Phytanic AcidRefsum DiseasePhytolEicosanoic AcidsMice, KnockoutMicrobodiesChondrodysplasia PunctataChondrodysplasia Punctata, RhizomelicCoenzyme APeroxisomal DisordersOrganomercury CompoundsPeroxisomesZellweger SyndromeCarbon-Carbon LyasesMice, Inbred C57BLPan paniscusFatty AcidsLiverMixed Function OxygenasesCoenzyme A LigasesOxidation-ReductionCells, CulturedVitamin A DeficiencyPongo pygmaeusNebraskaFibroblastsHydroxylationAdrenoleukodystrophyMutationCarrier ProteinsFatsMice, TransgenicSignal TransductionGorilla gorillaGas Chromatography-Mass SpectrometryPhenotypeRNA, MessengerTranscription FactorsIohexolDisease Models, AnimalAcetyl-CoA C-AcetyltransferaseCell LineGene TargetingIronMice, 129 StrainPalmitic AcidsMolecular Sequence DataFormatesBody WeightHominidaeMice, Mutant StrainsBiological TransportDeficiency DiseasesRetinoid X Receptors5,8,11,14-Eicosatetraynoic AcidReceptors, Cytoplasmic and Nuclear