography-Mass SpectrometryEscherichia coliDietary ProteinsGene Expression ProfilingOxidation-ReductionIsoleucineChromatography, High Pressure LiquidGlycineCarbonModels, BiologicalArginineAmino Acid Transport SystemsRNA, MessengerSmith-Lemli-Opitz SyndromeProteinsCarbohydrate MetabolismProteomeAspartic AcidPhenotypeOrnithineGene Expression Regulation, BacterialMass SpectrometryTime FactorsCarbon RadioisotopesAminoisobutyric AcidsInfant, NewbornMagnetic Resonance SpectroscopyBiological TransportCarnitineCitric Acid CycleAmino Acid MotifsBinding SitesPhylogenyProtein BiosynthesisInsulinDNA, ComplementaryGlutamatesRefractive ErrorsArachidonic AcidDNAHomogentisate 1,2-DioxygenaseValineLysineBile Acids and SaltsSaccharomyces cerevisiaeNutritional RequirementsHomocystinuriaRecombinant ProteinsTranscriptomealpha-GalactosidaseCysteineTranscription, GeneticOligonucleotide Array Sequence Analysis